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P M0PFx'MThe questions were distributed as follows: Gynaecology : 12 Development 1 Physiology 1 Contraception 3 Tumours 6 Surgeries 1 Normal Pregnancy 1 Pregancy Complication 6 Note that 1/3rd of the questions are from tumours and are often repeats and could be easily answered by studying classification, staging and treatment. And contraception will give another few questions and a knowledge of contraception + tumours will make one get 50% of OG questions and this is the trend in every exam (including state exams). All the topics listed above are important. In addition, a few more important topics are: 1. Clinical histories a. A multigravida with painless bleeding PV b. A primigravida with high BP c. A 35-year-old women with irregular bleeding... 2. Foetal diameters and pelvic measurements and positions 3. Changes in pregnancy (normal and the common abnormal conditions) 4. Vesicular mole and ectopic pregnancy 139. Pure gonadal dysgenesis will be diagnosed in the presence of: A. Bilateral streak gonads. B. Bilateral dysgenetic gonads. C. One side streak and other dygenetic gonads. D. One side streak and other normal looking gonad. Answer: A (Bilateral streak gonads) Ref: Harrison 15th edn, 2176 Quality: Spotter Status: Repeat QTDF: Harrison Discussion Few conditions that are favourite for examiners: Turner's syndrome Gonadal dysgenesis is characterised by 3 primary amenorrhoea, 3 sexual infantilism, 3 short stature, 3 multiple congenital anomalies, 3 and bilateral streak gonads in phenotypic women with any of several defects of the X chromosome. Mixed gonadal dysgenesis in which a unilateral testis and a contralateral streak gonad may be present; Pure gonadal dysgenesis in which bilateral streak gonads are associated with a 3 normal 46,XX or 46,XY karyotype, 3 normal stature, and 3 primary amenorrhoea; and Noonan's syndrome, an autosomal dominant disorder in both sexes characterised by 3 webbed neck, 3 short stature, 3 congenital heart disease, 3 cubitus valgus, and 3 other congenital defects despite 3 normal karyotypes and 3 normal gonads. Explanation Self Explanatory Comments In pure gonadal dysgenesis, the gonads are not developed and the female phenotype is due to the failure of gonadal development. Tips Chromosomal aberrations and variations in sexual development are hot topics. 140. A 20-year-old woman gives a history of sharp pain in the lower abdomen for 2-3 days every month approximately 2 weeks before the menses. The most probable etiology for her pain is: A. Endometriosis. B. Dysmenorrhoea. C. Pelvic tuberculosis. 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Which of the following are organophosphates: A. dieldrin B. parathion C. malathion D. Kepone 5. Propoxur Ref::Trip 5th Page 81 Park 550 table Quality:::reader Discussion Explanation: anticholinesterases Reversible Carbamates Acridine Physostigmine (Eserine) Neostigmine Pyridostigmine Edrophonium Rivastigmine Donepezil tacrine Irreversible Organophosphates Carbamates Dyflos DFP Echothiophate Parathion Malathion Diazinon TIK 20 Tabun Sarin Soman Carbaryl (Sevin) Propoxur(Baygon) Explanation A. dieldrin-organochlorine pesticide. incorrect choice. B. parathionirreversible OPC. correct choice. C. malathion irreversible OPC. correct choice D. Kepone/chlordecone- organochlorine pesticide. incorrect choice pesticide 5. Propoxurirreversible carbamates. incorrect choice Correct choices: b c 203. Which of the following are features of spinal shock a. Spasticity b. Urinary retention c. Areflexia d. Sensory level e. Increased DTRs Ref::clinical acumen Quality:::spotter thinker reader BATA Discussion Spinal shock(neuronal) is the initial state just after an acute insult causing an UMN lesion caused by the temporary depressant effect on the anterior horn cells. Characterized by paralysis,areflexia,flaccidity,the chracteristic hypertonia and increased relexes of cotticospinal lesion appear after few hrs-days. Explanation Correct choices B C d 217. Which of the following predispose a patient to prehepatic encepalopathy a. Constipation b. Bacterial peritonitis c. Hemorrhage d. Hyperkalemia e. Dehydration Ref: HPIM 1715 Quality:::spotter thinker reader BATA Discussion Common precipitants of hepatic failure Increased nitrogen load GIT bleeding Excess dietary protein Azotemia Constipation Electrolyte & metabolic imbalance Hypokalemia Alkalosis Hypoxia Hyponatremia Drugs Narcotics and Tranqulizers Sedatives Diuretics Miscellaneous Infection surgery Superimposed acute liver disease Progressive liver disease Explanation: A. Constipation B. Bacterial peritonitis being an infection. correct choice. C. Hemorrhage D. Hyperkalemia: Hypokalemia not Hyperkalemia is known to worsen hepatic Encephalopathy. 5. Dehydration can cause hypovolemia & electrolyte disturbances that can ppt. hepatic Encephalopathy Correct choices: a b c e 8. the drugs useful in the treatment of ectopic pregnancy is A. Methotrexate B. Actinomycin D C. Cyclophosphamide D. Potassium fluoride 5. Adriamycin Ref:: Dutta 202 Quality::: spotter Explanation A. Methotrexate: used in medical therapy. correct choice. B. Actinomycin D. correct choice. C. Cyclophosphamide. Incorrect choice. D. Potassium fluoride: potassium chloride is used in ectopic pregnancy. Incorrect choice. 5. Adriamycin is not used in ectopic pregnancy. Correct choices A b 210. Adventitial bursitis due to tuberculosis is found in which of the following sites commonly a. Prepatellar b. Greater trochanter of femur c. Sub acromial d. Metatarsal e. Sub olecranon 209. Snow ball opacities in vitreous is seen in which of the following a. Parsplanitis b. Rheumatoid arthritis c. Anterior unietis d. Retinitis pigmentosa e. Endothelial dystrophy Ref: http://www. indmedica. com/cos/journal/vasculitis. html Quality:::spotter thinker reader BATA Explanation A. Parsplanitis is characterized by snowball opacities. B. Rheumatoid arthritis is one of the causes of pars planitis hence may show snow ball opacities C. Anterior uveitis D. Retinitis pigmentosa 5. Endothelial dystrophy Correct choices: A b 77. The left border of the heart is formed by a. Pulmonary Artery b. Pulmonary vein c. Right ventricle d. Ascending aorta e. Arch of aorta Ref:: BDC 226,Grays 38th 1476 Quality::: spotter thinker reader BATA Discussion Anatomically Right border is formed by RA. Left border of heart is formed by LA and LV. Upper border formed by LA, asc aota & pul trunk infron of it. Inferior border of the heart is formed by RV and contribution of LV at the apex. Correct choices NONE OF THE CHOICES ARE CORRECT Or 77. left border of the heart in chest XR is formed by a. pul artery b. pul vein c. abdominal aorta d. arch of aorta e. right ventricle Quality::: :reader Reference: Discussion: Borders of cardiac silhouette on PA view Right border from above downwards Superior vena cava Outer border of R atrium Sometimes asc, arch of aorta & inferior vena cava Left border from above downwards Aortic knuckle Pul. Trunk or L pul artery L atrial appendage outer border of L ventricle correct choice: a d 9. the resting membrane potential depends on which of the following ions A. Magnesium B. Calcium C. Potassium D. Sodium 5. Chloride Ref:: Ganong 50 Quality::: spotter Discussion The ionic basis of RMP: Explanation A. Magnesium has no role in RMP. B. Calcium has role in action potential in muscle cells not RMP C. Potassium. The major ion whose movements produce RMP. Correct choice. D. Sodium. incorrect choice. 5. Chloride. No role. Correct choices C 79. In acute inflammation the migration of neutrophils and its attachment to endothelium is mediated by which of the follwing. a. Integrins b. Selection s c. Adhesins d. Perforins e. Opsonins Ref:: Robbins 29, 273 Quality:::spotter thinker reader BATA Explanation a. Integrins are transmembrane glycoproteins that function as cell receptors for extra cellular matrix. correct choice. b. Selectins=the loose and transient adhesions involved in rolling of leucocytes over endothelial cells are accounted for by the selectin family of molecules. E-selectin are present on on endothelial cells, P-selectin on platelets and endothelial cells and L-Selectins on leucocytes. c. Adhesins-are molecules that bind bacteria to cells e. g. lipoteichoic acid and protein F. d. Two classes of cytotoxins include perforins and granzymes. . The perforins form pores in the targets cell membranes. incorrect choice. e. Opsonins are protiens or peptides that label targets for phagocytosis by PMNs and/or macrophages. incorrect choice, Correct choices b 102. Susruta samhita was translated by a. Celsius b. harnel c. Bhargabhatta d. heslar e. Bernard Ref: http://www. ayurveda. com/online%20resource/ancient_writings. htm Quality::: BATA Discussion: http://www. ayurveda. com/online%20resource/ancient_writings. htm Sushruta Samhita The Sushruta Samhita deals with the practice and theory of surgery, is an important source of Ayurvedic aphorisms. This work is the first to enumerate and discuss the pitta sub-doshas and the marmas. With its emphasis on pitta, surgery, and blood, this work best represents the transformational value of life. It is dais that this work was first redacted by Nagarjuna. This work, originally written in Sanskrit, is now available in English with Devanagari. Bhishagratnas translation is English and Sanskrit. P. V. Sharma has recently written a translation with both the Sanskrit/Devanagari and English that includes Dallanas commentary. Dallana has been regarded as the most influential commentator on Sushrutas work. Explanation Correct choices B d 21. Prozone phenomenon in precipitation reaction indicates a. False positive reaction b. False negative reaction c. due to excess antibodies d. Due to excess antigens e. Broken antibodies Ref: : AN 91 Quality::: spotter 203. Which of the following are features of spinal shock f. Spasticity g. Urinary retention h. Areflexia i. Sensory level j. Increased DTRs Ref::clinical acumen Quality:::spotter thinker reader BATA Discussion Spinal shock(neuronal) is the initial state just after an acute insult causing an UMN lesion caused by the temporary depressant effect on the anterior horn cells. Characterized by paralysis,areflexia,flaccidity,the chracteristic hypertonia and increased relexes of cotticospinal lesion appear after few hrs-days. Explanation 6. Spasticity appears hrs day after spinal shock has passed in an UMN lesion. 7. Urinary retention is a feature of spinal cord disease. appears first in case of disease originating from the canal and spreading outwards and last in mass lesions compressing spinal cord from the outside. Its a feature of spinal shock. 8. Areflexia is a feature of spinal shock. 9. Sensory level is seen in case of corticospinal lesion. 10. Increased DTRs will be seen after the spinal shock has passed. Correct choices B C d 202. Diseases inherited with triple repeat sequences include a. Huntingtons chorea b. Alzheimers disease c. Spinocerebellar ataxia d. Amyotrophic lateral sclerosis e. Ataxia telangiectasia Ref:: Robbins 197,739,741,157 Quality:::spotter thinker reader BATA Discussion Harrison 2294 table gives explicit information about genetic defects in neurological disease. Robbins has enumerated three diseases having triple repeat sequences: Fragile X syndrome Huntington;s ds, Myotonic dystrophy Explanation A. Huntingtons chorea:AD : CAG triple repeats in gene encoding proein huntingtin B. Alzheimers disease:AD mutations presenilin,apolipoprotein E4,APP genen C. Spinocerebellar ataxia:expansion of trinucleotide repeats in ataxin gene D. Amyotrophic lateral sclerosis:AD mutation in Cu-Zn superoxide Dismutase SOD. 5. Ataxia telangiectasia AR mutation in ATM gene which causes triple repeat sequences and abnormal production of protein. Correct choices A c e 59. Tumor markers of hepatocellular carcinoma include a. CEA b. Des gamma carboxyprothrombin c. CA 19-9 d. Fucosylated alpha protein e. Alpha fetoprotien elevated in greater than 70% Ref:: HPIM 579, CMDT 689 http://www. intouchlive. com/consults/ccn9903b. htm Quality:::spotter thinker reader BATA Discussion Alpha fetoprotein levels raised in Cirrhosis Massive liver necrosis Chronic hepatitis hepatocellular carcinoma Normal pregnancy Fetal distress or death Fetal neural tube defects-enencephaly & spina bifida Gonadal germ cell tumours teratoblastoma, Levels above 1000 ng/ml HCC CEA (Carcino Embryonic Antigen) elevated in: malignancies of the gastrointestinal tract (pancreas, colon, rectum), lung, breast, prostatic and ovary. inflammation and heavy smoking. CA-125 normally found in adult female fallopian tube, endometrium and endocervix. CA-15 elevated breast and lung cancer. . CA-199 elevated in intra-abdominal carcinomas, adenocarcinomas of the lung, gastric, biliary and colonic neoplasms. Explanation a. serum CEA levels alone are not specific for hepatocellular carcinoma but are nonetheless raised. correct choice. b. Des gamma carboxyprothrombin, an abnormal typre of [rothrombin which correlates with h levels of AFP. c. CA 19-9 levels are elevated in HCC. D most of the patients with hepatocellular carcinoma have an elevated serum concentration of fucosylated alpha-fetoprotein. correct choice. e. Alpha-fetoprotein elevated in greater than 70% . true. Correct choices A bcde 67. Which of the following are causes of posterior mediastinal mass: A. Neuroenteric cyst B. Neurogenic cyst C. Anterior thoraxic meningocele D. Lymphoma E. Bronchogenic cyst Anterior mediastinum: Middle Mediastinum: Posterior mediastinum: Germ cell neoplasm Lymphoma: Morgagni hernia Pericardial cyst Thymic lesions: Thyroid (Retrosternal goiter) Foregut duplication cysts Castlemans disease Lymphangioma Lymphoma Bronchogenic cyst Bochdalek Hernia Extramedullary Hematopoiesis Ganglioneuroma Ganglioneuroblastoma Neuroblastoma Lateral thoracic meningocele Malignant tumor of nerve sheath origin Neurofibroma Paraganglioma Pheochromocytoma Schwannoma Explanation A. Neuroenteric cyst is present in the posterior mediastinum or paravertebral area. B. Neurogenic cyst is present in the posterior mediastinum C. Anterior thoracic meningocele is present in the posterior mediastinum D. Lymphoma is a tumour of the middle or anterior mediastinum E. Bronchogenic cyst is a tumour of the middle mediastinum. Correct choices Abc 213. Peripheral neuropathy is seen in all of the following except a. Tuberculosis b. Polyarteritis nodasa c. Diabetes mellitus d. SLE 89. Diabetes mellitus is associated with all of the following except: a. Neuropathy b. Encephalopathy c. Myopathy d. Myelitis e. Myelopathy Ref: CMDT 1191,HPIM 2481 Quality:::spotter thinker reader BATA Discussion Diabetic neuromuscular involvement may manifest as: A. Distal symmetric polyneuropathy B. Isolated peripheral neuropathy-mononeuropathy C. Mononeuritis multiplex D. Painful neuropathy 5. Autonomic neuropathy 6. Cranial neuropathypainful opthalmoplegia 7. Diabetic amyotrophy/proximal neuropathy/lumbosacral plexopathy 8. Ischemic myopathy of thigh muscles D e 127. In carbon monoxide toxicity a. There is left shift of oxygen dissociation curve b. Saturation of oxygen at 50% PaO2 is decreased c. Oxygen content of arterial blood is decreased d. Induces a state of metabolic acidosis e. Oxygen is used in treatment Ref: Ganong 17th 633 Quality:::spotter thinker reader BATA Discussion Explanation a. There is left shift of oxygen dissociation curve. COHb shifts the curve of the remaining HbO2 to left decreasing the amount of O2 released by the normal saturated Hb. b. Saturation of oxygen at 50% PaO2 is decreased. I think this choice should be saturation of Hb at given PO2 is decreased which is untrue because the curve shifts to the left. This increases the saturation of Hb at givenPO2 and even makes the available HbO2 useless for oxygenation because it wont release the O2. c. Carboxu Hb reduces oxygen transportation by Hb thus Oxygen content of arterial blood is decreased. correct. d. Induces a state of metabolic acidosis because of the hypoxia e. Ventilation with O2 is preferable to ventilation with fresh air since O2 hastens the dissociation of COHb. Hyperbaric O2 is useful. 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E F ! @! ! @! @  +! ! @! !   M%a @b@%@U% U% V% @W% X% X% @Y%Y%cC,cC,C  + = G X s {bailey, Reference: and love 724g 435CcCc(C cCchcCUchcSchc'# CcCc Cc'C& cCzcCEcCcCscCRcCzc Cc23CAcCc"C/ c%SL c.C  CecCC-cCCcC@B, CcSchc+# 7#8#4#)C chcSchc0# Cchc(# ,C chc,3 035363 C`chcSDchcS.chcCchc+3 ScC@B,Cc CCXchc.# #|C:C|DERMATOLOGY 8 Questions The question distribution is as follows Dermatology had 6 questions Venerology had 2 questions Questions from AIDS are discussed with Questions from Medicine Question. 56. Acantholysis is characteristic of: 1. Pemphigus vulgaris. 2. Pemphigoid. 3. Erythema multiforme. 4. Dermatitis hepetiformis. Answer 1. Pemphigus vulgaris. Reference Reference - Harrison Table 58-1. Immunologically Mediated Blistering Diseases Also can be seen in SARP - SARP 6th Edition : Page 38 PARAS - PARAS 4th Edition : Page 151 Sure Sucess in PG Entrance 1st Edition : 201 Quality: Spotter Status: Repeat QTDF: All books give this Discussion Pemphigus Vulgairs 1. is an Auto Immune Mediated blistering skin disease(other immune mediated blistering skin diseases are Pemphigus Foliaceus, Bullous Pemphigoid, Cicatrical Pemphigoid, Dermatitis Herpetiformis, Epidermolysis Bullosa Acquista and Linera IgA disease) 2. HLA-DR4 and DRW6 3. Acantholyssis and Intraepidermal L\Blisters are haracteristic features 4. Acantholytic cells are Round cells with hyperchromatic nucleus and Perinuclear Halo 5. Nikolskys Sign is seen(Other diseases with Nikolskys Sign are Pemphigus, Pophyria, Steven Johnsons Toxic Epidermal Necrolysis, Staphylococcal Scalded Skin Syndrome) Nikolskys Sign is negative in Pemphigoid 6. Tzancks Test is used. 7. Tzancks Cell is Keratinocyte 8. IgG antibodies are seen 9. Row of Tombstones appearance is present in Pemphigus Vulgaris Explanation 1. Pemphigus vulgaris presents with Acantholysis and Intraepidermal Bullae. 2. Pemphigoid presents with subepidermal bullae IgG Antobodies are present against Basement Membrane and usually affect the elderly in 60 80 years and Mucosal Involvement is rare. There is no statistical association with internal malignancy and HLA and Direct Immunonoflourescence reveals IgG and C3 deposits . 3. Erythema multiforme is usually due to Viral(Herpes) or other Bacteria and Fungus. Lesions come in crops and last for 2 ot3 weeks,and commonly affect the face, dorsal surface of hand and feet and ecxtensor sirface of forearm and legs, palms and soles. Target Lesions (Bullets Eye lesions) are specific and they consist of 3 conventric zones of color changes and are mostly found acrally on the hand and feet in Erythema Multiformae Minor 4. Dermatitis herpetiformis presents as Intensely priiritic, chronic, papulovesicular lesions that are symmetrically distributed over extensor surfaces. Associate with gluten sensitive Enteropathy. More than 90 % express HLA B8 HLA DRW3 and HLA DQW2. Subepidermal Blisters with Neutrophils ar seen and Granular IgA deposits are seen in the dermal papillae. The IgA antibodies are against Gliadin. Treatmetn is with Dapsone and if the patient cannot tolerate Dapsone, Sulphapyridine is substituted. Diet should exclude Gluten which is present in Barley, Rye and Wheat. Oats are tolerated and Gluten is not seen in Rice Comments Though Dermatology is a bigggggggg topic, the questions that are usually asked can be answered with minimal knowledge from SARP, PARAS and Sure Success in PG. Tips PemphiguS has Superficial (Intra epidermal) blisters PemphigoiD has Deep (Sub Epidermal) blisters And among Pemphigus P.Erythematosus and P.Foliaceous show intraepidermal Acantholytic Split in Stratum Granulosum (Pnemonic EFG)and P.Vulgaris and P.Vegetans show Intraepidermal Acantholytic split in between the Basal layer and the Prickle cell layer Question. 57. A 40 year old male developed persistent oral ulcers followed by multiple flaccid bullae on trunk and extremities. Direct examination of a skin biopsy immunofluorescence showed intercellular igG deposits in the epidermis. The most probable diagnosis is: 1.Pemphigus vulgaris. 2.Bullous Pemphigoid. 3.Bullous Lupus erythematosus. 4.Epidermolysis bullosa acquisita. Answer 1.Pemphigus vulgaris. Reference Reference - Harrison Table 58-1. Immunologically Mediated Blistering Diseases Also can be seen in Pasricha 4th EditionPage 199 SARP - SARP 6th Edition : Page 38 PARAS - PARAS 4th Edition : Page 151 Sure Sucess in PG Entrance 1st Edition : 201 Quality: Spotter Status: Repeat QTDF: All books give this Discussion Pemphigus Vulgaris is due to autoimmunity directed against Cadherin Pemphigus Foliaceus is due to autoimmunity directed against Desmoglein and this Drug induced Pemphigus is seen after administration of Penicillamine and Captopril Pemphigus Vegitans is the least common Explanation 1.Pemphigus vulgaris affects the age group 25 to 50 and IgG deposits are seen. The disease starts as painful erosions in oral mucosa. Some times scalp is also involved early. Lesions appear as crops of flaccid bullae. Commonest type of Pemphigus is Pemphigus Vulgaris and there is no pruritis 2.Bullous Pemphigoid presents as Large tense blisters on flexor surfaces, oromucosal lesions. Direct Immunoflourescence show linear deposits of IgG or C3. The blister is Eosinophil rich . 3.Bullous Lupus erythematosus. 4.Epidermolysis bullosa acquisita presents with Blisters, scarring and milia on dorsum o fhands, elbows, knees and oromucosal lesions. The sub epirdermal blister can be inflammatory or not. Comments Age, Deposits in the epidermis(intraepidermal), starting in oral mucosa, flaccid bullae all point towards Pemphigus Vulgaris Tips Let us see the differences between Pemphigus and Phempigoid Features Pemphigus Pemphigoid Age 40-60 60-80 HPE-Row of Tombstones Present Absent Nikolskys Sign Present Absent Bulla Location Intraepidermal Sub Epidermal Bulla Features Flacced Tense Mucosa (eg Oral ) Involved Not involved Acantholysis Present Absent Question. 58. A 5 year old boy has multiple asymptomatic oval and circular faintly hypopigmented macules with fine scalng on his face. The most probable clinical diagnosis is: 1.Pityriasis versicolor. 2.Indeterminate leprosy. 3.Pityriasis alba . 4.Acrofacial vitiligo. Answer 3.Pityriasis alba . Reference Behl,Pg-154 Also can be seen in Pasricha Pages 124,196 SARP - SARP 6th Edition : Page 45 PARAS - PARAS 4th Edition : Page 148 Quality: Spotter Status: Repeat QTDF: All books give this Discussion Pityriasis Alba is a chronic patch of mild erythema and is characterized by Hypopigmentation and Furfuraceous scaling. The size of patch is about that of a rupee coin and is usually solitary. It affects the cheeks and chin of children, to a less extent that of adults. It is harmless , not scarring and usually non infectious. It responds slowly to treatment which consists of nourishing diet, mild sunbath, vitamins and topical mild aspetics. It is more common in winter and is a manifestation of atopy. It is self limiting Explanation 1. Pityriasis versicolor is a superficial fungal infection caused by Malassezia furfur, a yeast like, nondermatophyte dimorphic fungus. The disease is produced by the hyphal form of the fungus( and not the yeast form). Most common in the upper trunk. The hypopigmentation is due to Azaliec Acid. KOH preparation shows Spaghetti and meatballs or Bacon and Eggs appearance. Multiple macules and/or patches of variable appearance (hypopigmented, hyperpigmented, dark brown or erythematous) surrounded by normal skin are the typical lesions of pityriasis versicolor.The lesions are scaly. The extension and severity of the lesions tend to be worse in tropical climates. Affected areas include the back, chest, abdomen, neck, and upper limbs. However, classically the back carries more lesions. The face is an area commonly affected in children and it is the forehead showing mostly hypopigmented macules that is found. Uncommon but possible locations include axilla, popliteal fossa, forearms, lower limbs, radiotherapy field and penis/genitalia. The lesions are aggravated by Systemic Steroids 2. Indeterminate leprosy presents with one or few hypopigmented or erythematous macules few cm in diameter. Lepormin test is positive. And sensory loss is usually absent and the lesion may heal in one or two years. Scaling is absent. 3. Pityriasis albas classical description is given in the question. Primarily is seen in young children before the age of puberty and macules are usally located on cheeks, but may be present any where on th efface. It is scaly, non anaesthetic and usually occurs in children in hill stations 4. Acrofacial vitiligo will not have scales. Acrofacial vitiligo affects distal end of fingers and facial orifices in circumferential pattern Comments A question that is being repeated for a long time and every time there is confusion whether the answer is Pityriasis Alba or TV!! Tips Fungal disorders of Skin and the investigations are to learned from Micro Also Question. 59. The test likely to help in diagnosis of a patient who presents with an itchy annular plaque on the face is 1. Gram Stain 2. KOH Mount 3. Tissue Smear 4. Woods Lamp Examination Answer 2. KOH Mount Reference Harrison 15th Edition Page 845 Also can be seen in SARP - SARP 6th Edition : Page PARAS - PARAS 4th Edition : Page Sure Sucess in PG Entrance 1st Edition : Quality: Thinker Status: Repeat QTDF: All books Discussion Itchy annular plaque on the face is usually Tinea Versicolor or Pityriasis Versicolor, a fungal infection located to Stratum Corneum. Tinea versicolor is caused by a nondermatophyte dimorphic fungus that is a normal inhabitant of the skin. As the yeast form Pityrosporum orbiculare, it generally does not cause disease (except for folliculitis in certain individuals). However, in some individuals, it converts to the hyphal form and causes characteristic lesions. The expression of infection is promoted by heat and humidity. The typical lesions consist of oval scaly macules, papules, and patches concentrated on the chest, shoulders, and back but only rarely on the face or distal extremities. On dark skin, they often appear as hypopigmented areas, while on light skin, they are slightly hyperpigmented. In some darkly pigmented individuals, they may only appear as scaling patches. A KOH preparation from scaling lesions will demonstrate a confluence of short hyphae and round spores (so-called spaghetti and meatballs). Solutions containing sulfur, salicylic acid, or selenium sulfide will clear the infection if used daily for a week and then intermittently thereafter. Treatment with a single 400-mg dose of ketaconazole is also effective Explanation 1. Gram Stain is used for finding out bacterial Infections 2. KOH Mount is the ideal investigation here and will show Spaghetti and meatballs or Bacon and Eggs appearance 3. Tissue Smear is not needed 4. Woods Lamp Examination is also useful ,but for a fungal infection the most ideal investigation is KOH mount Comments About Woods Lamp Made up of Nickel oxide and Silica Wavelength is 360nm ULTRAVIOLET Conditions Finding Flexures Accentuated Post inflammatory Fades Vitiligo Totally white Erythrasmna(C.Minutissimum) Coral Red Tinea Capitis Brilliant Green Tinea Versicolor Dull Yellow Pseudomonas Pale Blue/Green Tuberous Sclerosis (Ash Leaf) Blue white Urine in Porphyria Cutanea Tarda Pinkish Red Tips Coup dongle sign of Besnier is seen in scaling PV ( Coup dongle means Stroke of Nail) Question. 60. An eleven year old boy is having tinea capitis on his scalp. The most appropriate line of treatment is: 1. Oral griseofulvin therapy. 2. Topical griseofulving therapy. 3. Shaving of the scalp. 4. Selenium sulphide shampoo. Answer 1. Oral griseofulvin therapy. Reference Harrisons,15th,Pg-313, 1180 KDTripathi 4th Edition : page 774 Also can be seen in SARP - SARP 6th Edition : Page 34 PARAS - PARAS 4th Edition : Page 178 Sure Sucess in PG Entrance 1st Edition : 223 Quality: Spotter Status: Repeat QTDF: All books give this Discussion Both topical and systemic therapies may be used to treat dermatophyte infection. Treatment depends on the site involved and the type of infection. (Topical therapy is generally effective for uncomplicated tinea corporis, tinea cruris, and limited tinea pedis.) It is not effective as monotherapy for tinea capitis or tinea unguium. Topical imidazoles (miconazole, ketoconazole, econazole, clotrimazole, oxiconazole, and sulconazole), triazoles (terconazole), and allylamines (terbinafine and naftifine) may all be effective topical therapies for dermatophyte infections. Haloprogin, undecylic acid, ciclopirox-olamine, and tolnaftate are also effective, but nystatin is not active against dermatophytes. Treatment should continue until the patient is clear of infection by clinical examination and culture. Tinea pedis often requires longer treatment courses and is associated with a high relapse rate. Griseofulvin is the drug of choice for dermatophyte infections requiring systemic therapy. A daily dose of 500 mg of microsized or 350 mg of ultramicrosized griseofulvin administered with a fatty meal is an adequate dose for most dermatophyte infections. The duration of therapy may be as short as 2 weeks for uncomplicated tinea corporis but may be as long as 6 to 12 months for nail infections. The most common side effects of griseofulvin are gastrointestinal distress and headache. Dermatophyte infection of hair-bearing areas (e.g., tinea capitis) requires systemic antifungal therapy. The usual adult dose of griseofulvin is 1 g of microsized or 0.5 g of ultramicrosized given daily, and treatment should be continued for 6 to 8 weeks. Children should be treated with 15 to 20 mg/kg as a single daily dose given with a fatty meal. The adjunctive use of topical antifungal agents in addition to systemic therapy may be useful, but topical therapy alone is not adequate. Markedly inflammatory tinea capitis may result in scarring and hair loss, and systemic or topical glucocorticoids may be helpful in preventing this sequela. Recent studies in children have also suggested that both itraconazole (3 to 5 mg/kg for 6 to 10 weeks) and terbinafine (125 mg/d for 6 weeks) may be effective treatments for tinea capitis. Explanation 1. Oral griseofulvin therapy is the most appropriate line. 2. Topical griseofulving therapy is not effective. 3. Shaving of the scalp in not needed. 4. Selenium sulphide shampoo can also be used, but is nothe msotappropriate. Comments Tinea capitis is caused by Trichophyton Tonsurans, Trichophyton Schoenleinii, Microsporum Audouinii There are 4 clinical patterns Seborrhoic Pattern : Black Dot Pattern : Kerion : Favus : The type of Hair invasion may be Endothrix : Invasion inside the hair shaft Ectothrix : Invasion outside the hair shaft The dermatophytosis may be 1. Non inflammatory lesions of trunk, groin, hand, feet and sole which is treated by Topical Clotrimazole, Naftifine, Terbinafine etc 2. Hyperkeratosis lesions of palm treated by Whitfield ointment 3. Ring worm treated by Systemic Therapy Tips Terbinafine inhibits a fungal enzyme, squalene epoxidase, and stops the cells making ergosterol, the main component of the cell wall. Question. 61. An 8 month old child presented with itchy, exudative lesions on the face, palms and soles, The siblings also have similar complaints. The treatment of choice in such a patient is: 1. Sytemic ampicillin. 2. Topical betamethasone. 3. Systemic prednisolone. 4. Topical permethrin. Answer 4. Topical permethrin. Reference Harrison Chapter 398 Also can be seen at SARP - SARP 6th Edition : Page PARAS - PARAS 4th Edition : Page Sure Sucess in PG Entrance 1st Edition : Quality: Spotter Status: Repeat QTDF: All books Discussion The condition in this question is Scabies and for the treatment of scabies, 5% permethrin cream is less toxic than the once commonly used 1% lindane preparations and is effective against lindane-tolerant infestations. Both scabicides are applied thinly but thoroughly behind the ears and from the neck down after bathing and are removed 8 h later with soap and water. Lindane is absorbed through the skin, and its overuse has led to seizures and aplastic anemia. It should not be applied to pregnant women or infants. Alternatives include topical crotamiton cream, benzyl benzoate, and sulfur ointments. Successful treatment of crusted scabies requires the application first of a keratolytic agent such as 6% salicylic acid (to improve the penetration of scabicides) and then of scabicides to the scalp, face, and ears (with care to avoid the eyes). Repeated treatments or the sequential use of several agents may be necessary. A single oral dose of ivermectin (200 ug/kg) effectively treats scabies in otherwise healthy persons. Patients with crusted scabies may require two or more doses of ivermectin. Although ivermectin may become the agent of choice for treating crusted scabies, it has not yet received approval by the U.S. Food and Drug Administration (FDA) for any form of scabies. Its use should be reserved for persons who fail to respond to topical scabicides, the elderly, persons with generalized eczema, and other persons who may not tolerate topical therapy. Explanation 1. Sytemic ampicillin is for the bacterial superinfection. 2. Topical betamethasone is rarely used. 3. Systemic prednisolone is used for the pruritis after the Scabicidal agents are applied 4. Topical permethrin is the treatment of choice Comments Patients with scabies report intense itching that worsens at night and after a hot shower. Typical burrows may be difficult to find because they are few in number and may be obscured by excoriations. Burrows appear as dark wavy lines in the epidermis, measure 3 to 15 mm, and end in a small pearly bleb that contains the female mite. Such lesions generally develop on the volar wrists, between the fingers, on the elbows, and on the penis. Small papules and vesicles, often accompanied by eczematous plaques, pustules, or nodules, are symmetrically distributed in these sites and in skin folds under the breasts and around the navel, axillae, belt line, buttocks, upper thighs, and scrotum. Except in infants, the face, scalp, neck, palms, and soles are spared. Burrows and other typical lesions may be sparse in persons who wash frequently, and topical glucocorticoid treatment and bacterial superinfection may alter the appearance of the rash. Atypical presentations of scabies include bullous lesions, which resemble those of bullous pemphigoid, and vesicular lesions, which resemble those of dermatitis herpetiformis. Superinfection with nephritogenic strains of streptococci has led to acute glomerulonephritis. Crusted scabies resembles psoriasis in its typical widespread erythema, thick keratotic crusts, scaling, and dystrophic nails. Characteristic burrows are not seen in crusted scabies, and patients usually do not itch, although their infestations are highly contagious and have been responsible for outbreaks of classic scabies in hospitals. Bacteremia occurs frequently in AIDS patients with crusted scabies and prominent fissures. Persons with massive infestations occasionally present with diffuse pruritus and generalized papules or with minimal or no cutaneous signs. Tips A diagnosis of scabies should be considered in patients with pruritus and symmetric polymorphic skin lesions in characteristic locations, particularly if there is a history of household contact with a case. Burrows should be sought and unroofed with a sterile needle or scalpel blade, and the scrapings should be examined microscopically for the mite, its eggs, and its fecal pellets. A drop of mineral oil facilitates removal of the sample. Biopsies or scrapings of papulovesicular lesions may also be diagnostic. In the absence of identifiable mites or mite products, the diagnosis is based on clinical presentation and history. The possibility of other sexually transmitted diseases should be excluded in adults with scabies And few points about the itch mite !!! ITCH MITE at a Glance First described in 1687 Species are o Sarcoptes scabiei o Acarus scabiei Morphology o 0.4 mm o Tortoise like body o 2 pair of legs in front Suckers o 2 pair of legs behind bristles o Male No Sucker on 3rd pair 4 stages o Egg : 30 eggs @ 2-3/day o Larva : after 3-4 days 3 legs o Nymph: 3 days o Adult : 6-8 days Live for 1 to 2 months Spread o Close Contact o Contaminated clothing Sites o Wrist, o hands, o ext genitalia Control o Benzyl benzoate 25 % o Gamma HCl 0.5 % o Tetmosol 5 % o S Oint 2.5-10 % Question. 62. The syndromic management of urethral discharge includes treatment of: 1. Neisseria gonorrhoeae and herpes genitalis. 2. Chalamydia trachomatis and herpes genitalis. 3. Neisseria gonorrhoeae and Chlamydia trachomatis. 4. Syphilis and chancroid. Answer 3. Neisseria gonorrhoeae and Chlamydia trachomatis. Reference Social Hygiene Service & AIDS Unit, Department of Health, July 1998 (adapted and modified from the World Health Organisation, Regional Office for the Western Pacific) Quality: Spotter Status: New QTDF: Syndromic Management Booklet being circulated in Institutions Discussion General Principles of Management of Patients with STD Establish the diagnosis or syndrome by history, physical examination and screen for other possible STDs (multiple concomitant STDs are common). Routine screening and counselling even in asymptomatic patients (in particular female patients) is necessary. Prompt and simple treatment (preferrably single dose). Contact tracing by patient referral. Routine screening for contacts. Epidemiologic treatment to contacts. Health education on safer sex: monogamous relationship, proper and consistent condom use, prompt and routine medical consultation after unsafe exposure. Secure follow-up for test for cure. Secure follow-up for re-test for VDRL and HIV serology at 90 days. Treating STDs Using The Syndromic Approach Syndrome Remarks Pathology Etiology In Men and Non Pregnant Women In Pregnant Woemn Men or Women Genital Ulcers Syphilis, See Comments Chancroid Tab Cipro 1 gm Stat Genital herpes Men Urethral discharge Gonorrhoea and Ceftibuten 400 mg in single oral dose OR Ceftriaxone 500 mg single i.m.i. dose + Tab Erythromycin 500mg qid x 7days Spectinomycin 2 gm single i.m.i. dose OR Chlamydia Doxycycline 100 mg orally twice daily for 7 days OR Tetracycline 500 mg orally four times daily for 7 days OR Erythromycin 500 mg orally four times daily for 7 days OR Azithromycin 1 gm orally in a single dose Men Scrotal Swelling Rule ot Torsin testis Chlamydia Doxycycline 100 mg orally twice daily for 7 days OR Analgesics Tetracycline 500 mg orally four times daily for 7 days OR Scrotal Support Erythromycin 500 mg orally four times daily for 7 days OR Gonorrhoea Azithromycin 1 gm orally in a single dose Women Vaginal discharge Speculum Examination Cervicitis: Gonorrhoea and Ceftibuten 400 mg orally in a single dose OR Ceftriaxone 500 mg single i.m.i. dose + Tab Erythromycin 500mg qid x 7days Spectinomycin 4 gm single i.m.i. dose OR Ceftriaxone 250 mg single i.m.i. dose Chlamydia Doxycycline 100 mg orally twice daily for 7 days OR Tetracycline 500 mg orally 4 times daily for 7 days OR Erythromycin 500 mg orally 4 times daily for 7 days OR Azithromycin 1 gm orally in a single dose Vaginitis: Trichomoniasis and Tinidazole 2 gm as a single oral dose to be taken at the clinic Metronidazole 400-500 mg given orally twice daily for 7 days if single dose is not effective Candidiasis Clotrimazole vaginal pessary one tab nocternal for one week Isoconazole vaginal pessary two tab intravaginally nocte for once Nystatin 100,000 unit (one pessary) intravaginally nocte daily for 14 days Fluconazole 150 mg as a single oral dose Itraconazole 200 mg daily for 3 days Women Lower abdominal pain Look for Ectopic Missed Periods Bleeding PV Gonorrhoea, As above Chlamydia As above Anaerobes Tinidazole 2 gm as a single oral dose to be taken at the clinic Metronidazole 400-500 mg given orally twice daily for 7 days if single dose is not effective Others Men or Women Inguinal Bubo Chlamydia Doxycycline 100 mg orally twice daily for 7 days OR Tetracycline 500 mg orally 4 times daily for 7 days OR Erythromycin 500 mg orally 4 times daily for 7 days OR Azithromycin 1 gm orally in a single dose Neonate Eye Discharge Gonorrhoea and Chlamydia Explanation 1. Herpes genitalis comes under the treament of Genital Ulcers . 2. Herpes genitalis comes under the treament of Genital Ulcers 3. Neisseria gonorrhoeae and Chlamydia trachomatis cause Urethral discharge and in the syndromic management of Uretheral Discharge the therapy is aimed against these two. 4. Chancroid causes Genital Ulcers. Comments Management of Syphilis Primary syphilis; Secondary syphilis; Early Latent Syphilis; Late Latent Syphilis; Neurosyphilis Ocular syphilis Procaine Penicillin 1.2 megaunit imi 1.2 megaunit imi + Probenecid 500 mg 4x / day 2.4 megaunit imi + Probenecid 500 mg 4x / day No. of days 10 15 20 Alternative Treatment Doxycycline 100 mg 2x / day Tetracycline 500 mg 4x / day Erythromycin 500 mg 4x / day Doxycycline 100 mg 2x / day Tetracycline 500 mg 4x / day Erythromycin 500 mg 4x / day Doxycycline 100 mg 2x / day Tetracycline 500 mg 4x / day Erythromycin 500 mg 4x / day No. of days 15 15 28 Tips An emerging topic and questions can be asked to you both in Entrance Exams as well as from other sources!!!! Hence is the need of this detailed tables Question. 63. The most frequent cause of recurrent genital ulceration in a sexually active male is: 1. Herpes genitalis. 2. Aphthous ulcer. 3. Syphilis. 4. Chancroid. Answer 1. Herpes genitalis. Reference Harrison 15th Edition Chapter 132, Page 845 Quality: Spotter Status: Repeat QTDF: All books Discussion Sexually transmitted herpes simplex virus (HSV) infections now cause most genital ulcer disease throughout the world and an increasing proportion of cases of genital herpes in developing countries with generalized HIV epidemics, where the positive feedback loop between HSV and HIV transmission is a growing, intractable problem. Herpes Simplex type II is the most common cause of genital ulcer in developing countries. Disease % Herpes 62 & Chanchroid 12 to 20 % Syphilis 13 % LGV and Granuloma Inguinale Herpes Ulcers are painful, vesicular, multiple and are associated with firm tender lymphadenopathy Explanation 1. Herpes genitalis is the most common cause. 2. Oral lesions, including thrush, hairy leukoplakia, and aphthous ulcers, are particularly common in patients with untreated HIV infection.. 3. The typical primary chancre usually begins as a single painless papule that rapidly becomes eroded and usually becomes indurated, with a characteristic cartilaginous consistency on palpation of the edge and base of the ulcer (see Plate IID-47, Fig. 172-CD1). In heterosexual men the chancre is usually located on the penis, whereas in homosexual men it is often found in the anal canal or rectum, in the mouth, or on the external genitalia. In women, common primary sites are the cervix and labia. Consequently, primary syphilis goes unrecognized in women and homosexual men more often than in heterosexual men.. 4. Infection in Chancroid is acquired as the result of a break in the epithelium during sexual contact with an infected individual. a. After an incubation period of 4 to 7 days, the initial lesion-a papule with surrounding erythema-appears. b. In 2 to 3 days, the papule evolves into a pustule, which spontaneously ruptures and forms a sharply circumscribed ulcer that is generally not indurated. c. The ulcers are i. painful and ii. bleed easily; iii. little or no inflammation of the surrounding skin is evident. d. Approximately half of patients develop i. enlarged, ii. tender inguinal lymph nodes, which frequently become iii. fluctuant and iv. spontaneously rupture. e. The presentation of chancroid does not usually include all of the typical clinical features and is sometimes atypical. i. Multiple ulcers can coalesce to form giant ulcers. ii. Ulcers can appear and then resolve, with inguinal adenitis and suppuration following 1 to 3 weeks later; this clinical picture can be confused with that of lymphogranuloma venereum. iii. Multiple small ulcers can resemble folliculitis. iv. Other differential diagnostic considerations include the various infections causing genital ulceration, such as primary syphilis, condyloma latum of secondary syphilis, genital herpes, and donovanosis. v. In rare cases chancroid lesions become secondarily infected with bacteria; the result is extensive inflammation. Comments Donovanosis is caused by Calymmatobacterium granulomatis, an o intracellular, o gram-negative, o pleomorphic, o encapsulated (when mature) bacterium o measuring 1.5 by 0.7 um. C. granulomatis shares many morphologic and serologic characteristics and >99% homology at the nucleotide level with Klebsiella species that are pathogenic to humans. o Polymerase chain reaction amplification of the phoE gene shows it to be closely related to that in Klebsiella pneumoniae, K. rhinoscleromatis, and K. ozaenae. o Electron microscopy shows typical gram-negative morphology and a large capsule but no flagella. Filiform or vesicular protrusions occur on a corrugated cell wall. The incubation period is usually 1 to 4 weeks but may extend to 1 year. Skin lesions have been detected in infants 6 weeks to 6 months after birth. The disease begins as one or more o subcutaneous nodules that erode through the skin to produce o clean, o granulomatous, o sharply defined, o usually painless lesions. o bleed readily on contact, o slowly enlarge. The genitalia are involved in 90% of cases, the inguinal region in 10%, and the anal region in 5 to 10%. o Genital swelling, particularly of the labia, is a common feature and occasionally progresses to pseudoelephantiasis. o Phimosis and paraphimosis are common local complications, and progressive erosion of affected tissues may completely destroy the penis or other organs. Less common clinical variants include a o hypertrophic form (cauliflower- or wartlike lesions), o a necrotic form (destructive lesions with foul-smelling exudate, often resembling amebiasis), and a sclerotic or cicatricial form, which has a dry base with extensive scar tissue Tips Read about Syphilis and other diseases from Davidson and SARP, PARAS and Sure Success in PG ENT 5 Questions Analysis of the 5 questions show Ear 3 Nose 0 Throat 2 Of these only the question on Thyroplasty was for ENT Surgeons. The other 4 were repeats and could have been easily attempted. Questions on Tuning fork Tests are conspicuous by their absence Question. 69. A 5-year-old boy has been diagnosed to have posterior superior retraction pocket cholesteatoma. All would constitute part of the management, except: 1. Audiometry. 2. Mastoid exploration. 3. Tympanoplasty. 4. Myringoplasty. Answer 4. Myringoplasty. Reference Logan Turner Page 289 Fundamentals of Ear, Nose, Throat and Head and Neck Surgery - S.K.De - 7th Edition Page 123 Diseases of Ear, Nose and Throat. P.L.Dhingra - 2nd Edition Pages 35,75 Quality: Reader Status: Repeat QTDF: De Discussion Ear Perforations can be regarded as safe if they are central perforations or Tubotympanic type and unsafe if they are of attico antral type or associated with cholesteotoma. This boy in our Question has Unsafe type of CSOM. The objectives of the surgical management will be to 1. To remove the disease focus 2. To reconstruct the ear as far as possible, but not at the cost of objective 1. The management of such cases would consist of 1. Evaluation Radiological and Audiometry 2. Atticotomy 3. Modified Radical mastoidectomy 4. Tympanoplasty Explanation 1. Audiometry is needed for medicolegal purposes as we are doing a destructive or quasidestructive surgical procedure and we want to document that the patient already had a hearing loss as a consequence of the disease 2. Mastoid exploration is an essential part of management. 3. Tympanoplasty is done for reconstruction. 4. Myringoplasty is not done in cases of Unsafe Ear. It is done only in cases of Safe ear Comments Let us see the types of tympanoplasty Type Defect Procedure I Central perforation Repaired with a graft. Also called as Myringoplasty II Perforation of TM with Erosion of Malleus Graft is placed on Incus or remnant of Malleus III Perforation of TM with Absence of Malleus and Incus Graft is placed directly on head of Stapes IV Only Foot plate of Stapes is present Graft is placed in Foot plate of Stapes And round window is separated V Foot plate of Stapes is fixed. And Round window is functioning Another window is created in the horizontal canal Also called as Fenestration Operation Tips Myringoplasty is done is safe ear or tubotympanic type or central perforation Question. 70. Carharts notch in audiogram is deepest frequency of: 1. 0.5KHz 2. 2 KHz. 3. 4 KHz. 4. 8 KHz. Answer 2. 2 KHz. Reference Fundamentals of Ear, Nose, Throat and Head and Neck Surgery S.K.De 7th Edition Page 141 Diseases of Ear, Nose and Throat. P.L.Dhingra - 2nd Edition Page 93 Figure 13.2 Quality: Reader Status: Repeat QTDF: Dhingra Discussion Otosclerosis is a disease of the bony labynth where there are few bone changes Normal Bone Otosclerosis Normal :-) Abnormal :-( Dense Spongy Avascular Vascular Regualr Irregular Epidemiology It is more common is females More common around puberty More common in whites (The only use of remembering these American Statistics is for your Entrance Exams!!) Symptoms Hearing Loss o Painless, o Progessive o Insidous Onset o Bilateral o Conductive type Paracuses Williss the patient hears well in noisy surroundings Tinnitus Vertigo Monotonous Speech Signs Tympanic Membrane is NORMAL in most of the cases (Remember that this is the most common finding and the Schwartz sign though classical is not seen in all cases) Schwartz Sign may be seen It is a Reddish Blue or Flamingo Pink Tinge seen on the promontory through TM Cahartz notch is seen in Bone conduction curve. There is a dip in the conduction at various frequencies and the maximum dip occurring at the frequency of 2000 Hz or 2 Khz is called as Cahartz Notch Treatment See the discussion for the next question Explanation 1. 0.5KHz is not Cahartz Notch 2. Cahartz notch is at 2 KHz. 3. In noice induced hearing loss there is a curve at 4 KHz. 4. 8 KHz is not Cahartz Notch. Comments Bone Conduction is normal in Otosclerosis except in the Cochlear Variant Tips The notch at 4 Khz seen in Noice Induced Hearing loss is called as Boiler Makers Notch Question. 71. A 31-year-old female patient complaints of bilateral impairment of hearing for the past 5 years. On examination, tympanic membrance is normal and audiogram shows a bilateral conductive deafness. Impedance audiometry. Shows as type of curve and acoustic reflexes are absent. All constitute part of treatment, except: 1. Hearing aid. 2. Stapedectomy. 3. Sodium Fluoride. 4. Gentamicin. Answer 4. Gentamicin. Reference Fundamentals of Ear, Nose, Throat and Head and Neck Surgery S.K.De 7th Edition Page 141 Diseases of Ear, Nose and Throat. P.L.Dhingra - 2nd Edition Page 91 Quality: Reader Status: Repeat QTDF: De Discussion It needs just Basic ENT knowledge to understand that this is a case of Otosclerosis. And Otosclerosis is managed by Stapedectomy, which is the treatment of choice. Few patients who refuse surgery or are unfit for surgeries are managed by Hearing Aid. Sodium Flouride is used to arrest the progress of the disease Explanation 1. Hearing aid is used for those who refuse surgery or those who are unfit for surgery. 2. Stapedectomy is the treatment of choice. 3. Sodium Fluoride is used in the medical management to arrest further Otoscleosis but is not curative 4. Gentamicin has no role to play. Comments Let us see a Few points about Stapedectomy. In fixed Otosclerosis, the stapes is removed and a prosthetic is inserted between Incus and Oval Window. The prosthesis can be Teflon piston, stainless steel piston, tefwire or fat and stainless steel wire. In 90 % there is good improvement The indications are 1. AB Gap > 30 dB 2. Rinne Negative for 256 Hz and 512 Hz 3. Good cochlea The Steps of Stapedectomy are 1. Meatal Incision and Elevation of Tympanomeatal Flap 2. Exposure of Stapes Removal of Posterosuperior bone overhanging of canal 3. Removal of Stapes superstructure 4. Creation of hole in Stapes foot plate Stapedotomy or Removal of a part of foot plate Stapedectomy 5. Placement of Prosthesis 6. Repositioning of Tympanomeatal Flap Few more points 1. 2 % there may be sensorineural loss 2. Stapes Mobilisation gives temporary results 3. Fenestration operation is an outdated procedure in which a window is created in the lateral semicircular canal Tips Another theme couple where two questions are asked from the same topic - Otosclerosis Question. 72. A middle-aged male comes to the outer patient department (OPD) with the only complaint of hoarseness of voice for the past 2 years. he has been a chronic smoker for 30 years. On examination, a reddish area of mucosal irregularity overlying a portion both cords was seen. Management would include all except: 1. Cessation of smoking. 2. Bilateral cordectomy. 3. Microlaryngeal surgery for biopsy. 4. Regular follow-up. Answer 2. Bilateral cordectomy. Reference Fundamentals of Ear, Nose, Throat and Head and Neck Surgery S.K.De 7th Edition Page 441 Diseases of Ear, Nose and Throat. P.L.Dhingra - 2nd Edition Page 305 Quality: Reader Status: Repeat QTDF: Dhingra Discussion The probable diagnosis is Vocal Cord Papilloma or if you give more significance to the history of him being a smoker, then the diagnosis will move towards premalignant lesion Such a condition is managed by Cessation of Smoking Microlaryngeal surgery for o Biopsy Follow up Radiotherapy if the biopsy turns out to be Malignant Explanation 1. Cessation of smoking is a must. 2. Bilateral cordectomy is not needed. 3. Microlaryngeal surgery for biopsy is indicated. 4. Regular follow-up is a must in any case of premalignant lesions. Comments No question paper will be complete without a question on Neoplasia in ENT (as well as in Ophthal and Ortho), even though the number of questions asked in these subjects are not as high as in Medicine and Surgery. And to score marks in these areas is very simple as the amount to be studied is limited and there is little scope of a controversy arising from these topics Tips Go through the TNM Stages of the common tumours of ENT Question. 73. Type I Thyroplasty is for: 1. Vocal cord medialization. 2. Vocal cord laterlization. 3. Vocal Cord shortening. 4. Vocal cord lengthening. Answer 1. Vocal cord medialization. Reference Stell and Marans Head and Neck Surgery 4th Edition Scott and Brown 6th Edition Pages 5,6,20,21 Quality: MS ENT !!! Status: New QTDF: Stell and Marans Head and Neck Surgery 4th Edition Scott and Brown 6th Edition Pages 5,6,20,21(Are we supposed to read these books) Discussion Isshikis Type I Thyroplasty is used for Vocal Cord Medialisation. The complication following that surgery is airway obstruction Explanation 1. Vocal cord medialization. Is Type I Thyroplasty 2. Vocal cord laterlization. Is by Laser Cordectomy, Cordotomy, Cordopexy or Arytenoidectomy 3. Vocal Cord shortening is Type III Thyroplasty. 4. Vocal cord lengthening is Type IV Thyroplasty. Comments Thyroplasty is a surgical method of restoring vocal quality by altering the geometry of the thyroid cartilage. Type Vocal Cord Procedure I Medialisation II Lateralisation III Shortrening IV Lengthening Tips ENT will have few questions which may be unanswerable, but please note that there are very few people who can answer these and these kind of questions will not turn out to be a decider. On the other hand if you miss out a question on Tumours or Tuning fork tests, you will lag behind and may even be pushed out of the race FORENSIC MEDICINE 9 Questions Few Words Regarding Forensic Medicine I am giving references from 2 books. 1. The Essentials of Forensic Medicine and Toxicology by Narayana Reddy and 2. Principles of Forensic Medicine by Apurba Nandy 1st Edition Nandy is a complete book and those who are in the Idea of going to Govt Services (that means you have to be Medico legal experts may better read Apurva Nandy) The Pages of Narayana Reddy are not mentioned because, to the best of my knowledge, if there is a group of five people preparing for PG Entrance, it is certain that there are five editions!!! Questions in AIPG 2003 Came from 1. Medical Ethics - 1 Question 2. Identification - 1 Questions 3. Firearms - 1 Question 4. Post mortem changes - 4 Questions 5. Toxicology - Snakes - 1 Question 6. Forensic Psychiatry - 1 Question All the questions were spotters and all are repeats 8 out of the 9 questions (except section 193 for Perjury) had been asked more than once and are given in SARP, Sure Success in PG and in PG Entrance Made Easy. One question is directly from Parikh Question. 69. Perjury means giving willfull false evidence by a witness while under oath, the witness is liable to be prosecuted for perjury and the imprisonment may extend to seven years. This falls under which section of IPC? 1. 190 of Indian Penal Code. 2. 191 of Indian Penal Code. 3. 192 of Indian Penal Code. 4. 193 of Indian Penal Code. Answer 4. 193 of Indian Penal Code. Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 2 about recording evidence Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 7 Quality: Spotter Status: Repeat QTDF: All books Discussion Medico legally relevant Indian Penal Codes and Crime Penal Codes Please note that the codes marked bold also deal with Poisons (Toxicology) Cr.PC Pertaining to 39 Every person, aware of the commission of, or of the intention of any other person to commit any offence punishable under IPC shall forwith give information to the nearest Magistrate or police officer of such commission or intention 40 Poisons 174 Inquest 175 Poisons 174 Death in Police Custody IPC Pertaining to 35 Poisons 44 Injury 82 No Criminal responsibility below 7 years 83 Children with normal maturity between 7 and 12 with normal maturity - responsible 84 Criminal Responsibility of Insane-McNaughten 84 Intoxication without knowledge/against will 85 Voluntarily taking alcohol 87 Below 18 years no valid consent for physical examination 88-93 Legal protection to Medical Doctors 89 Consent from Guardians for age below 12 90 Validity of Consent - fear, Intoxication etc 118 Concealing design to commit offence punishable with death or imprisonment for life 176 Poisons 177 Furnishing False Information 178 Refusing Oath or affirmation when duly required by public servant to make it 179 Refusiong to answer public servant authorised to question 182 False information with aan intent to cause public servant to use his lawful power to the injury of another person 190 Threat of injury to induce person to refrain from applying for protection to public servant 191 Giving false evidence. 192 Fabricating false evidence 193 Punishment for false evidence 7 years 194 Giving or fabricating false evidence with intent to procure conviction of capital offence 195 Giving or fabricating false evidence with intent to procure conviction of offence punishable with imprisonment for life or imprisonment 197 Issuing or signing False Certificate 201 Causing disappearence of evidence of offence or giving false information to screen offenders 202 Not informing Police 203 Giving false information respecting an offence committed 204 Destruction of document to prevent its production as evidence 272 Adulterating Food or Drink (6 months/Rs 1000) 273 Selling adulterated food or drink 274 Adulteration of drugs (in West Bengal - life imprisonment) 275 Selling Adulterated drugs 276 Selling a different drug 277 Fouling Water / Spring / Reservoir 278 Making Atmosphere noxious 284 Negligent Act with respect to Poisons 294 Punishment for Exhibitionism 299 Culpable Homicide not amounting to murder {Likely to cause death} for example 1.Provocation( e.g. Adultery) 2.Exceeding personal limits (Private Defence)3.Heat of Passion (Argument) 4. Consent (Euthanasia) 300 Murder {Sufficient to cause death} / Infanticide 302 Punishment for Murder / Infanticide 303 When a life imprisonment prisoner kills another prisoner (removed from IPC now) 304 Punishment for Culpable homicide 304 A Criminal Negligence/Rash & Negligent Act 304 B Dowry Death 306 Abetment of Suicide 309 Attempt for Suicide 312 Medical Negligence / Causing Miscarriage 313 Causing Miscarriage without the consent of the female 314 Death by an act done for miscarriage 315 Act to prevent child birth or to cause it die 316 Death of quick unborn child / Criminal Abortion 317 Abandoning Infant 318 Concealment of Birth / Punishment for Abandonment 319 Hurt 320 Grievious Injury 323 Punishment for Hurt 324 Dangerous weapons / Poisons / Corrosives 325 Punishment for Grievious Injury 326 Dangerous weapons / Poisons / Corrosives 328 Poisons 331 ? Assault 351 Assault Definition 354 Punishment for Indecent Assault 355 Punishment for Indecent Assault 361 Rape is a punishable Offence / Kidnap of minor(boy below 16 and girl below 18) 366 A Kidnapping an Indian girl below 18 for Prostitution 366 B Importing any foreign girl below 21 for Prostitution 369 Kidnap a child below 10 years for movable property 375 Rape 376 Punishment for Rape 376 A Man with his wife during separation 376 B Public servant with women in custody 376 C Superintendent of Jail, Remand Home 376 D Member of the management or staff of a hospital with any women in that hospital 377 Unnatural Offences / Lesbianism 420 !!!! 493 Cohabitation by deceitfully inducing to a belief of lawful marraige 497 Adultery / Artificial Insemination 498 A Dowry death Relatives Indian Evidence Act 32 Dying Declaration Year Opium Act/ Other Regulations 1843 Mc Naughtens Rule 1857 Only the central govt can cultivate opium 1878 Import export of opium prohibited 1919 Import Export permitted 1919 Indian Medical Degrees Act 1923 Workmens Compensation act 1930 Dangerous Drugs 1933 Indian Medical Councils Act - Uniform Standard 1933 Dangerous Drugs 1938 Dangerous Drugs 1940 Drugs and Cosmetics 1948 Declaration of Geneva 1948 ESI 1948 Indian Factory Act 63 1950 Drug Control Act for Maximum Price 1951 Plantation Labour Act 1954 Durham 1954 Drugs and Magic Remedies not for Abortion, Contraception, Increased Sex, Menstruation, Venereal Diseases 1955 Medicinal and Toilet preparation Act 1956 Indian Medical Councils Act 1960 Court for Juvenile Offenders 1960 Geneva Convention Act - Red Cross Emblem 1962 Drugs and Cosmetics 1964 Durham 1971 Acccepted by West Bengal ( 9.2.1971) 1974 Bengal Medical Act 1986 COPRA Drugs and Schedules C Biological and Special Products H Poisons L Antibiotics, Antihistamines Explanation 1. IPC 190 deals with Threat of injury to induce person to refrain from applying for protection to public servant 2. IPC 191 deals with Giving false evidence. 3. IPC 192 deals with Fabricating false evidence. 4. IPC 193 deals with Punishment for false evidence. And reads Whoever intentionally gives false evidence in any stage of a judicial proceeding, or fabricates false evidence for the purpose of being used in any stage of a judicial proceeding, shall be punished with imprisonment of either description for a term which may extend to seven years, and shall also be liable to fine, and whoever intentionally gives or fabricates false evidence in any other case, shall be punished with imprisonment of either description for a term which may extend to three years, and shall also be liable to fine. Comments Though IPCs 190 to 229 deal with FALSE EVIDENCE AND OFFENCES AGAINST PUBLIC JUSTICE., the punishment of Perjury is mentioned in Section 193 Tips A complete list of IPCs is found at www.rxpg.com www.rcpgonline.com and www.targetpg.com Question. 70. The most reliable criteria in Gustafsons method of identification is: 1.Cementum apposition. 2.Transparency of root. 3.Attrition. 4.Root resorption. Answer 2.Transparency of root. Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 4 about Gustafsons Method Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 63 Quality: Spotter Status: Repeat QTDF: All books Discussion After 21 years, age can be determined by examining few characteristic features in the teeth. Gustafsons method uses the following 1. Attrition 2. Periodontitis 3. Secondary Dentine 4. Root Resorption 5. Cementum Apposition 6. Transparency of Root Even though, there are individual criteria in each of these, they are beyond the scope of this book and interested reader may please refer Principles of Forensic Medicine 1st Edition by Apurva Nandy Miles remarked that of all the criteria used by Gustafson, Transparency or Translucency of Root is the single most dependable criteria Explanation 1.Cementum apposition. 2.Transparency of root is the most reliable 3.Attrition. 4.Root resorption . Comments Since Questions from Gustafsons method may not go beyond this, let us see something more important and more often asked. Permanent 3M 2M 1M 2PM 1PM Can Lat In Med In Med In Lat In Can 1PM 2PM 1M 2M 3M Years 17-25 12-14 6 10 9 11 8 7 7 8 11 9 10 6 12-14 17-25 Temporary 2M 1M Can Lat In Med In Med In Lat In Can 1M 2M Months 24 12 18 8 7 7 8 18 12 24 Months 24 12 18 9 6 6 9 18 12 24 Temporary 2M 1M Can Lat In Med In Med In Lat In Can 1M 2M Years 17-25 12-14 6 10 9 11 8 7 7 8 11 9 10 6 12-14 17-25 Permanent 3M 2M 1M 2PM 1PM Can Lat In Med In Med In Lat In Can 1PM 2PM 1M 2M 3M Legend: 1. 3M is Third Molar, 2PM is Second Premolar, Can is Canine 2. For Temporary Teeth (Shown in the Inner four rows, the numbers refer to the months) Few more points 1. Third Molar is the Wisdom Teeth 2. Other methods used in relation to the teeth are the a. Boydes Formula b. Stacks Method Tips About Mixed Dentition 1. Mixed Dentition occurs from Eruption of First Permanent teeth (First Molar) to the Last Canine 2. Remember that the total number of teeth increase only when the Permanent Molars erupt. It is because all other permanent teeth erupt by pushing out a milk teeth 3. The number of teeth increases from 6 months to 2 years and at two years it is 20 (5 x 4) 4. At the sixth year, the number increases from 20 to 24, because the first molar erupts and no tooth falls (Remember that there are 4 first molars- Upper Right, Upper Left, Lower Right, Lower Left) 5. From 7 to 12 years the number remains 24 because as and when a tooth erupts, it displaces another and the number remains constant. 6. There is an addition of more from the age of 12 to 14 when the second Molar erupts and the total number becomes 28 7. Then the number remains constant till 17 and again 4 more are added from 17 to 25 and the number is 32 Question. 71. Blackening and tattooing of skin and clothing can be best demonstrated by 1. Luminol spray 2. Infra red photography 3. UV light 4. Magnifying lens Answer 2. Infra red photography Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 4 Identification Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 196 Parikh 6th Edition Page 2.37 Quality: Spotter Status: Repeat QTDF: Apporva Nandy Discussion A large part of the spectrum and its relationship to the world around us is invisible because we are limited to seeing electromagnetic wavelengths which extend only from those characteristic of violet-blues to those of the deep reds. Photographic materials can extend our vision, especially when aided by special light sources and various filters. Explanation 1. Luminol spray is used in detecting the blood stains. Luminol is a chemical that glows greenish-blue when it comes into contact with blood even traces that are years old. To be exact, it reacts to hemoglobin. Luminol is so sensitive, it can detect blood at 1 part per million. In other words, if there is one drop of blood within a container of 999,999 drops of water, luminol will glow. Investigators typically use luminol at crime scenes where no blood is visible. They spray the chemical over a wide area in near-total darkness, so any reaction is obvious. Officers then photograph or videotape the result, using a flash technique that picks up the glow while making the area around it visible and identifiable on film, so the context of the crime scene isnt lost. But does a glow mean theres blood present? Not necessarily. Luminol reacts to some metals, paints, cleaning products and plant matter. However, the chemicals reaction to each differs in intensity; metals, for example, cause an immediate glow that quickly fades, while blood glows longer. A specialist can tell the difference, and then perform more conclusive tests to determine whether the blood is human. 2. Infra red photography uses films that are sensitive to both the light we can see and some of the longer length (above 700 nm) infra-red radiation. The film is also sensitive in the UV region (below 400 nm). There are scientific uses for such films which include forensic applications and aerial crop and forest surveys. Here the absorption bands are numerous which gives a very complex pattern of the graph for each material tested. It is used to find heat 3. UV light is also used for forensic purposes. It is commonly used in seeing Tattoo marks, Scars, Illegible ink etc 4. Magnifying lens can be used for a whole lot of purposes. Comments This is a question, which unless carefully read will misguide you. The question asks blackening and tattooing which are seen in firearm injuries (for which infra red is the preferred choice) and not the Tattoo marks made in the skin, which are read by uv lamp Tips Even though the topic is very small. A lot of Questions are being asked from Firearm. This is best studied from Apurva Nandy. Question. 72. Mummification refers to: 1. Hardening of muscles after death. 2. Colliquative putrifaction. 3. Saponification ofsubcutaneous fat. 4. Dessication of a dead body. Answer 4. Dessication of a dead body. Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 7 about postmortem changes Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 166 Parik 6th Edition 9.40 to 9.44 Quality: Spotter Status: Repeat QTDF: All books Discussion Mummification is a process of rapid drying of the dead body due to environmental factors, when the soft tissue becomes dark, hard and stay preserved. The dry, hard skin gets almost adhered with the underlying bones Explanation 1. Hardening of muscles after death is Rigor Mortis. 2. Colliquative putrifaction is seen in the brain. 3. Saponification of subcutaneous fat is Adipocere formation. It occurs in a. Areas where there is moisture b. Relative Dimunition of Air c. Bacteria and Fat splitting enzyme 4. Dessication and dehydration of a dead body is Mummification. It occurs in a. High temperature b. Low moisture c. Free Air circulation around the body (increasing the circulation) Comments Mummification helps in identification, and the place of disposal can be guessed Tips Post mortem changes are the source of maximum number of Questions from Question. 73. In suspected case of death due to poisoning where cadaveric regidity is lasting longer than usual, it may be a case of poisoning due to: 1. Lead. 2. Arsenic. 3. Mercury. 4. Copper Answer 2. Arsenic. Reference Parikh 6th Edition Page 9.10 Quality: Spotter Given Only in Parikh Status: Repeat QTDF: Parikh Discussion In Acute Arsenic Poisoning, Rigor Mortis lasts longer than usual Explanation 1. Lead.does not delay Cadaveric Spasm 2. In Acute Arsenic Poisoning, Rigor Mortis lasts longer than usual 3. Mercury does not delay Cadaveric Spasm. 4. Copper does not delay Cadaveric Spasm Comments Petechial haemorrhages under the endocardium of the left ventricle are important points for diagnosis Tips With modern day Advances in Forensic Medicine, Arsenic can hardly used as a Homicidal poison, as it can be easily detected Question. 74 Post mortem lividity is unlikely to develop in a case of 1. Drowning in well 2. Drowning in fast flowing river 3. Post mortem submersion 4. Drowning in clorinated swimming pool Answer 2. Drowning in fast flowing river Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 7 about postmortem changes Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 151 Parikh 6th Edition 3.10 Quality: Spotter Status: Repeat QTDF: All books Discussion Hypostasis is discolouration of the skin and organs after death due to accumulation of fluid blood in the dependent parts of the body. Post mortem lividity is also called Post mortem hypostasis Livor Mortis Vivices Suggilation Postmortem Staining Explanation 1. Postmortem lividity develops in Drowning in well 2. Postmortem lividity does not develop in Drowning in fast flowing river as the position of the body is constantly changing 3. Postmortem lividity develops in Post mortem submersion 4. Postmortem lividity develops in Drowning in clorinated swimming pool Comments The colour normally is at first Bluish pink, then Bluish purple The colour of the lividity changes in Poisoning due to various agents are Pink Cyanide Bright Cherry Red Carbonmonoxide Color of the skin is bright cherry-red if saturation of carbonmonoxide in the blood is > 30%. If < 20%, then such a coloration is not visible Reddish Brown Aniline, Nitrites Chocholate Brown Potassium Chlorate Dark Brown Phosphorus Greyish Brown Septic abortin caused by C. welchii Black Opiates Bluish green Hydrogen Sulphide Tips Contact palor is a phenomenon which refers to the paleness of the areas that are in direct contact with the surface. This is similar to Contact Flattening in Rigor Mortis Question. 75 The following situations are associated with rise of temperature after death EXCEPT 1. Burns 2. Heat Strokes 3. Pontine Hemorrhage 4. Septicemia Answer 1. Burns Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 7 about postmortem changes Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 150 Parikh 6th Edition Page 3.29 to 6.31 Quality: Spotter Status: Repeat QTDF: All books Discussion In certain conditions, instead of promoting the process of cooling of the body, act in a way, so that, the body temperature is either high at the time of death or is increased for sometime after death, so that, at a particular time after death the body may appear disproportionately warmer than what it should have been. This is termed as Post Mortem Caloricity and the conditions are 1. Post mortem Glycogenolysis a. This is a normal phenomenon and the rise is 3.6oF or 2oC 2. Various Causes of Death such as a. Septicaemia, i. Infectious diseases, ii. Bacteremia iii. Tetanus b. Asphyxial Conditions c. Severe convulsions i. Tetanus ii. Strychnine d. Hyperpyrexia at death i. Heat Stroke ii. Pontine Haemorrhage e. High Atmospheric Temperature Explanation 1. Burns does not cause post mortem caloricity 2. Heat Stroke is a cause of post mortem caloricity 3. Pontine Hemorrhage is a cause of post mortem caloricity 4. Septicemia is a cause of post mortem caloricity Comments Early cooling of the body delays the process of Rigor Mortis and Decomposition. When the heat of the body is preserved, the process of Rigor Mortis and Decomposition start Early Tips Site used for recording internal temperature Rectum 4 above Anus Subhepatic Thermometer used Chemical Thermometer Graduation- 0oC or 50oC Question. 76. A patient has been allegedly bitten by cobra snake. The venom in such a bite would be: 1. Musculotoxic. 2. Vasculotoxic. 3. Cardiotoxic. 4. Neurotoxic. Answer 4. Neurotoxic. Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 29 Organic Irritant Poisons Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 7 Parikh 6th Edition 9.40 to 9.44 Quality: Spotter Status: Repeat QTDF: All books Discussion The poisons of Snakes can be 1. Neutotoxic a. Seen in i. Cobra ii. Krait b. Venom i. Paralysis of Muscles of face ii. ResemblesCurare iii. Symptoms at the site of bite is minimal iv. Krait only paralysis v. Cobra convulsions and Paralysis 2. Vasculotoxic a. Seen in i. Viper b. Venom i. Enzymatic destruction of cell wall ii. Coagulation disorders iii. Acts on Endothelial cells and RBC hemoilysis iv. Symptoms at the site of bite are severe v. Cellulitis may be seen 3. Myotoxic a. Seen in i. Seasnake b. Venom i. Myalgia ii. Myoglobulinuria iii. Respiratory Failure Explanation 1. Venom of Sea snake is Musculotoxic. 2. Venom of Vipers are Vasculotoxic. 3. Cardiotoxins are seen in venomo ffew snakes 4. Venom of Neurotoxic. Comments The other substances seen in venom of snakes are Neurotoxin Hemolysin Proteolysin Fibrinolysin Cholinesterase Coagulase Cardiotoxin Nucleotidase Hyaluronidase Phospholipase A Tips Snakes are such an important topic in FM that one can hardly set a question paper (MCQ as well as theory) without asking a question from that. Be prepared to face a question about what snake belongs to Elapidae and and what is Viviparous !!! Question. 77. All the following are related to legal responsibility of an insane person except. 1. Mc Naughtens rule 2. Durham s rule. 3. Currens rule. 4. Rule of nine. Answer 4. Rule of nine. Reference The Essentials of Forensic Medicine and Toxicology by Narayana Reddy Chapter 21 Forensic Psychiatry Principles of Forensic Medicine by Apurba Nandy 1st Edition Page 381 Parikh 6th Edition Pages 6.29 to 6.31 Quality: Spotter Status: Repeat QTDF: All books Discussion There are few laws which deal with situations where one has to deal with persons who dont have a sound mind and McNaughtens Rule, Durhams Rule and Currens Rule deal with those situations Explanation 1. Mc Naughtens rule states Every man is to be presumed to be sane, and to possess a sufficient degree of reason to be responsible for his crimes, until the contrary be proved to the satisfaction of the Jurors; and that to establish a defense on the ground of insanity, it must be clearly proved tahgt at the time fo committing the act, the party accused was labouring under such a defect of reason, from the defect of mind, as not to know the nature and quality of the act, he was doing or, if he did know it, that he did not know he was doing what was wrong. It is similar to IPC 84 that states Nothing is offence which is done by a person who at the time of doing it by reason of unsoundness of mind is incapable of knowing the nature of act, or that he is doing what is either wrong or contrary to law 2. Durham s rule of 1954 States that an accused person is not criminally responsible if his unlawful act is the product of mental disease or mental defect. 3. Currens rule of 1964 states that an accused person is not criminally responsible, if a the time of commiting the act, he did not have the capacity to regulate his conduct to the requirements of the law, as a result of mental disease or defect. 4. Rule of nine is used for assessing the burns. The percentage of area attributed to different parts are Head and Neck - 9 % of the total body area Front of Chest - 9 % of the total body area Back of Chest - 9 % of the total body area Front of Abdomen - 9 % of the total body area Back of Abdomen - 9 % of the total body area Right Upper Limb - 9 % of the total body area Left upper Limb - 9 % of the total body area Right Thigh - 9 % of the total body area Left Thigh - 9 % of the total body area Right Leg - 9 % of the total body area Left Leg - 9 % of the total body area Pudental Area - 1 % of the total body area Comments Generally Increase in Depth of Burns leads to increased Morbidity and Increase in Area of Burns leads to increased Mortality Males can withstand burns better than females Tips There are various classification of Burns. Aspirants should know atleast Dupuuytrens and Wilsons Medicine 49 Questions However note that there is no clear demarcation as to whether a question has come from Medicine or one of the allied subjects such as Microbiology, Pathology, Pharmacology or Paediatrics. A break up shows that 15 questions (30%) came from Clinical Topics and this makes Hutchison and Macleod Important books. It may appear as if few topics have not contributed. The truth is that those questions are elsewhere (GIT along with Surgery) Theory Clinical Total General 3 2 5 Infection 2 0 2 Hematology 3 3 6 Cardiology 7 7 14 Resp 9 0 9 GIT / Liver 0 0 0 Kidney 2 0 2 Neurology 3 3 6 Immunology 4 0 4 Endocrinology 1 0 1 34 15 49 Question 78. Which of the following symbol represent adopted individuals: [* | In-line.WMF 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Answer 4. [?][o] Reference Ahuja 5th Edition Page 8 http://wwwrhjh.lkwash.wednet.edu/homehelp/familytree/sld011.htm Quality: Reader Status: New QTDF: Ahuja Discussion Please see the symbols used for Pedigree Chart. From any standard text book. Explanation Self Explanatory Comments Picture Questions for the first time and that too a question from the latest edition of Ahuja Tips There are a few other symbols used in Medicine. Please go through the symbols used for marking Findings in Examination of Respiratory System from Golwalia and Krishna Das Question 79. All of the following are the electrocardiographic features of severe hyperkalemia except. 1. Peaked T waves. 2. Presence of U waves. 3. Sine wave pattern. 4. Loss of P waves. Answer 2. Presence of U waves. Reference Harrison 15th Edition Chapter 49 and Page 1269 Ganong Quality: Reader Status: Repeat QTDF: Harrison Discussion Hyperkalemia, defined as a plasma K+ concentration ?5.0 mmol/L, occurs as a result of either K+ release from cells or decreased renal loss. Increased K+ intake is rarely the sole cause of hyperkalemia since the phenomenon of potassium adaptation ensures rapid K+ excretion in response to increases in dietary consumption. The earliest electrocardiographic changes include increased T-wave amplitude, or peaked T waves. More severe degrees of hyperkalemia result in a prolonged PR interval and QRS duration, atrioventricular conduction delay, and loss of P waves. Progressive widening of the QRS complex and merging with the T wave produces a sinewave pattern. The terminal event is usually ventricular fibrillation or asystole. Explanation 1. Peaked T waves is seen. 2. Presence of U waves is not seen. 3. Sine wave pattern is seen. 4. Loss of P waves is seen. Comments Iatrogenic hyperkalemia may result from overzealous parenteral K+ replacement or in patients with renal insufficiency. Pseudohyperkalemia represents an artificially elevated plasma K+ concentration due to K+ movement out of cells immediately prior to or following venipuncture. Contributing factors include prolonged use of a tourniquet with or without repeated fist clenching, hemolysis, and marked leukocytosis or thrombocytosis. The latter two result in an elevated serum K+ concentration due to release of intracellular K+ following clot formation. Pseudohyperkalemia should be suspected in an otherwise asymptomatic patient with no obvious underlying cause. If proper venipuncture technique is used and a plasma (not serum) K+ concentration is measured, it should be normal. Tips Gordons syndrome is a rare condition characterized by hyperkalemia, metabolic acidosis, and a normal GFR. These patients are usually volume-expanded with suppressed renin and aldosterone levels as well as refractory to the kaliuretic effect of exogenous mineralocorticoids. It has been suggested that these findings could all be accounted for by increased distal Cl- reabsorption (electroneutral Na+ reabsorption), also referred to as a Cl- shunt. A similar mechanism may be partially responsible for the hyperkalemia associated with cyclosporine nephrotoxicity. Hyperkalemic distal (type 4) RTA may be due to either hypoaldosteronism or a Cl- shunt (aldosterone-resistant). Question 80. Hypocalcemia is characterized by all of the following features except: 1. Numbness and tingling of circumoral region. 2. Hyperactive tendon reflexes. 3. Shortening of Q-T interval in ECG. 4. Carpopedal spasm. Answer 3. Shortening of Q-T interval in ECG. Reference Harrison 15th Edition Chapter 341 and 340 Quality: Spotter Status: Repeat QTDF: All books Discussion A decrease in the concentration of free calcium ions in plasma results in increased neuromuscular irritability and tetany. This syndrome is characterized by peripheral and perioral paresthesia, carpal spasm, pedal spasm, anxiety, seizures, bronchospasm, laryngospasm, Chvosteks sign, Trousseaus sign, and Erbs sign, and lengthening of the QT interval of the electrocardiogram. In infants tetany may be manifested only by irritability and lethargy. The level of calcium ions that determines which features of tetany will be manifested varies among individuals. Tetany is also influenced by other components of the ECF; e.g., hypomagnesemia and alkalosis lower whereas hypokalemia and acidosis raise the threshold for tetany. Explanation 1. Numbness and tingling of circumoral region is present. 2. Hyperactive tendon reflexes is present. This is the basis of asking the patients to hyperventilate when we are not able to elicit a reflex. Hyperventilation causes Alkalosis which causes tetany 3. of Q-T interval in ECG is prolonged. 4. Carpopedal spasm is present. Comments Increases in total serum calcium concentration are usually accompanied by increases in free calcium levels and may be associated with anorexia, nausea, vomiting, constipation, hypotonia, depression, and occasionally lethargy and coma. Persistent hypercalcemia, especially when accompanied by normal or elevated levels of serum phosphate, may cause o ectopic deposition of a solid phase of calcium and phosphate in walls of blood vessels, connective tissue about the joints, gastric mucosa, cornea, and renal parenchyma. o Hypercalcemia per se alters renal function in addition to the pathologic effects of calcium phosphate deposition. Tips One formula that approximates the amount of calcium bound to protein is % of Protein bound Calcium = 0.8 x albumin (g/L) + 0.2 x globulin(g/L) + 3 A simplified correction is The correction is to add 1 mg/dL to the serum calcium level for every 1 g/dL by which the serum albumin level is below 4.0 g/dL. If the serum calcium level, for example, is 7.8 mg/dL (a subnormal value) and the serum albumin level is only 3.0 g/dL, then the stated serum calcium level is corrected by adding 1 mg/dL; the corrected value of 8.8 mg/dL is within the normal range. Question 81. All of the following may occur in Noonans syndrome except: 1.Hypertrophic cardiomyopathy. 2.Cryptoorchidism. 3.Infertility in females. 4.Autosomal dominant transmission. Answer 3.Infertility in females. Reference Nelson 15th Edition Chapter 535 Harrison 15th Edition Chapters 328, 338 and Page 2175 Quality: Thinker Status: New QTDF: Harrison Discussion The term Noonan syndrome has been applied to phenotypic males and females who have certain anomalies that occur also in females with Turner syndrome. These boys and girls have normal karyotypes. The disorder is usually sporadic, but affected siblings of the same and of different genders have been reported. Total or partial expression is present in 20% of relatives. Reports of male-to-male transmission suggest an autosomal dominant gene with variable expressivity. The gene has been mapped to chromosome 12q.The most common features are 1. Normal Karyotype 2. Normal Sex Chromosomes 3. Normal Gonads in females 4. Short stature, 5. Webbing of the neck, 6. Pectus carinatum or pectus excavatum, 7. Cubitum valgum, 8. Congenital heart disease, (most often Hypoertrophic Cardiomyopathy, pulmonary valvular stenosis or atrial septal defect) 9. Characteristic facies. 10. Hypertelorism, 11. Epicanthus, an 12. Antimongoloid palpebral slant, 13. Ptosis, 14. Micrognathia, and 15. Ear abnormalities (High Frequency Sensineural hearing loss) are common. Other abnormalities such as 16. Clinodactyly, 17. Hernias, and 18. Vertebral anomalies occur less frequently. 19. Moderate mental retardation occurs in 25% of patients. 20. Males frequently have cryptorchidism and small testes; they may be hypogonadal or normal. 21. In females Puberty is delayed 2 yr on average; adult height is achieved by the end of the 2nd decade and usually reaches the lowest limit of the normal population. 22. No Primary Gonadal Failure in Females Explanation 1. Hypertrophic cardiomyopathy is seen. 2. Cryptoorchidism is present. 3. Infertility in females is not present. 4. Autosomal dominant transmission is the rule. Comments Note that Noonan can occur in both Males and Females and there is Hypogonadism and Cryptorchidism in Males and Normal Gonads in Females and we have Pulmonary Stenosis and ASD (Every one knows the defect in Turners!!!) Tips Forget the popular saying that Noonan is Male Turner. It occurs in both males as well as in females Question 82. Thiamine deficiency is known to occur in all of the following except: 1. Food faddist. 2. Homocstinemia 3. Chronic alcoholic. 4. chronic heart failure patient on diuretics. Answer 2. Homocstinemia Reference Harrison 15th Edition Page 1375, Chapter 75, 240 Quality: Reader Status: New QTDF: Harrison Discussion Most dietary deficiency of thiamine worldwide is the result of poor dietary intake. In western countries, the primary causes of thiamine deficiency are alcoholism and chronic illness, such as cancer. Alcohol is known to interfere directly with the absorption of thiamine and with the synthesis of thiamine pyrophosphate. Malnourished individuals with alcoholic liver disease are also at increased risk of thiamine deficiency because of diminished storage sites in liver and muscle. Thiamine should always be replenished when refeeding a patient with alcoholism, as carbohydrate repletion without adequate thiamine can precipitate acute thiamine deficiency. In many cases, malnutrition is accompanied by thiamine deficiency, although this hypovitaminosis may also occur in the presence of an adequate protein and caloric intake, particularly in the Far East, where polished rice deficient in thiamine may be a major dietary component. In western nations, the widespread use of thiamine-enriched flour limits the presence of deficiency primarily to alcoholics and food faddists. The measurement of the thiamine-pyrophosphate effect (TPPE) can biochemically quantitate thiamine stores. An elevated TPPE, indicative of thiamine deficiency, has been found in 20 to 90% of patients with chronic heart failure. The deficiency appears to result from both reduced dietary intake and a diuretic-induced increase in the urinary excretion of thiamine. The acute administration of thiamine to these patients increases the left ventricular ejection fraction and the excretion of salt and water Explanation Self Explanatory Comments Vitamins are important Tips Question 83. A 30-yer-old HIV positive patient presents with fever, dyspnoea and non-productive cough. Patient is cyanosed. His chest X-ray reveals bilateral, symmetrical interstitial infiltrates. The most likely diagnosis is: 1. Tuberculosis. 2. Cryptococcosis. 3. Pneunocytis carinii pneumonia. 4. Toxoplasmosis. Answer 3. Pneunocytis carinii pneumonia. Reference Harrison 15th Edition Chapter 209 RobbinsBasic pathology, Page 430 Quality: Reader Status: Repeat QTDF: Harrison Discussion Patients with P. carinii pneumonia develop dyspnea, fever, and nonproductive cough. Symptoms in non-HIV-infected patients often begin after the glucocorticoid dose has been tapered and typically last 1 to 2 weeks. HIV-infected patients are usually ill for several weeks or longer and have relatively subtle manifestations. However, the clinical picture in individual patients is quite variable, and a high index of suspicion and elicitation of a careful history are key factors in early detection. Physical findings include tachypnea, tachycardia, and cyanosis, but lung auscultation reveals few abnormalities. The white blood cell count is variable and is usually governed by the patients underlying disease. Assessment of arterial blood gases demonstrates hypoxia, an increased alveolar-arterial oxygen gradient (PAO2 ? PaO2), and respiratory alkalosis. There also may be changes in pulmonary function test values (diffusing capacity) and increased uptake with nuclear imaging techniques (gallium scan). Elevated serum concentrations of lactate dehydrogenase (LDH) have been reported; they probably reflect lung parenchymal damage but are not specific to P. carinii infection. In general, laboratory abnormalities are less severe in HIV-infected patients than in non-HIV-infected patients. The classic findings on chest radiography consist of bilateral diffuse infiltrates beginning in the perihilar regions, but various atypical manifestations (nodular densities, cavitary lesions) have also been reported. Patients who receive aerosolized pentamidine have an increased frequency of upper-lobe infiltrates and pneumothorax. Early in the course of pneumocystosis, the chest radiograph may be normal. Although P. carinii usually remains confined to the lungs, cases of disseminated infection have occurred in both HIV-infected and non-HIV-infected patients. One risk factor for extrapulmonary spread in patients with HIV is the administration of aerosolized pentamidine. The most common sites of extrapulmonary involvement are the lymph nodes, spleen, liver, and bone marrow. Clinical manifestations range from incidental findings at autopsy to specific organ involvement. Histopathologic examination reveals the presence of P. carinii and the characteristic associated foamy material. Treatment for the extrapulmonary forms of pneumocystosis is the same as that for pneumonia. Explanation 1. Tuberculosis can be considered as a DD, if PCP os not given as a choice. 2. Cryptococcosis. Pulmonary cryptococcosis causes chest pain in about 40% of patients and cough in 20%. The chest x-ray shows one or more dense infiltrates, which are often well circumscribed. Cavitation, pleural effusions, and hilar adenopathy are infrequent. Calcification is not evident, and fibrotic stranding is rarely noticeable 3. Pneunocytis carinii pneumonia. 4. The most common manifestation of acute toxoplasmosis is cervical lymphadenopathy. The nodes may be single or multiple, are usually nontender, are discrete, and vary in firmness. Lymphadenopathy also may be found in suboccipital, supraclavicular, inguinal, and mediastinal areas. Generalized lymphadenopathy occurs in 20 to 30% of symptomatic patients. Between 20 and 40% of patients with lymphadenopathy also have headache, malaise, fatigue, and fever. A smaller proportion of symptomatic individuals have myalgia, sore throat, abdominal pain, maculopapular rash, meningoencephalitis, and confusionToxoplasmosis. Comments AIDS is a important Topic Tips Question 84. In actinomycosis of the spine, the abscess usually erodes: 1. Intervertebral disc. 2. Into the pleural cavity. 3. Into the reteroperitoneal space. 4. Towards the skin. Answer 4. Towards the skin. Reference Harrison 15th Edition Chapter 166 Page 1010 Quality: Reader Status: Repeat QTDF: Harrison Discussion Actinomycotic infection of the bone is usually due to adjacent soft tissue infection but may be associated with trauma (e.g., fracture of the mandible) or hematogenous spread. Because of slow disease progression, new bone formation and bone destruction are seen concomitantly. Infection of an extremity is uncommon and is usually a result of trauma. Skin, subcutaneous tissue, muscle, and bone (with periostitis or acute or chronic osteomyelitis) are involved alone or in various combinations. Cutaneous sinus tracts frequently develop Explanation Self Explanatory Comments Tips Question 85. Most sensitve and specific test for diagnosis of iron defficiency is : 1. Serum iron levels. 2. Serum ferritin levels. 3. Serum transferring receptor population : 4. Transferrin saturation. Answer 2. Serum ferritin levels. Reference Harrison 15th Edition Chapter 105 and Page 662 Park 17th Edition Page 424 Quality: Reader Status: Repeat QTDF: Harrison and other books Discussion Free iron is toxic to cells, and the body has established an elaborate set of protective mechanisms to bind iron in various tissue compartments. Within cells, iron is stored complexed to protein as ferritin or hemosiderin. Apoferritin binds to free ferrous iron and stores it in the ferric state. As ferritin accumulates within cells of the RE system, protein aggregates are formed as hemosiderin. Iron in ferritin or hemosiderin can be extracted for release by the RE cells although hemosiderin is less readily available. Under steady state conditions, the serum ferritin level correlates with total body iron stores; thus, the serum ferritin level is the most convenient laboratory test to estimate iron stores. The normal value for ferritin varies according to the age and gender of the individual (Fig. 105-3). Adult males have serum ferritin values averaging about 100 ug/L, while adult females have levels averaging 30 ug/L. As iron stores are depleted, the serum ferritin falls to ?15 ug/L. Such levels are virtually always diagnostic of absent body iron stores Explanation 1. Serum iron levels is not the most sensitive test. 2. Serum ferrition levels is the most sensitive test. 3. Serum transferring receptor population is not the most sensitive test: 4. Transferrin saturation is not the most sensitive test. Comments Anaemia is a favourite topic for examiners Tips Question 86. All the statrment about lactoferrin are true, except: 1. It is present in secondary granules of neutrophil 2. It is present in exocrine secretios of body. 3. It has great affinity for iron. 4. It transports iron for erythropoiesis. Answer 4. It transports iron for erythropoiesis. Reference Harrison 15th Edition Chapters 147, 42, 64, 317, 319 http://ndt.oupjournals.org/cgi/content/full/16/2/224 http://web2.iadfw.net/uthman/nutritional_anemia/nutritional_anemia.html Quality: Thinker Status: New QTDF: Harrison Discussion The promyelocyte divides to produce the myelocyte, a cell responsible for the synthesis of the specific or secondary granules which contain unique (specific) constituents such as lactoferrin, vitamin B12-binding proteins, membrane components of the nicotinamide-adenine dinucleotide phosphate (NADPH) oxidase required for hydrogen peroxide production, histaminase, and receptors for certain chemoattractants and adherence-promoting factors (CR3) as well as receptors for the basement membrane component, laminin Chap 305 Upon interaction of neutrophils with opsonized bacteria or immune complexes, azurophilic granules (containing myeloperoxidase, lysozyme, elastase, and other enzymes) and specific granules (containing lactoferrin, lysozyme, collagenase, and other enzymes) are released, and microbicidal superoxide radicals (O2?) are generated at the neutrophil surface. The generation of superoxide leads to inflammation by direct injury to tissue and by alteration of macromolecules such as collagen and DNA Lactoferrin is present in polymorphonuclear leukocytes and acts as an iron scavenger with bactericidal activity [3]. As a part of the acute-phase reaction, lactoferrin synthesis increases during inflammation. It can bind large amounts of free iron [11]. The iron bound to lactoferrin is taken up by activated macrophages, which express specific lactoferrin receptors. During inflammation, this causes iron deprivation of the erythroid precursors, which fail to express lactoferrin receptors. Iron is essential for the growth of some microbes and sequestration of iron in the form of insoluble compounds, such as lactoferrin and haemosiderin, is thought to be part of the host defence against bacterial and viral infections [15]. However, a decrease in erythropoiesis may also reflect a relative deficit of erythropoiesis in the face of an increased demand to produce neutrophil granulocytes and other immunocompetent cells. In fact Iron trapped in lactoferrin is useless as far as Erythropoiesis is concerned. Explanation 1. It is present in secondary granules of neutrophil 2. It is present in exocrine secretios of body. 3. It has great affinity for iron. 4. Iron is not available for erythropoiesis when trapped in Lactoferrin. Comments Iron is not available for erythropoiesis when trapped in Lactoferrin and this is one of the factors in the pathogenesis of Anaemia of Chronic Infections Tips Ga binds to serum and cellular transferrin and lactoferrin and is preferentially taken up by neutrophils, macrophages, bacteria, and tumor tissue (e.g., lymphoma) and is useful in the identification of infection and malignancies. Question 87. All of the following are poor prognostic factors for acute myeloid leukemias, except: 1. Age more than 60 years. 2. Leucocyte count more than 1,000,000/ul. 3. Secondary leukenias. 4. presence of t ( 8:21 ) Answer 4. presence of t ( 8:21 ) Reference Robbins Pathologic Basis Of Disease ,6th Edition ,Page 678 Harrison 15th Edition Chapter 111 Quality: Reader Status: Repeat QTDF: Harrison Discussion The single most important prognostic factor is attainment of Complete Remission. Complete Remission is defined after examination of both blood and bone marrow and should last 4 weeks. The blood neutrophil count must be 1500/uL and the platelet count 100,000/uL. Hemoglobin concentration or hematocrit are not considered in determining CR. Circulating blasts should be absent. While rare blasts may be detected in the blood during marrow regeneration, they should disappear on successive studies. Bone marrow cellularity should be 20% with trilineage maturation. The bone marrow should contain 5% blasts, and Auer rods should be absent. Extramedullary leukemia should not be present. Chromosome findings at diagnosis are an independent prognostic factor. Patients with t(8;21), inv(16), or t(15;17) have extremely good prognoses, while those with no cytogenetic abnormality have a moderately favorable outcome when treated with high-dose cytarabine. Patients with del(5q), -7, and abnormalities involving 12p have a very poor prognosis. Patients with certain abnormalities, such as inv(3), rarely achieve CR with standard induction chemotherapy. Explanation 1. Age more than 60 years indicates poor prognosis. 2. Leucocyte count more than 1,000,000/ul. indicates poor prognosis 3. Secondary leukemias indicate poor prognosis. 4. presence of t ( 8:21 ) indicate goof prognosis Comments A normal Hemoglobin is a BAD indicator. The reason is that the leukaemia is so Rapid that you are able to see the full blown picture even before the Blood Hb% has begun to drop down. That means we are dealing with a fairly aggressive tumour Tips Question 88. A 63-year-old man presented with massive splenomegaly, lymphadenopathy and a total leucocyte count of 17000 per mm3. The flowcytometery showed CD 19 positive, CD5 positive, DC 23 negative, monoclonal B cells with bright kappa positivity comprising 80% of the peripheral blood lymphoid cells. The most likely diagnosis is: 1. Mantle cell lymphoma. 2. Splenic lymphoma with villous lymphocytes. 3. Follicular lymphoma. 4. Hairy cellleukemia. Answer 1. Mantle cell lymphoma. Reference Harrison 15th Edition Chapter 112 Quality: Reader Status: Repeat QTDF: Harrison Discussion Mantle cell lymphoma makes up ~6% of all non-Hodgkins lymphomas. Recognized as a separate entity only in the past decade, this lymphoma was previously placed in a number of other subtypes. Its existence was confirmed by the recognition that these lymphomas have a characteristic chromosomal translocation, t(11;14) between the immunoglobulin heavy chain gene on chromosome 14 and the bcl-1 gene on chromosome 11, and regularly overexpress the BCL-1 protein. Mantle cell lymphoma (MCL) is a B-cell lymphoma that has previously been called diffuse small-cleaved cell lymphoma. Sometimes it was and is called intermediate differentiation lymphoma or centrocytic lymphoma. These lymphomas are classified as indolent but their aggressive nature is noted by NCI. MCL primarily afflicts men over 50, who almost always present with advanced, Stage III or IV disease. Four histologic subtypes have been noted - Nodular, Diffuse, Mantle Zone and Blastic. Blastic appears to have the worst prognosis with Nodular and Diffuse having longer average survival times. MCL has pan-B cell antigens CD19, CD20, and CD22 with surface IgM and IgD in addition to the pan-T antigen CD5. CD5 distinguishes MCL from follicular lymphomas which rarely express this antigen. The lack of CD23 and a higher antigen density of CD20 and surface Ig is useful in distinguishing MCL from small lymphocytic lymphoma. MCL has a unique cytogenetic translocation involving chromosomes 11 and 14. This juxtaposes the enhancer element of the Ig heavy chain JH region on chromosome 14 to the bcl-1 proto-oncogene which encodes the cyclin D1 protein on chromosome 11. The overexpression of cyclin D1 produces excessive B-Cell proliferation. The diagnosis of mantle cell lymphoma can be made accurately by an expert hematopathologist based on morphologic findings and proof that the tumor is a B cell lymphoma. As with all subtypes of lymphoma, an adequate biopsy is important. The differential diagnosis of mantle cell lymphoma includes other small-cell B cell lymphomas. In particular, mantle cell lymphoma and small lymphocytic lymphoma share a characteristic expression of CD5. Mantle cell lymphoma usually has a slightly indented nucleus. The most common presentation of mantle cell lymphoma is with palpable lymphadenopathy, frequently accompanied by systemic symptoms. Approximately 70% of patients will be stage IV at the time of diagnosis, with frequent bone marrow and peripheral blood involvement. Of the extranodal organs that can be involved, gastrointestinal involvement is particularly important to recognize. Patients who present with lymphomatosis polyposis in the large intestine usually have mantle cell lymphoma. often have Waldeyers ring involvement, Explanation 1. Mantle cell lymphoma suits the clinical picture. 2. Splenic lymphoma with villous lymphocytes is a type of B Cell Lymphoma. 3. Follicular Lymphoma Follicular lymphomas make up 22% of non-Hodgkins lymphomas worldwide and at least 30% of non-Hodgkins lymphomas diagnosed in the United States. This type of lymphoma can be diagnosed accurately on morphologic findings alone and has been the diagnosis in the majority of patients in therapeutic trials for low-grade lymphoma in the past. The clinical characteristics of follicular lymphoma are median age 59 rare in children 4. Hairy cellleukemia.is a rare disease that presents predominantly in older males. Typical presentation involves pancytopenia, although occasional patients will have a leukemic presentation. Splenomegaly is usual. The malignant cells appear to have hairy projections on light and electron microscopy and show a characteristic staining pattern with tartrate-resistant acid phosphatase. Bone marrow is typically not able to be aspirated, and biopsy shows a pattern of fibrosis with diffuse infiltration by the malignant cells. Patients with this disorder are prone to unusual infections including infection by Mycobacterium avium intracellulare, and vasculitic syndromes have been described. Hairy cell leukemia is responsive to chemotherapy with interferon ?, pentostatin, or cladribine, with the latter being the usually preferred treatment. Clinical complete remissions with cladribine occur in the majority of patients, and long-term disease-free survival is frequent. Comments Current therapies for mantle cell lymphoma are unsatisfactory. Patients with localized disease might be treated with combination chemotherapy followed by radiotherapy; however, these patients are exceedingly rare. For the usual presentation with disseminated disease, treatments are unsatisfactory, with the minority of patients achieving complete remission. Aggressive combination chemotherapy regimens followed by autologous or allogeneic bone marrow transplantation are frequently offered to younger patients. For the occasional elderly, asymptomatic patient, observation followed by single-agent chemotherapy might be the most practical approach. Combined used of rituximab (anti-CD20 antibody) and chemotherapy may be associated with better response rates. Tips Only mantle cell lymphoma and typical B cell CLL are usually CD5 positive Question 89. A 40 year old male had undergone splenectomy 20 years ago. Peripheral blood smear examination would show the presence of: 1. Dohle bodies 2. Hypersegmented neutrophils. 3. Spherocytes. 4. Howell-Jolly bodies. Answer 4. Howell-Jolly bodies. Reference Harrison 15th Edition Chapter 63 Quality: Reader Status: Repeat QTDF: Harrison Discussion Old and damaged erythrocytes are less deformable and are retained in the cords, where they are destroyed and their components recycled. Red cell inclusion bodies such as parasites, nuclear residua (Howell-Jolly bodies), or denatured hemoglobin (Heinz bodies) are pinched off in the process of passing through the slits, a process called pitting. The culling of dead and damaged cells and the pitting of cells with inclusions appear to occur without significant delay since the blood transit time through the spleen is only slightly slower than in other organs. The absence of the spleen has minimal long-term effects on the hematologic profile. In the immediate postsplenectomy period, there may be some leukocytosis (up to 25,000/uL) and thrombocytosis (up to 1 x 106/uL), but within 2 to 3 weeks, blood cell counts and survival of each cell lineage are usually normal. The chronic manifestations of splenectomy are marked variation in size and shape of erythrocytes (anisocytosis, poikilocytosis) and the presence of Howell-Jolly bodies (nuclear remnants), Heinz bodies (denatured hemoglobin), basophilic stippling, and an occasional nucleated erythrocyte in the peripheral blood. When such erythrocyte abnormalities appear in a patient whose spleen has not been removed, one should suspect splenic infiltration by tumor that has interfered with its normal culling and pitting function. Explanation 1. Dohle bodies are discrete, blue-staining non-granular areas found in the periphery of the cytoplasm of the neutrophil in infections and other toxic states. They represent aggregates of rough endoplasmic reticulum. 2. Hypersegmented neutrophils are seen in Vit B12 deficiency. This is one of the faourite Oral Questions in Medicine. A RBC Disorder diagnosed by looking at WBC in peropheral smear 3. Spherocytes are seen in Congenital Spherocytosis. 4. Howell-Jolly bodies are seen after splenectomy. Comments Read the major bodies in Davidson Tips Piching Off is Pitting Question 90. Leukoerythroblastic picture may be seen in all of the following except: 1. Myelofibrois. 2. Metastatic careinoma. 3. Gauchers disease. 4. Thalassemia. Answer 4. Thalassemia. Reference Harrisons,15th Edition Page 700 Quality: Reader Status: New QTDF: Harrison Discussion Fibrosis of the bone marrow , usually accompanied by a characteristic blood smear picture called leukoerythroblastosis, can occur as a primary hematologic disease, called myelofibrosis or myeloid metaplasia , and as a secondary process, called myelophthisis. Myelophthisis, or secondary myelofibrosis, is reactive. Fibrosis can be a response to invading tumor cells, usually of an epithelial cancer of breast, lung, and prostate or neuroblastoma. Marrow fibrosis may occur with infection of mycobacteria (both Mycobacterium tuberculosis and M. avium) fungi, or HIV, and in sarcoidosis. Intracellular lipid deposition in Gauchers disease and obliteration of the marrow space related to absence of osteoclast remodeling in congenital osteopetrosis also can produce fibrosis. Secondary myelofibrosis is a late consequence of radiation therapy or treatment with radiomimetic drugs. Usually, the infectious or malignant underlying processes are obvious. Marrow fibrosis can also be a feature of a variety of hematologic syndromes, especially chronic myeloid leukemia, multiple myeloma, lymphomas, myeloma, and hairy cell leukemia. Explanation 1. Leukoelrythroblastic picture may be seen in Myelofibrois. 2. Leukoelrythroblastic picture may be seen in Metastatic careinoma. 3. Leukoelrythroblastic picture may be seen in Gauchers disease. 4. In Thalassemia, the leucoerythroblastic picture may in fact occur, but not always and only after Splenectomy Comments MYELOPHTHISIC ANEMIAS The pathophysiology has three distinct features: proliferation of fibroblasts in the marrow space (myelofibrosis); the extension of hematopoiesis into the long bones and most particularly into extramedullary sites, usually the spleen, liver, and lymph nodes (myeloid metaplasia); and ineffective erythropoiesis. The etiology of fibrosis is unknown but most likely involves dysregulated production of growth factors: platelet-derived growth factor and transforming growth factor ? have been implicated. Abnormal regulation of other hematopoietins would lead to localization of blood-producing cells in nonhematopoietic tissues and uncoupling of the usually balanced processes of stem cell proliferation and differentiation. Myelofibrosis is remarkable for pancytopenia despite extraordinarily large numbers of circulating hematopoietic progenitor cells. Anemia is dominant in secondary myelofibrosis, usually normocytic and normochromic. The diagnosis is suggested by the characteristic leukoerythroblastic smear. Erythrocyte morphology is very abnormal, with circulating nucleated red blood cells, teardrops, and shape distortions. White blood cell numbers are often elevated, sometimes mimicking a leukemoid reaction, with circulating myelocytes, promyelocytes, and myeloblasts. Platelets may be abundant and are often giant size. Inability to aspirate the bone marrow, the characteristic dry tap, can allow a presumptive diagnosis before the biopsy is decalcified. The course of secondary myelofibrosis is determined by its cause, usually a metastatic tumor or an advanced hematologic malignancy. Treatable causes must be excluded, especially tuberculosis and fungus. Transfusion support can relieve symptoms Tips Question 91. Raised serum level of lipoprotein (a) is a predictor of: 1. Cirrhosis of liver. 2. Rheumatic arthritis. 3. Atherosclerosis. 4. Cervical cancer. Answer 3. Atherosclerosis. Reference Harrison 15th Edition Chapter 344 Disorders if Lipoprotein Metabolism Harrison 15th Edition Chap 241 Pathogenesis of Atherosclerosis Quality: Spotter Status: New Question from a New Topic QTDF: Harrison and Journals Discussion Apoprotein(a), a large glycoprotein that shares a high degree of sequence homology with plasminogen, is made by hepatocytes and is secreted into plasma where it forms a covalent linkage with the apo B100 of LDL to form lipoprotein(a). The physiologic role of lipoprotein(a) is not known, but elevated levels are associated with an increased risk for atherosclerosis Lp(a) (often pronounced lipoprotein little a to distinguish it from apolipoprotein AI and others found in HDL) provides a potential link between hemostasis and blood lipids. The Lp(a) particle consists of an apoprotein (a) molecule bound by a sulfhydryl link to the apolipoprotein B moiety of a LDL particle. Apoprotein (a) has homology with plasminogen and may inhibit fibrinolysis by competing with plasminogen. Other risk factors for atherosclerosis related to blood clotting include elevated levels of fibrinogen or of the inhibitor of fibrinolysis, plasminogen-activator inhibitor (PAI) 1. Explanation Self Explanatory Comments Because plasma triglyceride levels rise and both HDL and LDL cholesterol levels fall modestly after a fat-containing meal (due to the action of CETP), it is preferable to measure plasma lipids after a 12-h fast. Measuring cholesterol levels alone will not detect individuals with isolated low HDL; screening for CHD should therefore include measurement of HDL. Because serum lipid levels vary from day to day, at least two to three measurements should be made days or weeks apart before initiating therapy. Some experts advocate the use of total cholesterol/HDL ratios as a better assessment of individual risk. This is a reasonable approach provided both the patient and physician are aware that the treatment goal is to reduce LDL. In addition, rare patients with very high or very low levels of both LDL and HDL have ratios that are not interpretable on the basis of population studies. Although some laboratories offer measurements of individual apoproteins (e.g., apo B100 and apo AI), or size estimates of LDL, this information is not generally helpful in decision-making. Measurement of lipoprotein (a) levels can provide an indication of risk that cannot be gleaned from lipid measurements. Lipoprotein electrophoresis is not useful except for the diagnosis of dysbetalipoproteinemia, a diagnosis that otherwise requires ultracentrifugation methods. Apo E genotyping is also helpful in the diagnosis of dysbetalipoproteinemia (although rarely the disorder can be due to other defects in the apo E gene). Both LDL and HDL cholesterol levels are temporarily decreased for several weeks after myocardial infarction or acute inflammatory states but can be accurately measured if blood is obtained within 8 h of the event. Tips Question 92. Recurrent ischemic events following thrombolysis has been patho-physiologically linked to which of the following factors : 1. Antivodies to thrombolytic agents 2. fibrinopeptife A 3. Lipoprotein (a) [LP(a)] 4. Triglycerides. Answer 3. Lipoprotein (a) [LP(a)] Reference Harrison 15th Edition Chapter 344 Disorders if Lipoprotein Metabolism Harrison 15th Edition Chap 241 Pathogenesis of Atherosclerosis Quality: Spotter Status: New Question from a New Topic QTDF: Harrison and Journals Discussion See the previous Question !!! Explanation 1. Antibodies to thrombolytic agents 2. fibrinopeptife A 3. Lipoprotein (a) [LP(a)] 4. Triglycerides. Comments Theme Couple !! Tips Question 93. Which of the heart valve is most likely to be involved by infective endocarditis following a septic abortion? 1. Aortic valve. 2. Tricuspid valve. 3. Pulmonary valve. 4. Mitral valve. Answer 2. Tricuspid valve. Reference Harrison 15th Edition Chapter 126 and page 1354 Quality: Final MBBS Status: Repeat QTDF: Harrison Discussion Endocarditis occurring among injection drug users, especially when infection involves the tricuspid valve, is commonly caused by S. aureus strains, many of which are methicillin-resistant Among injection drug users, infection involving valves on the left side of the heart presents with the typical clinical features of endocarditis. In almost 50% of patients with endocarditis associated with injection drug use, infection is limited to the tricuspid valve. These patients present with fever, faint or no murmur, and (in 75% of cases) prominent pulmonary findings, including cough, pleuritic chest pain, nodular pulmonary infiltrates, and occasionally pyopneumothorax. Nosocomial endocarditis (defined as that which results from hospital care within the prior month and most commonly presenting as intravascular catheter-associated bacteremia), if not associated with a retained intracardiac device, has typical manifestations. Endocarditis associated with flow-directed pulmonary artery catheters is often cryptic, with symptoms masked by comorbid critical illness, and is commonly diagnosed at autopsy. Transvenous pacemaker lead and/or implanted defibrillator-associated endocarditis commonly follows initial implantation or a generator unit change; may be associated with obvious or cryptic generator pocket infection; and results in fever, minimal murmur, and pulmonary symptoms similar to those encountered in addicts with tricuspid endocarditis Explanation 1. Aortic valve is commonly involved in Marfans. 2. Tricuspid valve is commonly involced in iv drug abusers. 3. Pulmonary valveis commonly involved in Functional PR in Pulmonay Hypertension. 4. Mitral valve is commonly affected in Rheumatic heart Disease. Comments Another question from Final Year Tips Question 94. The most common cause of tricuspid regurgitation is secondary to: 1. Rheumatic heart disease. 2. Dilatation of right ventricle. 3. Coronary artery disease. 4. Endocarditis due to intravenous drug abuse. Answer 2. Dilatation of right ventricle. Reference Harrison 15th Edition Chapter 236 ands Page 1354 Quality: Final MBBS Clinicals Status: Repeat QTDF: Harrison Discussion Most commonly, Tricuspid Regurgitation is functional and secondary to marked dilatation of the RV and the tricuspid annulus. Functional TR may complicate RV enlargement of any cause, including inferior wall infarcts that involve the RV, and it is commonly seen in the late stages of heart failure due to rheumatic or congenital heart disease with severe pulmonary hypertension, as well as in ischemic heart disease, cardiomyopathy, and cor pulmonale. It is in part reversible if pulmonary hypertension is relieved. Rheumatic fever may produce organic TR, often associated with TS. Infarction of RV papillary muscles, tricuspid valve prolapse, carcinoid heart disease, endomyocardial fibrosis, infective endocarditis, and trauma all may produce TR. Less commonly, TR results from congenitally deformed tricuspid valves, and it occurs with defects of the atrioventricular canal as well as with Ebsteins malformation of the tricuspid valve Explanation Self Explanatory Comments A question that is often asked in Final MBBS Tips Topic Couple !!! Question 95. Oslers nodes are typically seen in which one of the follwing : 1. chronic candida endocarditis. 2. Acute staphylococcal endocarditis 3. pseuduomonas endocarditis. 4. Libman sacks endocarditis. Answer 2. Acute staphylococcal endocarditis Reference Harrison 15th Edition Chapter 126 and Page 811 Quality: Reader Status: Repeat QTDF: Harrison Discussion The classic nonsuppurative peripheral manifestations of subacute endocarditis are related to the duration of infection and, with early diagnosis and treatment, have become infrequent. In contrast, septic embolization mimicking some of these lesions like subungual hemorrhage, Oslers nodes, is common in patients with acute S. aureus endocarditis. Musculoskeletal symptoms, including nonspecific inflammatory arthritis and back pain, usually remit promptly with treatment but must be distinguished from the symptoms of focal metastatic infection. Hematogenously seeded focal infection may involve any organ but most often is clinically evident in the skin, spleen, kidneys, skeletal system, and meninges. Arterial emboli, which may be asymptomatic and discovered only at autopsy, are clinically apparent in up to 50% of patients. Vegetations <10 mm in diameter (as measured by echocardiography) and those located on the mitral valve are more likely to embolize than are smaller or nonmitral vegetations. Embolic events(often with infarction)involving the extremities, spleen, kidneys bowel, or brain are often noted at presentation. With antibiotic treatment, the frequency of embolic events decreases from 13 per 1000 patient-days during the initial week to 1.2 per 1000 patient-days after the third week. Emboli occurring late during or after effective therapy do not in themselves constitute evidence of failed antimicrobial treatment. Neurologic symptoms, most often resulting from embolic strokes, occur in up to 40% of patients. Other neurologic complications include aseptic or purulent meningitis, intracranial hemorrhage due to hemorrhagic infarcts or ruptured mycotic aneurysms, seizures, and encephalopathy. Microabscesses in brain and meninges occur commonly in S. aureus endocarditis; surgically drainable abscesses are infrequent. Explanation Self Explanatory Comments Straight from Harrison Tips Question 96 . During cardiopulmonary resuscitaton intravenous calcium glouconate is indicated under all for the follwing circumstances except: 1. After I min. of arrest routinely. 2. Hypocalcemia 3. Calcium channel blocker toxicity 4. Electromechanical dissociaton. Answer 1. After I min. of arrest routinely. Reference Harrison 15th Edition Chapter 39 and Page 232 Quality: Thinker Status: New QTDF: Harrison Discussion Calcium is contraindicated in CPR because excess calcium worsens cellular death. It is indicated in Hypocalcemia Hyperkalemia (leads to cardiac standstill, ventricular and tachycardia/fibrillation) Over dosage of calcium channel blockers. Explanation 1. Intravenous Calcium is not recommended After I min. of arrest routinely. 2. Hypocalcemia is an indication of iv calcium 3. Calcium channel blocker toxicity is an indication of iv calcium 4. Electromechanical dissociaton is an indication of iv calcium. Comments Since this is a topic that had become quite frequent of late, few points are Given here though they are not directly related to this question Advanced life support is intended to achieve adequate ventilation, control cardiac arrhythmias, stabilize blood pressure and cardiac output, and restore organ perfusion. The activities carried out to achieve these goals include (1) intubation with an endotracheal tube, (2) defibrillation/cardioversion and/or pacing, and (3) insertion of an intravenous line. Ventilation with O2 (room air if O2 is not immediately available) may promptly reverse hypoxemia and acidosis. The speed with which defibrillation/cardioversion is carried out is an important element for successful resuscitation. When possible, immediate defibrillation should precede intubation and insertion of an intravenous line; CPR should be carried out while the defibrillator is being charged. As soon as a diagnosis of VT or VF is obtained, a 200-J shock should be delivered. Additional shocks at higher energies, up to a maximum of 360 J, are tried if the initial shock does not successfully abolish VT or VF. Epinephrine, 1 mg intravenously, is given after failed defibrillation, and attempts to defibrillate are repeated. The dose of epinephrine may be repeated after intervals of 3 to 5 min If the patient is less than fully conscious upon reversion, or if two or three attempts fail, prompt intubation, ventilation, and arterial blood gas analysis should be carried out. Intravenous NaHCO3, which was formerly used in large quantities, is no longer considered routinely necessary and may be dangerous in larger quantities. However, the patient who is persistently acidotic after successful defibrillation and intubation should be given 1 meq/kg NaHCO3 initially and an additional 50% of the dose repeated every 10 to 15 min. After initial unsuccessful defibrillation attempts, or with persistent electrical instability, a bolus of 1 mg/kg lidocaine is given intravenously, and the dose is repeated in 2 min in those patients who have persistent ventricular arrhythmias or remain in VF. This is followed by a continuous infusion at a rate of 1 to 4 mg/min. If lidocaine fails to provide control, other antiarrhythmic therapies should be tried. For persistent, hemodynamically unstable ventricular arrhythmias, intravenous amiodarone has emerged as the treatment of choice (150 mg over 10 min, followed by 1 mg/min for up to 6 h, and 0.5 mg/min thereafter). Intravenous procainamide (loading infusion of 100 mg/5 min to a total dose of 500 to 800 mg, followed by continuous infusion at 2 to 5 mg/min) may be tried for persisting, hemodynamically stable arrhythmias; or bretylium tosylate (loading dose 5 to 10 mg/kg in 5 min; maintenance dose 0.5 to 2 mg/min) may be tried as an alternative for unstable arrhythmias. Intravenous calcium gluconate is no longer considered safe or necessary for routine administration. It is used only in patients in whom acute hyperkalemia is known to be the triggering event for resistant VF, in the presence of known hypocalcemia, or in patients who have received toxic doses of calcium channel antagonists. Cardiac arrest secondary to bradyarrhythmias or asystole is managed differently. The patient is promptly intubated, CPR is continued, and an attempt is made to control hypoxemia and acidosis. Epinephrine and/or atropine are given intravenously or by an intracardiac route. External pacing devices are now available to attempt to establish a regular rhythm, but the prognosis is generally very poor in this form of cardiac arrest, even with successful electrical pacing. Pulseless electrical activity (PEA) is treated similarly to bradyarrhythmias, but its outcome is also dismal. The one exception is bradyarrhythmic/asystolic cardiac arrest secondary to airway obstruction. This form of cardiac arrest may respond promptly to removal of foreign bodies by the Heimlich maneuver or, in hospitalized patients, by intubation and suctioning of obstructing secretions in the airway. Tips Question 97. A post-operative cardiac surgical patient developed sudden hypotension, raised central venous pressure, pulses paradoxus at the 4th post operative hour. The most probable diagnosis is . 1.Excessive mediastinal bleeding. 2. Ventricular dysfunction. 3. Congestive cardiac failure. 4. Cardiac tamponade. Answer 4. Cardiac tamponade. Reference Harrisons,15th ,Page 1367 Quality: Thinker Status: New QTDF: Harrison Discussion CARDIAC TAMPONADE The accumulation of fluid in the pericardium in an amount sufficient to cause serious obstruction to the inflow of blood to the ventricles results in cardiac tamponade. The three most common causes of tamponade are neoplastic disease, idiopathic pericarditis, and uremia. Tamponade may also result from bleeding into the pericardial space either following cardiac operations and trauma (including cardiac perforation during diagnostic procedures) or from tuberculosis and hemopericardium. The latter may occur when a patient with any form of acute pericarditis is treated with anticoagulants. The three principal features of tamponade are o elevation of intracardiac pressures leading to elevated JVP, o limitation of ventricular filling, and o reduction of cardiac output. Leading to hypotension The quantity of fluid o 200 mL when the fluid develops rapidly o more than 2000 mL in slowly developing effusions o required to produce tamponade also varies directly with the thickness of the ventricular myocardium and inversely with the thickness of the parietal pericardium. The classic findings of falling arterial pressure, rising venous pressure, and faint heart sounds usually occur only with o severe, acute tamponade, o as occurs with cardiac trauma or rupture. Tamponade may also develop more slowly, and under these circumstances the clinical manifestations may resemble those of heart failure, including dyspnea, orthopnea, hepatic engorgement, and jugular venous hypertension. Tamponade should be considered in any patient with hypotension and elevation of jugular venous pressure with a prominent x descent; in contrast to constrictive pericarditis, in which the y descent is prominent, in cardiac tamponade it is diminutive or absent. A positive Kussmaul sign (see below) is rare in cardiac tamponade, as is a pericardial knock. Their presence suggests that an organizing process and epicardial constriction are present in addition to effusion. A widening of the area of flatness to percussion across the anterior aspect of the chest wall, a paradoxical pulse, hypotension, relatively clear lung fields, diminished pulsations of the cardiac silhouette on fluoroscopy, enlargement of the cardiac silhouette (especially in subacute or chronic tamponade), reduction in amplitude of the QRS complexes, and electrical alternans of the P, QRS, and T waves should raise the suspicion of cardiac tamponade. Paradoxical Pulse This important clue to the presence of cardiac tamponade consists of a greater than normal (10 mmHg) inspiratory decline in systolic arterial pressure. When severe, it may be detected by palpating weakness or disappearance of the arterial pulse during inspiration, but usually sphygmomanometric measurement of systolic pressure during slow respiration is required. Since both ventricles share a tight incompressible covering, i.e., the pericardial sac, the inspiratory enlargement of the right ventricle in cardiac tamponade compresses and reduces left ventricular volume; leftward bulging of the interventricular septum further reduces the left ventricular cavity as the right ventricle enlarges during inspiration. Thus in cardiac tamponade the normal inspiratory augmentation of right ventricular volume causes an exaggerated reciprocal reduction in left ventricular volume. Also, respiratory distress increases the fluctuations in intrathoracic pressure, which exaggerates the mechanism just described. Right ventricular infarction may resemble cardiac tamponade with hypotension, elevated jugular venous pressure, an absent y descent in the jugular venous pulse, and occasionally pulsus paradoxus. The differences between these two conditions are shown in. Paradoxical pulse occurs not only in cardiac tamponade but also in approximately one-third of patients with constrictive pericarditis. Paradoxical pulse is not pathognomonic of pericardial disease because it may be observed in some cases of hypovolemic shock, acute and chronic obstructive airways disease, and pulmonary embolus. Low-pressure tamponade refers to mild tamponade in which the intrapericardial pressure is increased from its slightly subatmospheric levels to +5 to +10 mmHg; in some instances hypovolemia coexists. As a consequence, the central venous pressure is normal or only slightly elevated, while arterial pressure is unaffected and there is no paradoxical pulse. The patients are asymptomatic or complain of mild weakness and dyspnea. The diagnosis is aided by echocardiography, and both hemodynamic and clinical manifestations improve following pericardiocentesis. Diagnosis Since immediate treatment of cardiac tamponade may be lifesaving, prompt measures to establish the diagnosis by echocardiography should be undertaken. When pericardial effusion causes tamponade, during inspiration right ventricular diameter increases while left ventricular diameter and mitral valve opening decrease. Often the right ventricular cavity is reduced in diameter, and there is late diastolic inward motion (collapse) of the right ventricular free wall and of the right atrium. Doppler ultrasound shows exaggerated pulmonic (and tricuspid) flow during inspiration, with reciprocal changes in aortic (and mitral) flow. If measured, the pericardial pressure is elevated and equal to the right atrial pressure. There is equalization of pressures, i.e., the pulmonary artery wedge is equal, or close, to right atrial, right ventricular, and pulmonary artery diastolic pressures. The square root sign in the ventricular pressure pulses and the prominent y descent in atrial and jugular venous pressure are characteristic of constrictive pericarditis (see below) and are rarely present in tamponade. TREATMENT :Pericardiocentesis must be carried out at once, Explanation Self Explanatory Comments CCF Resembles a slow developing tramponade Tips Question 98. All of the following heart sounds occur shortly after S2 except: 1. Opening snap. 2. Pericardial knock. 3. Ejection click. 4. Tumor plop. Answer 3. Ejection click. Reference Harrison 15th Edition Chapter 34. and Page 1259 Physical Diagnosis by Golwalia 8th Edition Page 312 Manual of Practical Medicine by Alaggappan 2nd Edition Page 73 Quality: Reader Status: New QTDF: Harrison Discussion Ejection Clicks may be Vascular or Valvular Valvular Ejection Clicks o Opening of Semilunar Valves o Aortic Ejection Click is heard in AS in Aortic Area, conducted all over pericardium and is not changed with Respiration o Pulmonary Ejection Click is PS in Pulmonary Area localized to pulmonary area and increases with Expiration (In fact Pulmonary Ejection Click is the only Right Sided event that is best heard in expiration) o Mid systolic Clicks Mitral Valve Prolapse / TVP Aneurysm of Interatrial or Interventricular septum Ebsteins Anomaly Severe Aortic Reguritation Vascular Ejection Clicks o In Aortic Area in Aortic Dilatation Systemic Hypertension o In Pulmonary Area in Pulmonary Artery Dilataion Pulmonary Hypertension Explanation 1. Opening snap is a diastolic Sound and occurs shortly after S2. Opening Snap is produced by the opening of AV Valves It is a sound generated due to the sudden early diastolic buckling of Anterior leaflet due to atrial pressure (Drooling Down during Diastole) Opening Snap Over Lower Left Parasternal Region o Tricuspid Stenosis o Ticuspid Reguritation o ASD Opening Snap Just internal to Apex o Mitral Stenosis o Mitral Regurgitation o VSD o PDA Absent OS or Soft OS in Mitral Stenosis Occurs in o Mild MS o Severe MS ( clock wise rotation of heart) o Calcification o Congenital MS o MS with AS or AR 2. Pericardial knock is a loud highfrequency diastolic Sound and occurs shortly after S2 heards in Constrictive Pericarditis due to abrupt halt to early diastolicfilling. 3. Ejection click. is a systolic sound which occurs after S1 or before S2 4. Tumor plop is a diastolic Sound and occurs shortly after S2 heard in Right orLeft Atrial Myxoma. Comments About Prosthetic Sounds Ball valves - Opening sound louder than closing sound Tilting disc valves - Only closuresound heard Bileaflet valves - Closure sounds well heaerd Mitral Prosthesis - Opening sound corresponds to Opening Snap and Closing sound to S1 Aortic Prosthesis - Opening sound corresponds to Ejection Click and Closing sound to S2 Tips Read Aout JVP !!! Question 99. An early systolic murmur may be caused by all of the following except: 1.Small ventricular septal defect. 2.Papillary muscle dysfunction 3.Tricuspid regurgitation. 4.Aortic stenosis. Answer 2.Papillary muscle dysfunction. Reference Harrison 15th Edition Chapter 236.and Page 1261 Physical Diagnosis by Golwalia 8th Edition Page 312 Manual of Practical Medicine by Alaggappan 2nd Edition Page 75 Quality: Thinker Status: New QTDF: Golwallia Discussion Causes of Early Systolic Murmurs Acute severe rMR and TR Virtually closed VSD Large VSD with Pulmonary Hypertension Tight MS and mild or no MR Papillary Muscle Rupture Causes of Ejection Systolic Murmurs Aortic Stenosis Pulmonary Stenosis HOCM Causes of Late Systolic Murmurs MR with Papillary Muscle dysfunction Mitral ValveProlapse Co Arctation of Aorta HOCM Explanation 1. Small ventricular septal defect causes Early Systolic Murmur. 2. Papillary muscle dysfunction causes Late systolic Murmur. 3. Tricuspid regurgitation causes Early Systolic Murmur. 4. The murmur of AS is characteristically an ejection (mid) systolic murmur that commences shortly after the S1, increases in intensity to reach a peak toward the middle of ejection, and ends just before aortic valve closure. More importantly conducted murmurs of Aortic Stenosis are early systolic........... Comments Most books on Clinical Diagnosis give 1,3,4 as causes of Early Systolic Murmur and choice 2 as Late Systolic Murmur. It is clearly mentioned in most of the text books that Paillary Muscle Dysfunction causes Late Systolic Murmur and Papillary Muscle Rupture causes Early Systolic Murmur.. Tips Please dont go by the word that Murmur of AS is the prototype of Midsystolic Murmurs. The murmur of AS starts in the early systolic phase; only the maximum intensity is midsystolic Question 100. All of the following statements regarding the ECG in acute pericarditis are true except: 1. T-wave inversions develop before ST elevations return to baseline. 2. Global ST segment elevation is seen in early pericarditis. 3. Sinus tachycardia is a common finding. 4. PR segment depression is present in majority of patients. Answer 1. T-wave inversions develop before ST elevations return to baseline. Reference Harrison 15th Edition Chapter 239 Quality: Reader - Intern Status: Repeat QTDF: Harrison Discussion The electrocardiogram (ECG) in acute pericarditis without massive effusion usually displays changes secondary to acute subepicardial inflammation. There is widespread elevation of the ST segments, often with upward concavity, involving two or three standard limb leads and V2 to V6, with reciprocal depressions only in aVR and sometimes V1. Usually there are no significant changes in QRS complexes, except for some reduction in voltage in patients with large pericardial effusions. After several days, the ST segments return to normal, and only then do the T waves become inverted. o In contrast, in acute myocardial infarction, reciprocal depression of ST segments is usually more prominent; QRS changes occur, particularly the development of Q waves, as well as notching and loss of R-wave amplitude; and T-wave inversions usually occur within hours before the ST segments have become isoelectric. Sequential ECGs are useful in distinguishing acute pericarditis from acute myocardial infarction. o In the latter, elevated ST segments return to normal within hours. Early repolarization is a normal variant and may also cause widespread ST-segment elevation, most prominent in left precordial leads. o However, in this condition the T waves are usually tall and the ST/T ratio is under 0.25, but this ratio is higher in acute pericarditis. Depression of the PR segment (below the TP segment) is also common and reflects atrial involvement. With large pericardial effusions, the QRS voltage is reduced; atrial premature beats and atrial fibrillation are sometimes noted Explanation 1. T-wave inversions develop after ST elevations return to baseline. 2. Global ST segment elevation is seen in early pericarditis. 3. Sinus tachycardia is a common finding. 4. PR segment depression is present in majority of patients. Comments This is a spotter for Any one who has worked in ICCU who will know that Pericarditis is associated with ST Elevations in all leads Tips To Rule out Acute Pericarditis is important, the patient (and the doctor) will be in dire straits if a case of Acute Pericarditis is thrombolysed and it turns into a Haemorrhagic Effusion Question 101. A 56 year old man presents in the casualty with severe chest pain and difficulty in breathing. His ECG was taken immediately. The above ECG suggest the following diagnosis: [* | In-line.WMF 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1.Ventricular fibrillation. 2.Acute pulmonary embolism. 3.Second degree heart block. 4.Atrial fibrillation. Answer 4.Atrial fibrillation. Reference Shamroth Quality: Thinker Status: New Question and New Format QTDF: ECG Strip !!! Discussion The ECG has the following features 1. Varying R-R Interval 2. Absent P waves Explanation 1.Ventricular fibrillation will not have this kind of QRD morphology. 2. Acute pulmonary embolism will not have Irregular Rhythm. 3. Second degree heart block should have P waves. 4. Atrial fibrillation classically is seen with Absent P waves and Varying R R Interval. Comments The only problem before us is that whether the P waves are absent as a result of Printing or were they originally absent Tips Next time you may get a Perfusion Scan or Scintigraphy !!! Be prepared Question 102 Troponin T is preferable to CPK-MB in the diagnosis of acute MI in all of the following situations except 1. bed side diagnosis of MI 2. Post operatively after CABG 3. Reinfarction after 4 days 4. Small Infarcts Answer 3. Reinfarction after 4 days Reference Harrison 15th Edition Chapter 231 and Page 1389 Quality: Spotter for a Intern (who attends his postings regularly J) Status: Repeat QTDF: Harrison Discussion Cardiac-specific troponin T (cTnT) and cardiac-specific troponin I (cTnI) have amino acid sequences different from those of the skeletal muscle forms of these proteins. These differences have permitted the development of quantitative assays for cTnT and cTnI with highly specific monoclonal antibodies. Since cTnT and cTnI are not normally detectable in the blood of healthy individuals but may increase after AMI to levels over 20 times higher than the cutoff value (usually set only slightly above the noise level of the assay), the measurement of cTnT or cTnI is of considerable diagnostic usefulness, and they are now the preferred biochemical markers for MI. The cardiac troponins are particularly valuable when there is clinical suspicion of either skeletal muscle injury or a small MI that may be below the detection limit for CK and CKMB measurements. Levels of cTnI may remain elevated for 7 to 10 days after AMI, and cTnT levels may remain elevated for up to 10 to 14 days. Thus, measurement of cTnT or cTnI has replaced measurement of lactate dehydrogenase (LDH) and its isoenzymes in patients with suspected MI who come to medical attention more than 24 to 48 h after the onset of symptoms. Explanation 1. Troponin T is useful for the bed side diagnosis of MI 2. Troponin T is useful for the diagnosis of Acute MI Post operatively after CABG 3. Troponin T is useful for the diagnosis of Reinfarction after 4 days as they remain elevated for 7 to 10 days 4. Troponin T is useful for the diagnosis of Small Infarcts Comments A Question from Clinical knowledge Tips Attend your postings regularly !!! Question 103. Exercise testing is absolutely contraindicated in which one fo the following : 1.One week following myocardial infarction 2. Unstable angina. 3. Aortic stenosis 4. peripheral vascular dicase. Answer 3. Aortic stenosis Reference Davidson 17th Edition Chapter 5 Page 255-256 Please refer the chart given for management of Unstable Angina Braunwald Table 5 7 Harrison 15th Edition Section 4 : 244 Stable Angina Section1 Pain :13 Chest Discomfort Quality: Thinker Status: New QTDF: Braunwald Discussion CONTRAINDICATIONS TO EXERCISE TESTING Unstable angina with recent rest pain Untreated-life-threatening cardiac arrhythmias Uncompensated congestive heart failure Advanced atrioventricular block Acute myocarditis or pericarditis Critical aortic stenosis Severe hypertrophic obstructive cardiomyopathy Uncontrolled hypertension Acute myocardial infarction (?4-5 days), rest angina - 48 h, unstable rhythm, severe aortic stenosis, acute myocarditis, uncontrolled heart failure, and active infective endocarditis. Acute systemic illness Aortic Stenosis in Braunwald The potential risk of sudden death is a legitimate concern when advising exercise limitations in patients with aortic stenosis. Syncope that precedes sudden death is believed to be initiated by left ventricular baroreceptors activated by an exercise-induced increase in left ventricular pressure or stretch, which causes vasodilatation in skeletal muscle followed by systemic hypotension. Malignant ventricular arrhythmias seldom initiate syncope but are thought to be the chief cause of death after a faint. Syncope-induced hypotension is more likely to provoke disturbances in ventricular rhythm in adults with coexisting coronary artery disease than in younger patients with normal coronary arteries and no myocardial ischemia. Management of Unstable Angina If there are no contraindiacations to surgery or angioplasty, exercise testing should be arranged 3 - 4 weeks later when the plaque has stabilised, with a view to recommending coronary arteriography if the test is positive at a low work load. Chest Discomfort An electrocardiogram is an essential test for adults with chest discomfort that is not due to an obvious traumatic cause. The presence of electrocardiographic changes consistent with ischemia or infarction is associated with high risks of acute myocardial infarction or unstable angina ; such patients should be admitted to a unit with electrocardiographic monitoring and the capacity to respond to a cardiac arrest. The absence of such changes does not exclude acute ischemic heart disease, but the risk of life-threatening complications is low for patients with normal electrocardiograms or only nonspecific ST-T-wave changes. If these patients are not considered appropriate for immediate discharge, they are often candidates for early or immediate exercise testing. Explanation 1.Stress Testing can be done 4-5 days following following myocardial infarction 2. Unstable angina is an indication for Exercise Stress Testing. 3. Aortic stenosis is an Absolute Contraindication 4. Peripheral vascular dicase is not an absolute contraindication. Comments AS and HOCM are important from Entrance point of view Tips Question 104. Cardiac output measured by thermodilution technique is unreliable in all of the following situations except: 1. Ventricular septal defect. 2. Tricuspid regurgitation. 3. Low cardiac output 4. Pumonary regugitation Answer 3. Low cardiac output Reference Harrison 15th Edition Chapter Quality: Reader Status: Repeat QTDF: Harrison Discussion An approach to the measurement of cardiac output during right heart catheterization is the thermodilution technique, in which a thermistor is mounted on the tip of a balloon flotation catheter and positioned in the pulmonary artery. Cold dextrose solution or saline is injected via a proximal port on the catheter into the vena cava or right atrium, and the change in temperature monitored at the thermistor is integrated electronically. This integral is inversely proportional to the volume flow rate past the thermistor, and if the temperatures of the injectate and pulmonary artery blood are measured, cardiac output (actually, pulmonary blood flow) can be calculated. In contrast to the Fick method, the indicator-dilution method is least reliable when the cardiac output is low. Please note that we measure Pulmonary Blood flow and consider it to be equal to systemic blood flow (and this is correct in normal heart). But in certain heart lesions the Pulmonary blood flow is grossly increased and so obviously we cannot take that to be equal to the systemic blood flow Explanation 1. Thermodilution is unreliable in Ventricular septal defect as a part of blood flows into Left Ventricle and so the Actual value is underestimated. If some blood comes into the Right Ventricle, again there is problem 2. Thermodilution is unreliable in Tricuspid regurgitation as a part of blood flows back into Atrium and so the Actual value is underestimated. 3. Thermodilution is least reliable in Low cardiac output, but nevertheless in Low Cardiac Output, the systemic and pulmonary blood flow are SAME 4. Thermodilution is unreliable in Pumonary regugitation as a part of blood flows back into Right Ventricle and so the Actual value is underestimated. Comments Please check yourself and be satisfied. This is all but one interpretationof this question Tips Question 105. Pulmonary hypertension may occur in all of the following conditions except: 1. Toxic oil syndrome. 2. Progressive systemic sclerosis. 3. Sickle cell anaemia. 4. Argemone mexicana poisoning. Answer 4. Argemone mexicana poisoning. Reference Harrison 15th Edition Page 1510 Lippincott Hurst Quality: Reader Status: Repeat QTDF: Dont know Discussion Etiology of Pulmonary Hypertension 1. Primary a. Familial b. Menarche and Pregnancy c. Autoimmune (Raynaud, ANA Antobody) d. Hepatic Cirrhosis e. Fenfluramine f. Cocaine g. Toxic Oil Syndrome Rape Seed Oil h. HIV 2. Secondary to Left Heart Pathology Explanation 1. Toxic oil syndrome causes Pulmonary Hypertension (at least in Spain, if not in Our Country).and the other chemicals causing Chemically induced scleroderma-like disorders are a. Vinyl chloride-induced disease b. Bleomycin-induced fibrosis c. Pentazocine-induced fibrosis d. Epoxy- and aromatic hydrocarbons-induced fibrosis 2. Progressive systemic sclerosis causes Pulmonary Hypertension. 3. Sickle cell anaemia leads to repeated microvascular occlusion of blood flow and then Acute and Sub acute Pulmonary Crisis. 4. Argemone mexicana poisoning is not known to cause Pulmonary Hypertension. Comments L Tips Question 106. Extensive pleural thickening and calcification expecially involving the diaphragmatic pleura are classical features of: 1. Coal workers pneumoconiosis. 2. Asbestosis. 3. Silicosis. 4. Siderosis. Answer 2. Asbestosis. Reference Harrison 15th Edition Chapter 254 Robbins Basic Pathology,Pg-228 Quality: Reader Status: Repeat QTDF: Harrison Discussion Asbestosis is a diffuse interstitial fibrosing disease of the lung that is directly related to the intensity and duration of exposure. Except for its association with a history of exposure to asbestos (generally in a work setting), asbestosis resembles the other forms of diffuse interstitial fibrosis. Usually, moderate to severe exposure has taken place for at least 10 years before the disease becomes manifest. Physiologic studies reveal a restrictive pattern with a decrease in lung volumes. Flow rates are commonly reduced less than would be predicted on the basis of the volume reduction. An early sign of severe disease may be a reduction in diffusing capacity. The chest radiograph can be used to detect a number of manifestations of asbestos exposure as well as to identify specific lesions. Past exposure is specifically indicated by pleural plaques, which are characterized by either thickening or calcification along the parietal pleura, particularly along the lower lung fields, the diaphragm, and the cardiac border. Without additional manifestations, pleural plaques imply only exposure, not pulmonary impairment. Benign pleural effusions may occur, particularly in patients with asbestosis, but are not necessarily restricted to those with overt disease. The fluid is sterile but may be a serous or blood-stained exudate and may occur bilaterally. The effusion may be slowly progressive or may resolve spontaneously. Explanation 1. Coal workers pneumoconiosis is manifested by the appearance on the chest radiograph of nodules ranging from 1 cm in diameter to the size of an entire lobe, generally confined to the upper half of the lungs. 2. Asbestosis classically presents with lower lobe lesions and involvement of diaphragmatic pleura. 3. Silicosis involves upper lobes. 4. Siderosis produces interstitial ibrotic hanges in the lungs. Comments Tips Isnt It an irony!!! that Silica , found below (earth) affects the upper lobes while Asbestos( found in roofs ) affects the lower lobes J Question 107. Which one of the following conditions may lead to exudative pleural effusion 1. Cirrhosis. 2. Nephrotic syndrome. 3. Congestive heart failure. 4. Bronchogenic carcinoma. Answer 4. Bronchogenic carcinoma. Reference Harrison 15th Edition Chapter 262 and Page 1515 Quality: Reader Status: Repeat QTDF: Harrison Discussion Malignant pleural effusions secondary to metastatic disease are the second most common type of exudative pleural effusion. The three tumors that cause approximately 75% of all malignant pleural effusions are lung carcinoma, breast carcinoma, and lymphoma. Most patients complain of dyspnea, which is frequently out of proportion to the size of the effusion. The pleural fluid is an exudate, and its glucose level may be reduced if the tumor burden in the pleural space is high. The diagnosis is usually made via cytology of the pleural fluid. If the initial cytologic examination is negative, then thoracoscopy is the best next procedure if malignancy is strongly suspected. At the time of thoracoscopy, talc or some similar agent should be instilled into the pleural space to effect a pleurodesis. If thoracoscopy is unavailable, then needle biopsy of the pleura should be performed. Patients with a malignant pleural effusion are treated symptomatically for the most part, since the presence of the effusion indicates disseminated disease and most malignancies associated with pleural effusion are not curable with chemotherapy. The only symptom that can be attributed to the effusion itself is dyspnea. If the patients lifestyle is compromised by dyspnea, and if the dyspnea is relieved with a therapeutic thoracentesis, then one of the following procedures should be performed: (1) tube thoracostomy with the instillation of a sclerosing agent such as talc, 5 g in a slurry, or doxycycline, 500 mg; (2) outpatient insertion of a small indwelling catheter; or (3) thoracoscopy with pleural abrasion or the insufflation of talc Explanation 1. Cirrhosis causes transudative Pleural Effusion. 2. Nephrotic syndrome causes transudative Pleural Effusion. 3. Congestive heart failure causes transudative Pleural Effusion. 4. Bronchogenic carcinoma. Comments Transudative and exudative pleural effusions are distinguished by measuring the lactate dehydrogenase (LDH) and protein levels in the pleural fluid. Exudative pleural effusions meet at least one of the following criteria, whereas transudative pleural effusions meet none: 1. pleural fluid protein/serum protein > 0.5 2. pleural fluid LDH/serum LDH > 0.6 3. pleural fluid LDH more than two-thirds normal upper limit for serum If a patient has an exudative pleural effusion, the following tests on the pleural fluid should be obtained: description of the fluid, glucose level, amylase level, differential cell count, microbiologic studies, and cytology Tips Note that Meigs Syndrome has Exudative Pleural Effusion Question 108. Diagnostic features of allergic broncho-pulmonary aspergillosis (ABPA) include all of the following except: 1.Changing pulmonary infiltrates. 2.Peripheral eosinophilia. 3.Serum precipitins against Aspergillosis fumigatus. 4.Occurance in patients with old cavitary lesions. Answer 4.Occurance in patients with old cavitary lesions. Reference Harrison 15th Edition Chapter 206 and Page 1178 Quality: Reader Status: Repeat QTDF: Harrison Discussion Aspergillus can colonize the damaged bronchial tree, pulmonary cysts, or cavities of patients with underlying lung disease. Balls of hyphae within cysts or cavities (aspergillomas), usually in the upper lobe, may reach several centimeters in diameter and may be visible on chest x-ray. Tissue invasion does not occur. The term allergic bronchopulmonary aspergillosis denotes the condition of patients with preexisting asthma who have eosinophilia, IgE antibody to Aspergillus, and fleeting pulmonary infiltrates from bronchial plugging Explanation 1.Changing pulmonary infiltrates is seen in Allergiv Bronchopulmonary Aspergillosis. 2.Peripheral eosinophilia is seen in Allergiv Bronchopulmonary Aspergillosis. 3.Serum precipitins against Aspergillosis fumigatus is seen in Allergiv Bronchopulmonary Aspergillosis. 4. Aspergillus species can colonize the skin and respiratory tract or cause fatal systemic illness. Aspergillus may cause aspergillomas in a previously existing cavity Comments Biopsy is usually required for the diagnosis of invasive aspergillosis of the lung, nose, paranasal sinus, bronchi, or sites of dissemination. Blood cultures are rarely positive, even in patients with infected cardiac valves (native or prosthetic). Detection of galactomannan antigen in serum suggests the diagnosis, but false-positives are frequent, particularly in children. Aspergillus hyphae can be identified presumptively by histology, but culture is required for confirmation and for determination of the species. Only culture can reliably distinguish aspergillosis from pseudallescheriasis; drug therapy for these two diseases differs Tips Treatment with intravenous amphotericin B (1.0 to 1.5 mg/kg daily) has resulted in the arrest or cure of invasive aspergillosis when immunosuppression is not severe. Liposomal amphotericin B at daily doses of 1 to 4 mg/kg has given results that seem roughly comparable to those obtained with amphotericin B deoxycholate. Itraconazole (200 mg twice daily) is useful in some less immunosuppressed patients with indolent or slowly progressive invasive aspergillosis. Question 109. A 25 year old man presented with fever, cough, expectoration and breathlessness of 2 months duration. Contrast enhanced computed tomography of the chest showed bilateral upper lobe fibrotic lessons and mediastinum had enlarged necrotic nodes with peripheral rim enhancement. Which one of the following is the most probable diagnosis? 1. Sarcoidosis. 2. Tuberculosis. 3. Lymphoma. 4. Silicosis. Answer 2. Tuberculosis 4. Silicosis also fits in the diagnosis. Reference Harrison 15th Edition Part Nine - Section 2 - Chap 254 - Environmental Lung Diseases - Occupational.........Analyse the question once more. And note that all the points given in the question paper are there in Harrison Oxford Textbook of Medicine 17.10 Quality: Reader Status: Topic Repeat QTDF: Harrison Discussion Workers exposed through sandblasting in confined spaces, tunneling through rock with high quartz content (15 to 25%), or the manufacture of abrasive soaps may develop acute silicosis with as little as 10 months exposure. The disease may be rapidly fatal in less than 2 years, despite the discontinuation of exposure. A radiographic picture of profuse miliary infiltration or consolidation is characteristic of acute silicosis. In long-term, less intense exposure, small rounded opacities in the upper lobes, with retraction and hilar adenopathy, classically appear on the radiograph after 15 to 20 years. Calcification of hilar nodes may occur in as many as 20% of cases and produces the characteristic eggshell pattern. These changes may be preceded by or associated with a reticular pattern of irregular densities that are uniformly present throughout the upper lung zones. The nodular fibrosis may be progressive in the absence of further exposure, with coalescence and formation of nonsegmental conglomerates of irregular masses in excess of 1 cm in diameter. 17.10.1.Hilar lymphadenopathy if symmetrical is almost always due to sarcoidosis. Tuberculosis and lymphoma (and other malignancies) must always be considered, and these diagnoses are more likely if the changes are unilateral. Lymphadenopathy is rarely observed in other diffuse lung diseases, with the notable exception of silicosis. 17.10.10. Calcification: Amongst patients with long-standing chronic persistent sarcoidosis there is a tendency for the lungs and hilar lymph nodes to show scattered foci of calcification in areas of hyaline fibrosis. On rare occasions, plaque-like or eggshell; calcification may develop in persistently enlarged hilar or mediastinal lymph glands, a finding more characteristic of silicosis. This calcification is dystrophic and not associated with hypercalcaemia. 17.10.16 Clinical features: Silicosis presents a spectrum of clinical appearances depending on the circumstances in which it is contracted. The most severe, acute silicosis, may be acquired from a relatively brief but very heavy exposure such as occurs in sandblasting without respiratory protection. Such patients become intensely breathless and die within months. Explanation Few can argue that Silicosis is not acute and that Silicosis does not have necrotic nodes Oxford text book of Medicine says in Silicosis Calcification occurs in Dystrophic Nodes in a egg shell pattern and there is also ACUTE SILICOSIS I am sure that the word dystrophic means dead and I think that dead is necrotic Comments There is a saying in Clinical Medicine that When you here hoofs, think of Horses and not Zebras. That means that we have to first rule out all the (atypical presentations) of Common entities before diagnosing a rare disease. And the question asks MOST PROBABLE DIAGNOSIS and TB is more common than silicosis. So for this question the answer is Tuberculosis, but the explanation was centred around Silicosis just to appraise you of the facts so that in future if you get this same question with the words Probable Diagnosis / Likely Diagnosis and None of the Above instead of TB as one of the choices, dont choose None you have to think of Silicosis Tips Question 110. A 60 year old male presented to the emergency with breathlessness, facial swelling and dilated veins on the chest wall. The most common cause is: 1. Thymoma 2. Lung Cancer. 3. Hodgkin s lymphoma. 4. Superior vena caval obstruction. Answer 4. Superior vena caval obstruction. Reference Harrison 15th Edition Chapter 102 Quality: Thinker Status: Repeat QTDF: Harrison Discussion Superior vena cava syndrome (SVCS) is the clinical manifestation of superior vena cava (SVC) obstruction, with severe reduction in venous return from the head, neck, and upper extremities. Malignant tumors, such as lung cancer, lymphoma, and metastatic tumors, are responsible for more than 90% of all SVCS cases. Lung cancer, particularly of small-cell and squamous-cell histologies, accounts for approximately 85% of all cases of malignant origin. Metastatic cancers to the mediastinum, such as testicular and breast carcinomas, account for a small proportion of cases. Other causes include benign tumors, aortic aneurysm, thyroid enlargement, thrombosis, and fibrosing mediastinitis caused by prior irradiation or histoplasmosis. Patients with SVCS usually present with neck and facial swelling (especially around the eyes), dyspnea, and cough. Other symptoms include hoarseness, tongue swelling, headaches, nasal congestion, epistaxis, hemoptysis, dysphagia, pain, dizziness, syncope, and lethargy. Bending forward or lying down may aggravate the symptoms. The characteristic physical findings are dilated neck veins, an increased number of collateral veins covering the anterior chest wall, cyanosis, and edema of the face, arms, and chest. More severe cases include proptosis, glossal and laryngeal edema, and obtundation. The clinical picture is milder if the obstruction is located above the azygos vein. The diagnosis of SVCS is a clinical one. The most significant chest radiographic finding is widening of the superior mediastinum, most commonly on the right side. Pleural effusion occurs in only 25% of patients, often on the right side. However, a normal chest radiograph is still compatible with the diagnosis if other characteristic findings are present. Computed tomography (CT) provides the most reliable view of the mediastinal anatomy. The diagnosis of SVCS requires diminished or absent opacification of central venous structures with prominent collateral venous circulation. Magnetic resonance imaging (MRI) has no advantages over CT. Invasive procedures, including bronchoscopy, percutaneous needle biopsy, mediastinoscopy, and even thoracotomy, can be performed by a skilled clinician without any major risk of bleeding. For patients with a known cancer, a detailed workup usually is not necessary, and appropriate treatment may be started after obtaining a CT scan of the thorax. For those with no history of malignancy, a detailed evaluation is absolutely necessary to rule out benign causes and determine a specific diagnosis to direct the appropriate therapy. Explanation Self Explanatory Comments There are few who say that the answer is Lung cancer as it is the most important cause of SVC Obstruction. But this question does not ask the most important cause of SVC Obstruction. This asks the most common cause of breathlessness, facial swelling and dilated veins on the chest wall. The answer is SVC Obstruction Tips If the question is very clear, please dont assume things Question 111. All of the following conditions may predispose to pulmonary embolism except: 1. protein S deficiency. 2. Malignancy. 3. Obesity. 4. Progesterone therapy. Answer 4. Progesterone therapy. Reference Harrison 15th Edition Chapter 261 and Page 1509 Bailey and Love 23rd Edition Page 255, 263 Quality: Reader Status: Repeat QTDF: All books Discussion Rudolf Virchow postulated more than a century ago that three potentially overlapping factors predisposed to venous thrombosis: (1) local trauma to the vessel wall; (2) hypercoagulability; and (3) stasis. We now believe that many patients who suffer pulmonary thromboembolism (Pulmonary Thromboembolism) have an underlying inherited predisposition that remains clinically silent until an acquired stressor occurs such as surgery, obesity, or pregnancy. When Pulmonary Thromboembolism is identified, a detailed family history for venous thromboembolism should be obtained. Explanation 1. Protein S deficiency is a cause of Thromboembolic phenomenon. 2. Malignancy is a cause of Thromboembolic phenomenon.(Remember Trousseaus Sign). 3. Obesity is a cause of Thromboembolic phenomenon. 4. Progesterone therapy does not lead toThromboembolic phenomenon. It is Estrogen which predisposes to Thromboembolic phenomenon. Comments Factor V Leiden The most frequent inherited predisposition to hypercoagulability is resistance to the endogenous anticoagulant protein, activated protein C. The phenotype of activated protein C resistance is associated with a single point mutation, designated factor V Leiden, in the factor V gene. This missense mutation?a single nucleotide substitution of adenine for guanine 1691?causes an amino acid substitution of glutamine for arginine at position 506. Participants with factor V Leiden had a much higher rate of recurrent venous thrombosis than those without. A single-point mutation in the 3? untranslated region of the prothrombin gene (G-to-A transition at nucleotide position 20210) appears to be associated with increased levels of prothrombin (factor II), the precursor of thrombin. The G20210A mutation conferred an approximate doubling of the risk of venous thrombosis. Nevertheless, factor V Leiden is more common than all other (identified) inherited hypercoagulable states, including the prothrombin gene mutation, deficiencies in protein C, protein S, antithrombin III, and disorders of plasminogen. Tips Please Read the risk factors of Pulmonary Embolism Question 112. A 55 year old man who has been on bed rest for the past 10 days, complains of breathlessness and chest pain. The chest X-ray is normal. The next investigation should be: 1. Lung ventilation-perfusion scan. 2. Pulmonary arteriography. 3. Pulmonary venous angiography. 4. Echocardiography. Answer 1. Lung ventilation-perfusion scan. Reference Harrison 15th Edition Chapter 261 Quality: Reader Status: Repeat QTDF: Harrison Discussion Dyspnea is the most frequent symptom of Pulmonary Thromboembolism, and tachypnea is its most frequent sign. Whereas dyspnea, syncope, hypotension, or cyanosis indicate a massive Pulmonary Thromboembolism, pleuritic pain, cough, or hemoptysis often suggest a small embolism located distally near the pleura. On physical examination, young and previously healthy individuals may simply appear anxious but otherwise seem deceptively well, even with an anatomically large Pulmonary Thromboembolism. They need not have classic signs such as tachycardia, low-grade fever, neck vein distention, or an accentuated pulmonic component of the second heart sound. Sometimes, a paradoxical bradycardia occurs. In older patients who complain of vague chest discomfort, the diagnosis of Pulmonary Thromboembolism may not be apparent unless signs of right heart failure are present. Unfortunately, because acute coronary ischemic syndromes are so common, one may overlook the possibility of life-threatening Pulmonary Thromboembolism and may inadvertently discharge these patients from the hospital after the exclusion of myocardial infarction with serial cardiac enzyme measurements and electrocardiograms. The differential diagnosis of Pulmonary Thromboembolism is broad. Although Pulmonary Thromboembolism is known as the great masquerader, quite often another illness simulates Pulmonary Thromboembolism. For example, when the proposed diagnosis of Pulmonary Thromboembolism is supposedly confirmed with a combination of dyspnea, chest pain, and an abnormal lung scan, the correct diagnosis of pneumonia might become apparent 12 h later when an infiltrate blossoms on chest x-ray, purulent sputum is first produced, and high fever and shaking chills develop. Explanation 1. Lung Scanning is the principal imaging test for the diagnosis of Pulmonary Thromboembolism. Small particulate aggregates of albumin labeled with a gamma-emitting radionuclide are injected intravenously and are trapped in the pulmonary capillary bed. A perfusion scan defect indicates absent or decreased blood flow, possibly due to Pulmonary Thromboembolism. Ventilation scans, obtained with radiolabeled inhaled gases such as xenon or krypton, improve the specificity of the perfusion scan. Abnormal ventilation scans indicate abnormal nonventilated lung, thereby providing possible explanations for perfusion defects other than acute Pulmonary Thromboembolism. A high probability scan for Pulmonary Thromboembolism is defined as having two or more segmental perfusion defects in the presence of normal ventilation 2. Selective Pulmonary Angiography is the most specific examination available for establishing the definitive diagnosis of Pulmonary Thromboembolism and can detect emboli as small as 1 to 2 mm. A definitive diagnosis of Pulmonary Thromboembolism depends upon visualization of an intraluminal filling defect in more than one projection. Secondary signs of Pulmonary Thromboembolism include abrupt occlusion (cut-off) of vessels; segmental oligemia or avascularity; a prolonged arterial phase with slow filling; or tortuous, tapering peripheral vessels. 3. Contrast Phlebography has been mostly replaced by ultrasonography. Venography is costly, uncomfortable, and occasionally results in contrast allergy or contrast-induced phlebitis. Contrast phlebography is worthwhile when there is a discrepancy between the clinical suspicion and the ultrasound result. Phlebography is also useful for diagnosing isolated calf vein thrombosis or recurrent DVT. A recently approved nuclear medicine test utilizing a synthetic peptide that binds preferentially to the glycoprotein IIb/IIIa receptors on activated platelets may eventually replace contrast phlebography in clinical practice. This radiopharmaceutical permits scintigraphic imaging of acute DVT and may be especially useful for differentiating acute from chronic DVT. 4. Echocardiography is useful for rapid triage of acutely ill patients who may have Pulmonary Thromboembolism. Bedside echocardiography can usually reliably differentiate among illnesses that have radically different treatment, including acute myocardial infarction, pericardial tamponade, dissection of the aorta, and Pulmonary Thromboembolism complicated by right heart failure. Detection of right ventricular dysfunction due to Pulmonary Thromboembolism helps to stratify the risk, delineate the prognosis, and plan optimal management. Comments Primary therapy consists of clot dissolution with thrombolysis or removal of Pulmonary Thromboembolism by embolectomy. Anticoagulation with heparin and warfarin or placement of an inferior vena caval filter constitutes secondary prevention of recurrent Pulmonary Thromboembolism rather than primary therapy. Primary therapy should be reserved for patients at high risk of an adverse clinical outcome. When right ventricular function remains normal, patients typically have good clinical outcomes with anticoagulation alone Important adjunctive measures include pain relief (especially with nonsteroidal anti-inflammatory agents), supplemental oxygenation, and psychological support. Dobutaminealpha-adrenergic agonist with positive inotropic and pulmonary vasolidating effects?may successfully treat right heart failure and cardiogenic shock. Volume loading should be undertaken cautiously because increased right ventricular dilatation can lead to even further reductions in left ventricular forward output. Tips Theme Couple on Pulmonary Embolism Question 113.The diffusion capacity of lung (DL co)is decreased in all of the following conditions except: 1. Interstitial lung disease. 2. Goodpasturs syndrome. 3. Emphysema. 4. primary pulmonary hypertension. Answer 2. Goodpasturs syndrome. Reference Harrison 15th Edition Page 1433 and Chapter 250 Quality: Reader Status: New QTDF: Harrison Discussion Both O2 and CO2 diffuse readily down their respective concentration gradients through the alveolar wall and pulmonary capillary endothelium. Under normal circumstances, this process is rapid, and equilibration of both gases is complete within one-third of the transit time of erythrocytes through the pulmonary capillary bed. Even in disease states in which diffusion of gases is impaired, the impairment is unlikely to be severe enough to prevent equilibration of CO2 and O2. Consequently, a diffusion abnormality rarely results in arterial hypoxemia at rest. If erythrocyte transit time in the pulmonary circulation is shortened, as occurs with exercise, and diffusion is impaired, then diffusion limitation may contribute to hypoxemia. Exercise testing can often demonstrate such physiologically significant abnormalities due to impaired diffusion. Even though diffusion limitation rarely makes a clinically significant contribution to resting hypoxemia, clinical measurements of what is known as diffusing capacity can be a useful measure of the integrity of the alveolar-capillary membrane Diffusing Capacity The ability of gas to diffuse across the alveolar-capillary membrane is ordinarily assessed by the diffusing capacity of the lung for carbon monoxide (DLCO). In this test, a small concentration of carbon monoxide (0.3%) is inhaled, usually in a single breath that is held for approximately 10 s. The carbon monoxide is diluted by the gas already present in the alveoli and is also taken up by hemoglobin as the erythrocytes course through the pulmonary capillary system. The concentration of carbon monoxide in exhaled gas is measured, and DLCO is calculated as the quantity of carbon monoxide absorbed per minute per mmHg pressure gradient from the alveoli to the pulmonary capillaries. The value obtained for DLCO depends on the alveolar-capillary surface area available for gas exchange and on the pulmonary capillary blood volume. In addition, the thickness of the alveolar-capillary membrane, the degree of / mismatching, and the patients hemoglobin level will affect the measurement. Because of this effect of hemoglobin levels on DLCO, the measured DLCO is frequently corrected to take the patients hemoglobin level into account. The value for DLCO, ideally corrected for hemoglobin, can then be compared with a predicted value, based either on age, height, and gender or on the alveolar volume (VA) at which the value was obtained. Alternatively, the DLCO can be divided by VA and the resulting value for DLCO/VA compared with a predicted value. Although abnormalities in diffusion are rarely responsible for hypoxemia, clinical measurement of diffusing capacity is frequently used to assess the functional integrity of the alveolar-capillary membrane, which includes the pulmonary capillary bed. Diseases that affect solely the airways generally do not lower DLCO, whereas diseases that affect the alveolar walls or the pulmonary capillary bed will have an effect on DLCO. Even though DLCO is a useful marker for assessing whether disease affecting the alveolar-capillary bed is present, an abnormal DLCO does not necessarily imply that diffusion limitation is responsible for hypoxemia in a particular patient. Measurement of DLCO may be useful for assessing disease affecting the alveolar-capillary bed or the pulmonary vasculature. In practice, three main categories of disease are associated with lowered DLCO: interstitial lung disease, emphysema, and pulmonary vascular disease. With interstitial lung disease, scarring of alveolar-capillary units diminishes the area of the alveolar-capillary bed as well as pulmonary blood volume. With emphysema, alveolar walls are destroyed, so the surface area of the alveolar-capillary bed is again diminished. In patients with disease causing a decrease in the cross-sectional area and volume of the pulmonary vascular bed, such as recurrent pulmonary emboli or primary pulmonary hypertension, DLCO is commonly diminished. Diffusing capacity may be elevated if pulmonary blood volume is increased, as may be seen in congestive heart failure. However, once interstitial and alveolar edema ensue, the net DLCO depends on the opposing influences of increased pulmonary capillary blood volume elevating DLCO and pulmonary edema decreasing it. Finding an elevated DLCO may be useful in the diagnosis of alveolar hemorrhage, as in Goodpastures syndrome. Hemoglobin contained in erythrocytes in the alveolar lumen is capable of binding carbon monoxide, so the exhaled carbon monoxide concentration is diminished and the measured DLCO is increased Explanation Self Explanatory Comments Lung Function tests and other function tests are important Tips Question 114. All of the following are associated with low C3 levels except: 1.Post streptococcal glomerulonephritis. 2.Membrano-proliferative Glomerulonephritis. 3.Good pastures disease. 4.Systemic lupus erythematosus. Answer 3.Good pastures disease. Reference Harrison 15th Edition Chapter 274 and Figure 274.1 and Page 1583 Quality: Reader Status: Repeat QTDF: Harrison Discussion Clinically Nephritic Syndrome or RPGN Pathogenically Anti GBM disease Pauci Immune GN Immune Complex GN Some Mimickers Serologically Anti GBM Positive Negative Negative Negative Negative ANCA Negative Positive Negative Negative Negative C3 Normal Normal Low Normal Normal Immunoflourescence Microscopy for Linear IgG and C3 Sparse or Absent IgG and C3 Granular IgG and C3 Granular IgG and C3 Sparse or Absent IgG and C3 DD 1.Anti GBM Disease 2.Good Pastures Syndrome 1.Wegeners 2.Microscopic PAN 3.Renal limited Cresenteric GN 1.Idiopathic ProliferativeGN, Cresenteric GN and MPGN 2.Post Infective GN-ASO, ADNAase 3.Lupus Nephritis-ANA, anti-dsDNA 4.Cryoglobulinaemia(Cryocrit, HCV) 5.Bacterial Endocarditis 6.Shunt Nephritis 1.IgA Nephropathy 2.HSP 3.Fibrillary GN 4.Visceral Abscess 1.Malignant HT 2.HUS/TTP 3.Interstitial Nephritis Scleroderma Crisis Toxemia Atheroemboli Explanation 1.Post streptococcal glomerulonephritis is associated with Low C3. 2.Membrano-proliferative Glomerulonephritis is associated with Low C3. 3.Good pastures disease is associated with Normal C3. 4.Systemic lupus erythematosus is associated with Low C3. Comments The various types of Glomerulonephritis is an often repeated question Tips Question 115. Central nervous system manifestations in chronic renal failure are a result of all of the following, except: 1. Hyperosmolarity. 2. Hypocalcemia. 3. Acidosis. 4. Hyponatremia. Answer 2. Hypocalcemia. Reference Harrison 15th Edition Chapter 270 and page 2221 Quality: Reader Status: Repeat QTDF: Harrison Discussion The total plasma Ca2+ concentration in patients with CRD is often significantly lower than normal. Patients with CRD tolerate the hypocalcemia quite well; rarely is a patient symptomatic from the decreased Ca2+ concentration. This may partly be due to the frequent concomitant acidosis, which offsets some of the neuromuscular effects of hypocalcemia. The hypocalcemia in CRD results from decreased intestinal absorption of Ca2+ due to vitamin D deficiency Explanation 1. Hyperosmolarity causes intra cellular Water depletion and produces neurological manifestations. 2. Hypocalcemia is tolerated because of the Co existent acidosis which increases the amount of free Ion ( Compare tis with hyperventilation and respiratory alkalosis causing Tetany, inspite of a Normal Total Serum Calcium). 3. Acidosis causes CNS symptoms. 4. Hyponatremia causes CNS symptoms. Comments Another question testing the fundamentals of Acid base and Mineral Metabolism Tips Also refer Harrison Page 1553. What do you find L Question 116. Absence seizures are characterized on EEG by: 1. 3Hz spike & wave. 2. 1-2Hz spike & wave. 3. Generalized polysikes. 4. Hyparrythmia. Answer 1. 3Hz spike & wave. Reference Harrison 15th Edition Chapter 360 and Page 2356 Quality: Reader Status: Repeat QTDF: Harrison Discussion Absence Seizures (Petit Mal) are characterized by sudden, brief lapses of consciousness without loss of postural control. The seizure typically lasts for only seconds, consciousness returns as suddenly as it was lost, and there is no postictal confusion. Although the brief loss of consciousness may be clinically inapparent or the sole manifestation of the seizure discharge, absence seizures are usually accompanied by subtle, bilateral motor signs such as rapid blinking of the eyelids, chewing movements, or small-amplitude, clonic movements of the hands. Absence seizures usually begin in childhood (ages 4 to 8) or early adolescence and are the main seizure type in 15 to 20% of children with epilepsy. The seizures can occur hundreds of times per day, but the child may be unaware of or unable to convey their existence. This can lead to a situation in which the patient is constantly struggling to piece together experiences that have been interrupted by the seizures. Since the clinical signs of the seizures are subtle, especially to new parents, it is not surprising that the first clue to absence epilepsy is often unexplained daydreaming and a decline in school performance recognized by a teacher. The electrophysiologic hallmark of typical absence seizures is a generalized, symmetric, 3-Hz spike-and-wave discharge that begins and ends suddenly on a normal EEG background. Periods of spike-and-wave discharges lasting more than a few seconds usually correlate with the clinical signs, but the EEG often shows many more periods of abnormal cortical activity than were suspected clinically. Hyperventilation tends to provoke these electrographic discharges and even the seizures themselves and is routinely used when recording the EEG Explanation 1. 3Hz spike & wave. 2. 1-2Hz spike & wave. 3. Generalized polysikes. 4. Hyparrythmia. Comments Tips Know the types of Epilepsy Question 117. Commonest presentation of neurocysticercosis is: 1. Seizures. 2. Focalneurological deficits. 3. Dementia. 4. Radiculopathy. Answer Ans. 1 Reference Harrison 15th Edition Chapter 223 and Page 1249 Quality: Reader Status: Repeat QTDF: Harrison Discussion Intestinal infections with T. solium may be asymptomatic. Epigastric discomfort, nausea, a sensation of hunger, weight loss, and diarrhea are infrequent. Fecal passage of proglottids may be noted by patients. In cysticercosis, the clinical manifestations are entirely different. Cysticerci can be found anywhere in the body, most commonly in the brain and the skeletal muscle. The clinical presentation of cysticercosis depends on the number and location of cysticerci as well as the extent of associated inflammatory responses or scarring. Neurologic manifestations are the most common. When inflammation surrounds cysticerci in the brain parenchyma, seizures are frequent. These seizures may be generalized, focal, or Jacksonian. Hydrocephalus results from obstruction of cerebrospinal fluid (CSF) flow by cysticerci and accompanying inflammation or by CSF outflow obstruction from arachnoiditis. Signs of increased intracranial pressure, including headache, nausea, vomiting, changes in vision, dizziness, ataxia, or confusion, are often evident. Patients with hydrocephalus may develop papilledema or display altered mental status. When cysticerci develop at the base of the brain or in the subarachnoid space, they cause chronic meningitis or arachnoiditis, communicating hydrocephalus, or strokes Minor diagnostic criteria include the presence of subcutaneous nodules, punctate soft tissue or intracranial calcifications, clinical manifestations suggestive of neurocysticercosis (such as seizures, hydrocephalus, or altered mental status), or disappearance of lesions in conjunction with anticysticercal drug therapy. Explanation Self Explanatory Comments Primary major diagnostic criterion. cystic lesions with or without enhancement (e.g., ring enhancement), one or more calcifications (which may also have associated enhancement), or focal enhancing lesions. Treatment Intestinal T. solium infection o Single dose of praziquantel (5 to 10 mg/kg). However, praziquantel can evoke an inflammatory response in the central nervous system if concomitant cryptic cysticercosis is present. Neurocysticercosis o Symptomatic treatment of seizures or hydrocephalus. Seizures can usually be controlled with anticonvulsants. o Antiparasitic drugs, Praziquantel (50 to 60 mg/kg daily in three divided doses for 15 days or 100 mg/kg in three doses given over a single day) or Albendazole (15 mg/kg per day for 8 to 28 days). Both agents may exacerbate the inflammatory response around the dying parasite, exacerbating seizures or hydrocephalus. To be carefully monitored. o High-dose glucocorticoids can be used during treatment or if symptoms worsen. Since glucocorticoids induce first-pass metabolism of praziquantel and may decrease its antiparasitic effect, cimetidine should be coadministered to inhibit praziquantel metabolism. Tips Question 118. Which of the following is the most common location of hypertensive hemorrhage? 1. Pons. 2. Thalamus. 3. Putamen/external capsule. 4. Subcortical white matter. Answer 3. Putamen/external capsule. Reference Harrisons 15th Edition Chapter 361 Page 2386 Robbins 6th Edition Page 1310 Quality: Final MBBS Status: Repeat QTDF: All books Discussion Hypertensive parenchymal hemorrhage (hypertensive hemorrhage or hypertensive intracerebral hemorrhage) usually results from spontaneous rupture of a small penetrating artery deep in the brain. The most common sites are the basal ganglia (putamen, thalamus, and adjacent deep white matter), deep cerebellum, and pons. When hemorrhages occur in other brain areas or in nonhypertensive patients, greater consideration should be given to hemorrhagic disorders, neoplasms, vascular malformations, and other causes. The small arteries in these areas seem most prone to hypertension-induced vascular injury. The hemorrhage may be small or a large clot may form and compress adjacent tissue, causing herniation and death. Blood may dissect into the ventricular space, which substantially increases morbidity and may cause hydrocephalus. If the patient survives, the clot liquefies, is absorbed, and leaves only a small residual cleft. The putamen is the most common site for hypertensive hemorrhage, and the adjacent internal capsule is invariably Explanation Self Explanatory Comments Hypertension is the leading cause of primary intracerebral hemorrhage. Prevention is aimed at reducing hypertension, excessive alcohol use, and use of illicit drugs such as cocaine and amphetamines. Tips Of late more and more questions are being asked from the Final Year Topics the topics most extensively studied for Clinical Exams. In this question paper, we have questions from Mumurs, Clicks, Tone, Tracts, Squints, Aneurysms, Tumours etc Question 119. A 60 year-old man with diabetes mellitus presents with painless, swollen right ankle joint. Radiographs ofthe ankle show destroyed joint with large number ofloose bodies. The most probable diagnosis is: 1. Charcot s joint 2. Cluttons joint. 3. Osteoarthritis. 4. Rheumatoid arthritis. Answer 1. Charcot s joint Reference Harrisons,15th Edition Chapter 325 and Pg-2007 Quality: Reader Status: Repeat QTDF: Harrison Discussion Neuropathic joint disease (Charcots joint) is a progressive destructive arthritis associated with loss of pain sensation, proprioception, or both. In addition, normal muscular reflexes that modulate joint movement are decreased. Without these protective mechanisms, joints are subjected to repeated trauma, resulting in progressive cartilage and bone damage. Neuropathic arthropathy was first described by Jean-Martin Charcot in 1868 in patients with tabes dorsalis. The term Charcot joint is commonly used interchangeably with neuropathic joint. Today, diabetes mellitus is the most frequent cause of neuropathic joint disease. A variety of other disorders are associated with neuropathic arthritis including leprosy, yaws, syringomyelia, meningomyelocoele, congenital indifference to pain, peroneal muscular atrophy (Charcot-Marie-Tooth disease), and amyloidosis. An arthritis resembling neuropathic joint disease is seen in patients who have received frequent intraarticular glucocorticoid injections into a weight-bearing joint and in patients with calcium pyrophosphate dihydrate crystal deposition disease. The distribution of joint involvement depends on the underlying neurologic disorder In tabes dorsalis, knees, hips, and ankles are most commonly affected; in syringomyelia, the glenohumeral joint, elbow, and wrist; and in diabetes mellitus, the tarsal and tarsometatarsal joints. Explanation 1. Charcot s joint is the most specific diagnosis for this case 2. Bilateral knee effusions are known as Cluttons joints.. 3. A diagnosis of Osteoarthritis is less specific for this case. 4. A diagnosis of Rheumatoid arthritis is less specific for this case.. Comments Charcot-Bottcher crystalloids o Spindle-shaped crystalloids 10 to 25 um long, found in human Sertoli cells. Charcot-Bouchard aneurysm : miliary aneurysm o Dilatation in the diameter of small arteries and arterioles secondary to lipohyalinosis from long-standing hypertension associated with intracerebral haematomas. Charcot-Leyden crystals : asthma crystals, Charcot-Neumann crystals, Charcot-Robin crystals, Leydens crystals. o Crystals in the shape of elongated double pyramids, formed from eosinophils, found in the sputum in bronchial asthma and in other exudates or transudates containing eosinophils. Charcot-marie disease o A hereditary motor and sensory neuropathy transmitted as an autosomal dominant trait and characterised by progressive distal wasting and loss of reflexes in the muscles of the legs (occasionally of the arms). Onset is usually in the second to fourth decades. Charcot-Marie-Tooth disease o A slowly progressive genetic disorder which is the most common of the inherited peripheral neuropathies, and encompasses a family of disorders characterised by distal muscle weakness and diminished nerve conduction velocity, due to the destruction of nerves with degeneration of the myelin sheath. Features include muscle atrophy in the feet and the legs, progressing to the hands and arms, often with foot drop and a slapping gait. o The predominant variety, designated CMT1, is an autosomal dominant disorder caused, in most cases, by duplication of a very large (1.5 Mb) region on chromosome 17p11.2-12. A related condition, hereditary neuropathy with liability to pressure palsies (HNPP), is associated with a large deletion in the same general region. o There is no specific treatment for this disorder. Charcots arteries : lenticulostriate arteries, lateral striate arteries o Any one of a variety of small arterys entering the base of the brain through the anterior perforated substance and supplying the striatum, globus pallidus, and internal capsule; most of these perforating arteries are branches of the M1 segment (clinical terminology) of the middle cerebral and and (rarely) of the anterior choroidal artery. Charcots disease o Amyotrophic lateral sclerosis Charcots foot o A foot disease associated with diabetic neuropathy that results in destruction of joints and soft tissue. Charcots gait o The gait of hereditary ataxia. Charcots intermittent fever o Fever, chills, right upper quadrant pain, and jaundice associated with intermittently obstructing common duct stones. Charcots joint o A joint that is deprived of any pain or position sense due to severe osteoarthritis. May also occur as the result of tabes dorsalis, diabetic neuropathy, amyloidosis or leprosy. Often treated with surgical fusion. Charcots syndrome : intermittent claudication o A symptom complex characterised by leg pain and weakness brought on by walking, with the disappearance of the symptoms following a brief rest. Charcots triad o In multiple (disseminated) sclerosis, the three symptoms: nystagmus, tremor, and scanning speech, combination of jaundice, fever, and upper abdominal pain that occurs as a result of cholangitis. Charcots vertigo o Tussive syncope Charcot-Weiss-Baker syndrome : carotid sinus syndrome o Stimulati on of a hyperactive carotid sinus, causing a marked fall in blood pressure due to vasodilation, cardiac slowing, or both; syncope with or without convulsions or A-V block may occur. Erb-Charcot disease : spastic diplegia : Erb-Charcot disease, infantile diplegia, Littles disease, spastic spinal paralysis, tabes spasmodica o A type of cerebral palsy in which there is bilateral spasticity, with the lower extremities more severely affected. Tips All Question papers will have questions on Joints and Arthritis Question 120. Following are the reatures of corticospinal involvement except; 1. Cog-wheel rigidity. 2. Spasicity. 3. Planter extensor response. 4. Exaggerated deep tendon reflexes. Answer 1. Cog-wheel rigidity. Reference Hutchison 21st Edition Page 265 Macleod 10th Edition Page 217 Harrison 15th Edition Table 356-3. The Neurologic Examination Quality: Spotter I Clinical Status: Repeat QTDF: !!! Discussion Every one who has passed MBBS will know that extensor plantar and exaggerated DTR (Deep Tendon Reflexes) are seen in Lesions of Pyramidal Tract . Let us see few points about Tone Muscle tone is tested by resistance to passive motion of a relaxed limb. During testing, it is useful to distract the patient from the examination to minimize active movements. In the upper limbs, tone is assessed by o repetitive pronation and supination of the forearm and o by rolling the hand at the wrist. In the lower limbs, tone is assessed by o the examiners hands are placed behind the thighs and rapidly raised; with normal tone the ankles drag along the table surface for a variable distance before rising, whereas increased tone results in an immediate lift of the heel off the surface. Decreased tone is most commonly due to o lower motor neuron, o peripheral nerve, or o cerebellar pathway disorders. Increased tone may be evident as o spasticity Resistance determined by the angle and direction of motion; (Nut Cracker) Corticospinal tract disease, o Rigidity Similar resistance at all angles of motion; (Lead Pipe) Extrapyramidal disease One frequently observed type of rigidity is the cogwheel rigidity of Parkinsons disease, in which passive motion elicits jerky interruptions in resistance. o Paratonia/Gegenhalten Fluctuating changes in resistance to repetitive passive movements; Frontal lobe pathways. Explanation 1. Cog-wheel rigidity is seen in Parkinsonism. 2. Spasicity is a hall mark of Pyramidal Tract. 3. Planter extensor response is often the first sign of Cortico spinal Tract. 4. Exaggerated deep tenedon reflexes is seen. Comments Often hypotonia is associated with decreased DTR and vice versa. However be careful in conditions like Cerebral Palsy where the exception is often the rule Tips Question 121. A lesion of ventrolateral part of spinal cord will lead to loss (below the level of lesion) of: 1.Pain sensation on the ipsilateral side. 2.Proprioception on the contralateral side. 3.Pain sensation on the contralateral side. 4.propriception on the ispilateral side. Answer 3.Pain sensation on the contralateral side. Reference Hutchison Macleod 10th Edition Page 226, Figure 6.44 Ganong 20th Edition Page 133 Quality: Spotter I Clinical Status: Repeat QTDF: All books Discussion To trivial a fact to merit discussion, yet.. Posterior Column carries Light touch, Position, Proprioception, Vibration on the same side and the Pain and Temperature are carried by the anterolateral columns. A point to be noted here is that the pain fibres cross after a few segments Explanation 1.Pain sensation on the ipsilateral side in rare cases at few segments. 2.Proprioception on the contralateral side will never be affectes. 3.Pain sensation on the contralateral side will be affected. 4.Propriception on the ispilateral side will be affected in the lesions of posterior column. Comments Please read Brown Sequard Syndrome Tips Hutchison, Macleod and Das gave answers to a substantial number of Questions in this AIPG 2003. May be the same trend will contuniue in future too. Be prepared Question 122. A 15 year old healthy boy with no major medical problem complaints that he breaks out with blocky areas of erythema that are pruritic over skin of his arm, leg and trunk every time within an hour of eating sea foods. The clinical features are suggestive of: 1. Localised immune-complex deposition. 2. Cell mediated hypersensitivity. 3. Locallized anaphylaxis. 4. Release of complement C3b. Answer 3. Locallized anaphylaxis. Reference Rook Quality: Thinker Status: New QTDF: Rook Discussion Type I Hypersensitivity can be localized or Generalised. Both of these happen when an allergen is introduced into the body. This in turn triggers a serious of reactions involving the IgE and Mast cells/Basophils and we get the classic picture. A example to the generalized reaction is the Anaphylaxis following Injection with Penicillin. The anaphylaxis can also be localized, as it is in this case. The local anaphylaxis usually presents with Urticaria, Hay feverm Allergic Rhinitis, Allergic Bronchial Asthma, Allergic Gastroenteritis etc. Some times the reaction happens at the site of contact with the antigen, Sometimes it may happen at a different site. The example of the former is the allergic Rhinitis and the latter is the Urticaria following eating certain foods, usually sea food. Explanation 1. Localised immune-complex deposition is Type III Reaction. 2. Cell mediated hypersensitivity is Type IV. 3. This is the classical description for Localized anaphylaxis. 4. C3b is for Opsonisation. In fact C3b and IgG are the main Opsonins Comments Of the two reactions occurring on the surface of the cells, type I hypersensitivity, mediated by IgE (immediate type or anaphylactic hypersensitivity), is of greatest interest to the allergist. In this circumstance, circulating basophils and tissue mast cells, the latter strategically located around blood vessels, become sensitized through the binding of IgE antibodies to their surface receptors. This is the initial event in the production of immune tissue injury following allergen interaction with cell-bound IgE antibody molecules; the ultimate outcome of the reaction depends on a broad spectrum of secondary events involving various types of lymphoid cells, inflammatory cells, mediator-producing cells, and the soluble products derived not only from all of these cells but from other tissues (platelets, endothelial cells) at the site of the reaction. For example, in particularly intense allergen-induced reactions in the skin, the initial wheal and flare does not entirely disappear but is replaced by an inflammatory lesion that reaches its maximal size at 6-12 hr and disappears in 24-72 hr. This late cutaneous response depends upon recruitment of inflammatory cells (polymorphonuclear leukocytes, eosinophils, and mononuclear cells) by chemotactic factors released in the early response. Late-phase reactions also occur in the lung and nose. The terms reaginic IgE, IgE reagins, and homocytotropic antibodies refer to molecules with activities against specific allergens, such as ragweed pollen, whereas nonspecific IgE molecules are found in the serum and tissues of all normal individuals. The normal role of IgE antibody appears to be to defend the host against tissue-invasive parasites. In humans the ability to induce antigen-specific release of mediators from mast cells and basophils is principally confined to antibodies of the IgE class. IgE antibodies, like IgA antibodies, are synthesized by plasma cells located predominantly under mucosal surfaces and particularly in the respiratory and gastrointestinal tracts. IgE-forming plasma cells arise following antigen-stimulated differentiation of B cells or their precursors. Chemical modifications of antigens used in immunotherapy of allergic diseases suppress IgE responses. Although the control of IgE antibody production is better known for animals than for humans, there is good reason to believe that similar mechanisms occur in the human. The association of IgE responses with HLA-linked immune response (IR) genes has been shown for several allergens (ragweed antigen Ra3 and HLA-A2, ragweed antigen Ra5 and HLA-B7, rye grass antigen I and HLA-B8). IgE synthesis in general, and specifically hypersensitivity, is genetically determined by immune cells, probably the specific helper T cells. Bone marrow transplantation from an atopic donor to a nonatopic recipient transfers the allergic diathesis to the recipient. Macrophages and dendritic cells process antigen for presentation to CD4 (helper T) cells, which are activated by interleukin (IL)-1. As a result, these T cells differentiate into TH2 cells, which after activation by processed antigen can synthesize IL-3, IL-4, IL-5, and granulocyte-macrophage colony-stimulating factor (GM-CSF) as well as other cytokines. IL-4 plays an important role in isotype switching of B cells from synthesis of IgM and IgG to synthesis of IgE. For optimal IgE synthesis, IL-5 (a non-isotype B cell growth factor) and IL-6 (a nonisotype B cell differentiation factor) are also needed. IL-5 and GM-CSF also induce eosinophil differentiation. IL-3 and IL-4 are mast cell growth factors. Gamma interferon, produced by another subset of T lymphocytes, can inhibit IL-4{endash}dependent IgE synthesis and IL-4{endash}induced expression of low-affinity IgE receptors (CD23) on B cells. Once formed, IgE antibody becomes reversibly bound or fixed to surface receptors of mast cells and basophils. The binding of IgE to its receptor (FER) involves the C4 and C3 domains of the Fc portion of the immunoglobulin molecule. In nonatopic individuals, only 20-50% of the receptors are occupied by IgE molecules. In atopic individuals with high serum IgE concentrations, a larger percentage, up to almost 100%, of their basophil and mast cell receptors is occupied by IgE. Once binding of IgE occurs, the basophils and mast cells are sensitized. Upon subsequent contact with this specific allergen, and if cell-bound IgE molecules are sufficiently numerous, allergen may bridge adjacent IgE molecules, causing an interaction between the IgE receptors. This causes a series of biochemical reactions (activation of methyltransferases, phospholipid methylation, Ca2+{plus} influx, and activation of the phospholipid diacylglycerol cycle). This results in fusion of the mast cell granules with the mast cell plasma membrane, causing release of pharmacologically active substances (such as histamine), known as chemical mediators. The released mediators act on tissue receptors to cause symptoms. The reaction is largely reversible; the mast cells and basophils participating in the reaction are not lysed, and the effects of mediators are only temporary. Although aggregated IgE can fix late components of the complement system through an alternative pathway, participation of the complement system in IgE-mediated hypersensitivity disorders has not been shown. Newly synthesized chemical mediators are released by the mast cell 6{endash}8 hr after antigenic stimulation. Thus, the late-phase reaction may last 12-48 hr. Interactions of cytokines with endothelial cells are important in localization of eosinophils at the site of the allergic reaction. Activation of endothelial cells by IL-1 causes upregulation of endothelial adhesion molecules, including E-selectin (endothelial leukocyte adhesion molecule-1), intercellular adhesion molecule-1 (ICAM-1), and vascular cell adhesion molecule-1 (VCAM-1). Endothelial activation by IL-4 results in upregulation of VCAM-1. Lectin-binding regions of selectins interact with ligands on leukocytes, causing rolling of leukocytes over endothelial cells. Interactions with the integrins, ICAM-1 and VCAM-1, then arrest the leukocytes, facilitating movement out of the vasculature at the site of the allergic reaction. The ligand for VCAM-1 is very late activation antigen-4; it is found on eosinophils but not neutrophils. Tips The usual tests for inhalant or food sensitivity make use of the reaction that occurs on the surface of mast cells between antigen and IgE antibody. Small amounts of extracts of pollens, molds, danders, and foods are introduced into the patients skin by scratch, puncture, or intradermal techniques. If IgE antibody specific for the test antigen is bound to the subjects mast cells, the interaction of injected antigen with cell-bound IgE releases histamine, a potent vasoactive agent that causes increased capillary permeability and dilatation and axon reflex stimulation, leading to the familiar wheal and flare reaction. The prototypic anaphylactic or IgE-mediated disease is ragweed hay fever. Others include anaphylactic reactions to insect venom, food-induced urticaria, and allergic conjunctivitis or rhinitis. Question 123. Which of the following increases the susceptibility to coronary artery disease: 1. Type V hyperlipoproteinaemia. 2. Von will Brandt s disease. 3. Nephritic syndrome. 4. Systemic lupus erythematosus. Answer 4. Systemic lupus erythematosus. Reference Harrison 15 Ed - Part Eight - Section 3- Chap 240 - Cardiac tumours ............. Quality: Thinker Status: New Question from an old topic QTDF: Harrison Discussion About the involvement of CVS in SLE, Pericarditis is common, occurring in about two-thirds of patients, and generally pursues a benign course, although rarely tamponade or constriction may result. The characteristic endocardial lesions of SLE, described by Libman and Sacks, consist of wartlike lesions most often located at the angles of the AV valves or on the ventricular surface of the mitral valve. Hemodynamically important valvular regurgitation is rare. Patients with the antiphospholipid syndrome have a higher incidence of cardiovascular abnormalities, including valvular disease (particularly regurgitant lesions), a variety of thrombotic disorders (venous and arterial thrombosis, thrombocytopenia, premature stroke), myocardial infarction, pulmonary hypertension, and cardiomyopathy. Myocarditis generally parallels the activity of the disease, and although common histologically, seldom results in clinical heart failure unless associated with hypertension. Although arteritis of large coronary arteries may rarely result in myocardial ischemia, there is also an increased frequency of coronary atherosclerosis that may be related to hypertension or glucocorticoid therapy. Explanation 1. With reference to the table in Harper dealing with hyperlipaedemias, CAD do occur in Type V hyper lipaedemia 2. Von will Brandt s disease is a bleeding disorder. 3. Nephritic syndrome in not even in the fray. 4. Systemic lupus erythematosus causes increased frequency of Coronary Atherosclerosis and Myocardial Infarction. Comments Harper and Harrison give 2 answers and both are in the Q.Paper in different choices. We go by Harrison Tips So far the questions used to come from Renal involvement in SLE. Now the system has changed. And I am sure you will be preparing SLE thoroughly Question 124. A 23- year old woman has experience episod of myalgias, pleural effusion, peicarditis and arthralgias without joint deformity over course of several years.The best laboratory screening test to diagnose her disease would be: 1. CD4 Lymphocyte count. 2. Erythrocyte sedimentation rate. 3. Antinuclear antibody. 4. Assay for thyroid hormones. Answer 3. Antinuclear antibody. Reference Harrison Chapter 311 Quality: Reader Status: Repeat QTDF: Harrison Discussion Clinical Manifestations of SLE are Systemic o Fatigue, malaise, fever, anorexia, nausea, weight loss Musculoskeletal o Arthralgias/myalgias- Almost all patients - most develop intermittent arthritis o Nonerosive polyarthritis o Hand deformities o Myopathy/myositis - Myopathy can be inflammatory (during periods of active disease), or secondary to treatment (hypokalemia, glucocorticoid myopathy, hydroxychloroquine myopathy). o Pain is often out of proportion to physical findings. o Symmetric fusiform swelling in joints [most frequently proximal interphalangeal (PIP) and metacarpophalangeal (MCP) joints of the hands, wrists, and knees], diffuse puffiness of hands and feet, and tenosynovitis can be seen. o Joint deformities are unusual, with 10% of patients developing swan-neck deformities of fingers and ulnar drift at MCP joints. o Erosions are rare; subcutaneous nodules occur. o Ischemic necrosis of bone is a common cause of hip, knee, or shoulder pain in patients receiving glucocorticoids Cutaneous o Malar rash o Discoid rash o Photosensitivity o Oral ulcers o Other rashes?maculopapular, urticarial, bullous, subacute cutaneous lupus o Alopecia o Vasculitis o Panniculitis Hematologic o Anemia (of chronic disease) o Hemolytic anemia o Leukopenia (?4000/mm3) o Lymphopenia (?1500/mm3) o Thrombocytopenia (?100,000/mm3) o Circulating anticoagulant o Splenomegaly o Lymphadenopathy Neurologic o Cognitive dysfunction o Mood disorder o Headache o Seizures o Mono- or polyneuropathy o Cerebrovascular disease o Demyelinating syndrome o Acute confusional state o Movement disorder o Aseptic meningitis o Myelopathy o Other (see text) Cardiopulmonary o Pericarditis is the most frequent manifestation of cardiac lupus; effusions can occur and occasionally lead to tamponade; constrictive pericarditis is rare. o Myocarditis can cause arrhythmias, sudden death, and/or heart failure. o Valvular insufficiency (usually aortic or mitral) can occur, with or without Libman-Sacks endocarditis. Lesions on valves are best detected by transesophageal echocardiography. o Myocardial infarcts usually result from degenerative disease, although they can result from vasculitis. o Coronary artery disease o Pleurisy and pleural effusions are common manifestations of SLE. o Lupus pneumonitis causes fever, dyspnea, and cough; x-rays show fleeting infiltrates and/or areas of platelike atelectasis; this syndrome responds to glucocorticoids. o However, the most common cause of pulmonary infiltrates in patients with SLE is infection. o Interstitial pneumonitis leading to fibrosis occurs occasionally; the inflammatory phase may respond to treatment; the fibrosis does not. o Pulmonary hypertension is an uncommon, grave manifestation of SLE. Infrequent pulmonary manifestations with high mortality rates include adult respiratory distress syndrome and massive intraalveolar hemorrhag o ARDS/hemorrhage Renal o Proteinuria ?500 mg/24 h o Cellular casts o Nephrotic syndrome o Renal failure Gastrointestinal o Nonspecific (anorexia, nausea, mild pain, diarrhea) o Vasculitis with bleeding or perforation o Ascites o Abnormal liver enzymes Thrombosis o Venous o Arterial Fetal loss Ocular o Retinal vasculitis o Conjunctivitis/episcleritis o Sicca syndrome Diagnosis Autoantibodies in Patients with SLE Incidence, % Antigen Detected Clinical Importance Antinuclear antibodies 98 Multiple nuclear Human cell substrates are more sensitive than murine. Repeatedly negative tests make SLE unlikely. Anti-DNA 70 DNA (ds) Anti-dsDNA is relatively disease-specific; anti-ssDNA is not. High titers are associated with nephritis and clinical activity in some patients. Anti-Sm 30 Protein complexed to 6 species of small nuclear RNA Specific for SLE. Total functional hemolytic complement (CH50) levels are the most sensitive measure of complement activation but are also most subject to laboratory error. Quantitative levels of C3 and C4 are widely available. Very low levels of CH50 with normal levels of C3 suggest inherited deficiency of a complement component, which is highly associated with SLE and with ANA negativity Explanation 1. CD4 Lymphocyte count does not given much information about SLE. 2. Erythrocyte sedimentation rate is inferior to ANA in diagnosing SLE. 3. Antinuclear antibody is the most sensitive test for SLE. 4. Assay for thyroid hormones is not useful as this patient has SLE. Comments Theme Couple Tips SLE is an important topic Question 125. Which of the following is not true about Berger s disease? 1. The pathologic changes are proliferative and usually confined to measangial cells: 2. Hematuria may be gross or microscopic. 3. On immunofluorescence deposits contain both IgA and IgG. 4. Absence of associated protyeinuria is pathognomonic. Answer 4. Absence of associated protyeinuria is pathognomonic. Reference Harrison 15th Edition Chapter 274 Robbins ,Page 962 Quality: Thinker Status: New QTDF: Harrison Discussion IgA Nephropathy or Bergers Disease Is the most common glomerulopathy worldwide HLA-B35 appears to be more common in French patients. Most cases are idiopathic. The renal and serologic abnormalities in IgA nephropathy and Henoch-Schonlein purpura are indistinguishable, and most authorities consider these to be a spectrum of a single disease. Less commonly, IgA nephropathy is found in association with systemic diseases, including o chronic liver disease, o Crohns disease, o gastrointestinal adenocarcinoma, o chronic obstructive bronchiolitis, o idiopathic interstitial pneumonia, o dermatitis herpetiformis, o mycosis fungoides, o leprosy, o ankylosing spondylitis, o relapsing polychondritis, and o Sjogrens syndrome. In many of these conditions, IgA is deposited in the glomerulus without inducing inflammation, and this may be a clinically insignificant consequence of perturbed IgA homeostasis. Patients with IgA nephropathy typically present with gross hematuria, often 24 to 48 h after a pharyngeal or gastrointestinal infection, vaccination, or strenuous exercise. Other cases are diagnosed upon detection of microscopic hematuria during routine physical examinations. Hypertension (20 to 30%) and nephrotic syndrome (~10%) are unusual at presentation. Light microscopy of renal biopsy specimens typically shows mesangial expansion by increased matrix and cells. Diffuse proliferation, cellular crescents, interstitial inflammation, and areas of glomerulosclerosis may be evident in severe cases. The diagnostic finding, for which the disease is named, is mesangial deposition of IgA, detected by immunofluorescence microscopy. C3 is usually detected in the area of immune deposits, and IgG is observed in 50% of cases. Electron microscopy reveals electron-dense deposits in the mesangium and, in severe cases, these extend into the paramesangial subendothelial space. TREATMENT There is no proven therapy for IgA nephropathy. suggested a benefit of o fish oils in patients with progressive disease and heavy proteinuria; o A trial of high-dose glucocorticoids with or without cytotoxic agents brosis, and arteriolar hyalinosis. Explanation 1. The pathologic changes are proliferative and usually confined to measangial cells: 2. Hematuria may be gross or microscopic. 3. On immunofluorescence deposits contain both IgA and IgG. 4. Proteinuria is present in 50 %pathognomonic. Comments Repeated Topic Tips Question 126. The syndrome of inappropriate antidiuretic hormone is characterized by the following 1. Hyponatremia and urine sodium excretion >20meq/l. 2. Hypernatremia and urine sodium excretion < 20meq/l. 3. Hyponatremia and hyperkalemia. 4. Hypernatremia and hypokalemia. Answer 1. Hyponatremia andurine sodium excretion >20meq/l. Reference Harrison 15th Edition Chapter 49 and Page 2059 Quality: Spotter Status: New QTDF: Harrison Discussion SIADH is characterized by hypoosmotic hyponatremia in the setting of an inappropriately concentrated urine (urine osmolality greater than 100 mosmol/kg). Patients are typically normovolemic and have normal Na+ balance. They tend to be mildly volume expanded secondary to water retention and have a urine Na+ excretion rate equal to intake (urine Na+ concentration usually greater than 40 mmol/L). By definition, they have normal renal, adrenal, and thyroid function and usually have normal K+ and acid-base balance. SIADH is often associated with hypouricemia due to the uricosuric state induced by volume expansion. In contrast, hypovolemic patients tend to be hyperuricemic secondary to increased proximal urate reabsorption Explanation 1. Hyponatremia and urine sodium excretions>20meq/l is seen in SIADH. 2. Hypernatremia and urine sodium excretion < 20meq/l is seen in Diabetes Insipidus. 3. Hyponatremia and hyperkalemia occurs in Addisons. 4. Hypernatremia and hypokalemia occurs in Cushings. Comments This question can be answered with knowledge of Physiology alone !!! Tips Acid Base and Electrolytes Balance as well as Endocrinology are Important Topics MICROBIOLOGY : 12 Questions The break up of the questions show the following trend General Micro 2 Immunology 1 (Other questions are elsewhere( Bacteriology 6 Virology 2 Mycology 0 (More questions in Skin / Medicine) Parasitology 1 And as usual Disinfection, sterilization and Vaccination rule over others Question. 127. A chest physician performs bronchoscopy in the procedure room of the out patient department. To make the instrument safe for use in the next patient waiting outside. The most appropriate method to disinfect the endoscope is by: 1. 70% alcohol for 5 min. 2. 2% gluteraldelyde for 20 min. 3. 2% formaldehyde for 10 min. 4. 1% sodium hypochlorite for 15 min. Answer 2. 2% gluteraldelyde for 20 min. Reference Ananthanarayanan 6th Edition page 29 Quality: Spotter Status: Repeat QTDF: Ananthanarayanan Discussion Glutaraldehyde [CHO-(CH2)3-CHO ] has a similar action like Formaldehyde, and is specifically effective against tubercle bacteria, fungi and viruses. It is less toxic and irriant to the eys than formaldehyde. This has no deleterious effects on the cement or lenses fo the instruments such as bronchoscopes and cystoscopes. It is also used for corrugated rubber anaesthetic tubes face masks, plastic endotracheal tubes, metal instruments and polythene tubing Explanation 1. 70% alcohol is used as skin antiseptics 2. 2% gluteraldelyde for 20 min is for bronchoscope. 3.Formaldehyde is for Fumigation. 4. Sodium hypochlorite is used as antiseptic for dressing wounds. Comments Tests used for testing disinfectants are Reidel Walker Test and Chick martin Test Tips As far as soaps are concerned, those prepared from Saturated fatty acids have more action against Gram Negative Bacteria and those prepared from unsaturated fatty acids have more action against Gram positive Bacteria Question. 128. Heat labile instruments for use in surgical procedures can be best sterilized by: 1. Absolute alcohol. 2. Ultra violet rays. 3. Cholorine releasing compounds. 4. Ethylene oxide gas. Answer 4. Ethylene oxide gas. Reference Jawetz Page 20 Ananthanarayanan 6th Edition Page 30 Quality: Spotter Status: Repeat QTDF: Ananthanarayanan Discussion Ethylene oxide is Colourless Liquid with Boiling Point 10.7oC At normal temperature and pressure, it is a Highly penetrating gas with a sweet ethereal smell Highly Inflammable Highly explosive if concentration > 3 % Acts by Alkylating Amino, Carboxyl, Hydroxyl and sulphydryl Reacts with DNA and RNA Metagenic and Carcinogenic Active against all types of microorganisms including viruses and spores Used for Sterilising Heart Lung machines, respirators, sutures, dental equipments, books and clothing Unsuitable for fumigating rooms Explanation 1. Ethyl and Isopropyl alcohol are bactericidal and action against virus is good. They have no specific actions against spores. Recommended for Skin and thermometers. 2. Ultra violet rays ar low energy, non ionizing radiation with poor penetration. Used ofr disinfecting enclosed areas such as entry ways, hospital wards , operation theatres and virus laboratories. 3. Cholorine releasing compounds are used as antiseptic for dressing wounds and also for disinfection of water. 4. Ethylene oxide gas is used as told above. Comments Beta propiolactone (BPL) is a condensation product of ketone and formaldehyde and is more effective for fumigation Tips This chapter Sterilisation and Disinfection has been asked in almost all Entrance Exams in there is seldom a paper without one question being asked from this. This chapter can be best compared to the Chapter dealing with Postmortem changes in FM as far the frequency of MCQs are concerned Question. 129. The earliest immunoglobulin to be synthesized by the fetus is: 1. IgA. 2. IgG. 3. IgE. 4. IgM. Answer 4. IgM. Reference Ananthanarayanan 5th Edition Page 82 Quality: Spotter Status: Repeat QTDF: Ananthanarayanan Discussion IgM is phylogenetically the oldest Immunoglobulin and the earliest Ig to be synthesized by the foetus Explanation 1. IgA is a. found in mucosal surfaces and is b. the only Ig secreted by the seromicous glands and c. the only Ig to fix complemt throughthe alternate pathway. 2. IgG a. can cross placenta and is b. the Ig with maximum serum concentration. 3. IgE is a. reagenic Antibody and is b. the only heat labile Ig and c. the Ig with shortest Half like. 4. IgM is a. the first Antibody to be synthetised by the foetus, b. has the maximum mol wt, and is c. the marker for congenital infection and d. the marker for recent infection. Comments Tabular columns dealing with the different features of the various Immunoglobulins are to be read thoroughly. Not always do we get a simple question like this from this topic. Chaterjee Biochemistry may also be referred Tips : Mnemonic : In an Immunoglobulin the Constant Region is the C Terminal and so obviously the Variable is the N Terminal Question. 130. A 60 years old man is diagnosed to be suffering from Legionnaires disease after he returns home from attending a convention. He could have acquired it: 1. From a person suffering from the infection while traveling in the aeroplane. 2. From a chronic carrier in the convention center. 3. From inhalation of the aerosal in the air conditioned room at convention center. 4. By sharing an infected towel with a fellow delegate at the convention. Answer 3. From inhalation of the aerosal in the air conditioned room at convention center. Reference Ananthanarayanan 6th Edition Pages 377 Harrison 15th Edition Page 945 and 1062 Quality: I Clinical Status: Topic Repeat from AI 2000 QTDF: Ananthanarayanan Discussion Legionellaceae are o aerobic, o nonsporeforming, o unencapsulated o gram-negative bacilli o that stain poorly with Gram stain when performed on smears from clinical specimens. o Microorganisms in tissue can be better visualized with the Gimenez or silver stains (Dieterle or Warthin-Starry). Stained smears of Legionella pneumophila taken from colonial growth resemble Pseudomonas. L. micdadei stains acid-fast. o No Man to Man Transmission o No Animal Reservoir (but found intracellularly) o Human are affected predominantly The organisms are fastidious and o require L-cysteine, ferric ion, and alpha-ketoacids for growth. o Colonies develop within 3-5 days on buffered charcoal yeast extract agar (BCYE), EPIDEMIOLOGY. o Fresh water (lakes, streams, thermally polluted waters, potable water) is the environmental reservoir of Legionella in nature o Invasive pneumonia (Legionnaires disease) is related to exposure to potable water or to aerosols containing the bacteria. The growth of Legionella occurs more readily in hot water, and exposure to warm water sources is an important risk factor for disease. o Legionella are facultative intracellular parasites and grow inside protozoans present in biofilms consisting of organic and inorganic material found in plumbing and water storage tanks and a variety of other bacterial species. o Sporadic cases of community-acquired Legionnaires disease can be attributed to potable water in the local environment of the patient. o Outbreaks of Legionnaires disease have been associated with protozoans in the implicated water source; replication within these eukaryotic cells presumably amplifies and maintains Legionella within the potable water distribution system. Outbreaks of community-acquired pneumonia have been linked to common sources, including evaporative condensors and cooling towers.. CLINICAL MANIFESTATIONS. Legionnaires disease was originally believed to cause a clinical syndrome called o atypical pneumonia and was associated with o extrapulmonary signs and symptoms, including diarrhea, hyponatremia, hypophosphatemia, abnormal liver function tests, confusion, and renal dysfunction. o Although a subset of patients may exhibit classical manifestations, Legionella infection typically causes pneumonia that is indistinguishable from disease produced by other infectious agents. Fever, cough, may be productive of purulent sputum or may be nonproductive and chest pain are common presenting symptoms;. o Classic chest radiographic appearance showed rapidly progressive alveolar filling infiltrates, in usual cases of pneumonia the chest radiographic appearance is widely variable, appearing as tumor-like shadows, evidence of nodular infiltrates, unilateral or bilateral infiltrates, or cavitation, although cavitation is rarely seen in nonimmunocompromised patients. o A few clinical features may help to differentiate Legionella pneumonia from other causes. Legionella pneumonia produces an acute-onset febrile illness, the radiograph shows alveolar filling infiltrates, and there is no clinical response to broad-spectrum beta-lactam (penicillins and cephalosporins) or aminoglycoside antibiotics. o Pontiac fever is a self-limiting illness that develops following aerosol exposure and may represent a toxic or hypersensitivity response to Legionella.Pontiac fever in adults and children is characterized by high fever, myalgia, headache, and extreme debilitation, lasting for a few days. Cough, breathlessness, diarrhea, confusion, and chest pain may occur, but there is no evidence for invasive infection. The disease is self-limited without sequelae. Virtually all exposed individuals seroconvert to Legionella antigens. LABORATORY DIAGNOSIS. o Culture of Legionella from sputum, other respiratory tract specimens, blood, or tissue is the gold standard method against which indirect methods of detection should be compared. o Specimens obtained from the respiratory tract that are contaminated with oral flora must be treated and processed to reduce contaminants and plated onto selective media. o Direct immunofluorescence antibody (DFA) screening, TREATMENT. o Erythromycin, with or without rifampin, has been empirically established as effective therapy. o The newer macrolides, including azithromycin and clarithromycin, and the fluoroquinolone agents (ciprofloxacin) are more active than erythromycin in experimental models of infection. o In serious infections or in high-risk patients, parenteral therapy is recommended initially; a switch to oral therapy can be made when the patient has had a clinical response. o The duration of therapy for Legionnaires disease is 2-3 wk. o Treatment of extrapulmonary infections, including prosthetic valve endocarditis and sternal wound infections, may require prolonged therapy. o Alternative antibiotics include doxycycline and trimethoprim-sulfamethoxazole (TMP-SMZ). Beta-lactams and aminoglycosides, and other antibiotics that do not penetrate mammalian cells, are not clinically effective. Relapse (recrudescence) may occur following cessation of erythromycin therapy. Explanation 1. May be Rubella, Parvo Virus or Mycoplasma be got From a person suffering from the infection while traveling in the aeroplane. ( The coomon diseases are omitted) 2. A chronic carrier in the convention center can transmit Streptococcus, Meningococcus, Diphtheria 3. Inhalation of the aerosal in the air conditioned room at convention center can lead to Legionella 4. Sharing an infected towel with a fellow delegate at the convention can lead to many disorders, but not classical fever after a convention Comments The question is very simple. The source of spread of Legionnnaires is being asked. Well, even if the question paper had the word Convention, serious contenders will immediately go for Air Conditioner. This question would be a tougher one if the clinical features are given and we are asked to find the diagnosis Tips The chapter on Miscellaneous Bacteria has to be mastered, as more questions are being asked nowadays from there Question. 131. The following are true regarding Lymes Disease, except: 1. It is transmitted by ixodes tick. 2. Erythema chronicum migrans may be a clinical feature. 3. Borrelia recurrentis is the aetiological agent. 4. Rodents act as natural hosts. Answer 3. Borrelia recurrentis is the aetiological agent. Reference Ananthanarayanan 6th Edition Pages 356 to 359 Harrison 15th Edition Page 1062 Quality: Reader Status: Repeat QTDF: Ananthanarayanan Discussion Borrelia are large, motile, refractile spirochetes with irregular, wide open coils. Readily stained by pordinary methods 10 to 30 micron long and 0.3 to 0.l7 micron wide Gram negative Commensals on Buccal and Genital Mucosa Two common species are Borrelia recurrentis and Borrelia burggorferi Borrelia recurrentis Epidemic Relapsing Fever o Louse (Pediculus humanus): B. recurrentis Endemic relapsing fever o Tick Ornithodoros: B.duttoni B.hermsii B.parkeri Human contact is often unnoticed, because these ticks are nocturnal feeders, have a painless bite, and detach immediately following a short blood meal. The cyclic nature of relapsing fever is explained by the ability of Borrelia organisms to continually undergo antigenic (phase) variation Louse-borne disease has a o longer incubation period, o longer periods of pyrexia, o fewer relapses, and o longer remission periods than tick-borne disease. Each illness is associated with o sudden onset of high fever, headache, photophobia, nausea, vomiting, myalgia, and arthralgia. o Additional symptoms may appear later and include abdominal pain, a productive cough, and mild respiratory distress. Bleeding manifestations are common and include o epistaxis, hemoptysis, hematuria, and hematemesis. The child may be lethargic and often has a diffuse, erythematous, macular, or petechial rash over the trunk and shoulders. This rash is more common in louse-borne fever (25%), is of 1-2 days duration, and occurs almost exclusively during the end of the primary febrile episode. There may also be lymphadenopathy, pneumonia, and splenomegaly. Hepatic tenderness associated with hepatomegaly is a common sign. Jaundice is not uncommon and may occur in half of affected children. CNS manifestations may be the principal feature of late relapses in tick-borne disease; they include lethargy, stupor, meningismus, convulsions, peripheral neuritis, focal neurologic deficits, and cranial nerve paralysis. Myocarditis and hepatitis are not uncommon and may be responsible for death. The initial symptomatic period characteristically ends with a crisis in 4{endash}10 days, marked by abrupt diaphoresis, hypothermia, hypotension, bradycardia, profound muscle weakness, and prostration. In untreated patients subsequent relapse occurs within 1 wk and is followed by up to five relapses with symptoms during each relapse becoming milder and shorter; the afebrile remission period lengthens. Severe manifestations include myocarditis, hepatic failure, and disseminated intravascular coagulation. Diagnosis depends on demonstration of spirochetes in thin or thick blood smears stained with Giemsa or Wright stain. During afebrile remissions, spirochetes disappear from the blood. TREATMENT AND PROGNOSIS. Oral or parenteral tetracycline is the drug of choice for louse-borne and tick-borne relapsing fever. In children under 12 yr of age erythromycin (50 mg/kg/24 hr) for a total of 10 days is recommended. For older children and young adults, tetracycline (500 mg every 6 hr) for 10 days has been effective. Single-dose treatment with erythromycin or tetracycline (a single 500-mg oral dose) is efficacious in adults, but experience in children is limited. Resolution of each febrile episode either by natural crisis or as a result of antimicrobial treatment is usually accompanied within 2 hr by the Jarisch-Herxheimer reaction, which is associated with clearing of the spirochetemia. Attempts to control this reaction by prior treatment with corticosteroids or antipyretics have met with limited success. With adequate therapy the mortality rate for relapsing fever is below 5%. A majority of patients recover from their illness with or without treatment after the appearance of antiborrelial antibodies, which agglutinate, kill, or opsonize the spirochete. No vaccine is available, and disease control requires avoidance or elimination of the arthropod vectors. In epidemics of louse-borne disease, dissemination can be prevented by good personal hygiene and delousing of persons, dwellings, and clothing with commercially available insecticide Borrelia burggorferi By Tick of the Ixodes species. The skin is the initial target of infection by B. burgdorferi. Inflammation induced by B. burgdorferi leads to the development of the characteristic rash. Early Localized Disease. o The first clinical manifestation of Lyme disease is the typical annular rash, which is called erythema migrans o Without treatment, the rash gradually expands (hence the name migrans) to an average diameter of 15 cm and remains present for at least 1-2 wk and usually longer. Early Disseminated Disease. o Secondary erythema migrans lesions, o a common manifestation of early disseminated Lyme disease o caused by hematogenous spread of the organisms to multiple skin sites. o Aseptic meningitis, with signs of meningeal irritation, such as nuchal rigidity, uveitis, and rarely, o Focal neurologic findings, especially cranioneuropathies, are a manifestation of this stage of the illness. Paralysis of the facial (seventh) nerve is relatively common in children and may be the initial and the only manifestation of Lyme disease. o carditis, with varying degrees of heart block, may occur with early disseminated Lyme disease. o The paralysis usually lasts from 2 to 8 wk and resolves completely in most cases. There is no evidence that the clinical course of the facial palsy is affected by antimicrobial treatment. Late Disease. o Arthritis, beginning months after the initial infection, is the usual manifestation of late Lyme disease. o Arthritis typically involves the large joints, especially the knee, which is affected in more than 90% of the cases, but any joint may be affected. o Although the joint is swollen and tender, patients do not experience the exquisite pain that is typical of bacterial arthritides. Late manifestations of Lyme disease involving the o central nervous system (CNS) o (sometimes termed tertiary neuroborreliosis) are rarely reported in children. o In adults, chronic demyelinating encephalitis, polyneuritis, and impairment of memory have been attributed to Lyme disease Explanation 1. Lymes disease is transmitted by ixodes tick.. It gets this name because it was first observed in Lyme in Connecticut 2. Erythema chronicum migrans may be a clinical feature. 3. Borrelia recurrentis is the aetiological agent of Relapsing fever. 4. Rodents act as natural hosts for Lymes. Comments Genus Species Disease Treponema pallidum Syphilis Endemicum Bejel Middle East Sibbens Scotland Njoera Zimbabwe Dichuchwa Bechuanaland Skerljevo Eastern Europe Siti Gambia Pertune Yaws Caroteum Pinta Borrelia Burgdoferi Lymes recurrentis Relapsing fever vincenti Vincents angina Leptospira Interrogans Icterrohaemorrhagiae Weils Disease Rats Canicola Canicola Fever Dogs Grippotyphus Swamp or Marsh fever Field Mice Pomona Swineherd fever Pig Hebdomadis Seven day fever Field Mice Fortbragg / autumnalis Fort Bragg Fever / Pre tibial Fever, Not known Pyrogens Febriel spirochetes Pig Battaviae Indonesian Weil Disease Rat Hardjo Dairy form fever Cattle Tips Erythema is reddish discolouration of skin it can be generalized erythema or localised erythema. Several diseases and organisms produce reddish discolouration of skin. Based on site of occurrence, causative organisms and morphology of lesion several different types of erythema and described. Erythema marginatum of Rheumatic fever, Erythema infectiosum (fifth disease) caused by parvo Big virus. Erythema Multiforms in Steven Johnson syndrome, Erythema rodosum caused by drugs and certain infection (leprosy). Erythema arthriticum epidemicum Haverhill fever is used to indicate Streptobacillus moniliformis infections not associated with rat bite resulting from contaminated food or water. Erythema ab igne : erythema caloricum : toasted shins :A reticulated, pigmented, macular eruption that occurs, mostly on the shins, of bakers, stokers, and others exposed to radiant heat. Erythema gyrotum upon in internal malignanacy, Erythema Chronicum migrans in Lymes disease. Erythema necrolyticum Migrans is seen in Glucaganoma Question. 132. The following are true for Bordetella perussis except. 1. It is a strict human pathogen. 2. It can be cultured from the patient during catarrhal stage. 3. It leads to invasion of the respiratory mucosa. 4. Infection can be prevented by a acellular vaccine. Answer 4. Infection can be prevented by a acellular vaccine. Reference Ananthanarayanan 6th Edition Ananthanarayanan 5th Edition Page 316 Quality: Thinker Status: New QTDF: Anathanarayanan Discussion About Clinical Features of Pertussis: 1. Catarrhal Stage lasts 7-10 days prodrome of mild upper respiratory tract symptoms: o anorexia and listlessness o cough - hacking and nocturnal o coryza and rhinorrhea o inflammed mucous membranes o insidious and most contagious stage 2. Paroxysmal Stage lasts a mean of 10-14 days but can last up to 6-10 weeks paroxysmal cough o characterized by 5-15 rapid coughs followed by a characteristic inspiratory whoop, a few normal breaths and then more of the same (chronic cough) o paroxysms initially occur at night and then become more frequent during the day (5-50 episodes per day) o the face may become suffused or cyanotic during an episode o paroxysms of coughing often end in vomiting o may be associated with copious amounts of viscid fluid leading to aspiration and vomiting o fever absent or minimal 3. Convalescent Stage 1. lasts 2-4 weeks and sometimes months 2. paroxysmal cough o not as frequent or severe as in the paroxysmal stage o symptoms gradually wane but may last for 6 months o with each URI for up to a year after the acute infection, many children will develop a pertussis-like cough Explanation 1. It is a strict human pathogen. 2. It can be cultured from the patient during catarrhal stage. 3. It leads to invasion of the respiratory mucosa and this leads to the desquamation of the mucosa. (Ananthanarayanan 5th Edition Page 314). Pertussis Bacteria doesnot invade Blood stream, but it does invade respiratory mucosa. (Obviously it cannot be suspended in the Alveolar air and produce this much symptoms) and the infection extends to the lungs to produce bronchopneumonia . According to Harrison Infection with B. pertussis is initiated by attachment of the organism to the ciliated epithelial cells of the nasopharynx. Attachment is mediated by surface adhesins (e.g., pertactin and filamentous hemagglutinin), which bind to the integrin family of cell-surface proteins, probably in conjunction with pertussis toxin. The role of fimbriae in adhesion or maintenance of infection has not been fully delineated. At the site of attachment, the organism multiplies, producing a variety of other toxins that cause local mucosal damage (tracheal cytotoxin, dermatonecrotic toxin). 4. Anathanarayanan 5th Edition Page 316 says, Even fully immunized subjects may develop pertussis but the disease will be very mild in them. That means that INFECTION OCCURS after Administration of Acelullar Vaccine, but full blown disease doesnot occur. Comments Though there are controversies as far as this question is concerned, Points 1, 2 and 3 are 100 % true. Hence we take choice 4 as the answer as we have the word INFECTION Tips Culture of Nasopharyngeal Secretions are used for Diagnosis Question. 133. A labourer involved with repair-work of sewers was admitted with fever, jaundice and renal failure. The most appropriate test to diagnose the infection in this patient is: 1. Weil Felix test. 2. Paul Bunnel test. 3. Microscopic agglutination test. 4. Micro immunofluorescence test. Answer 3. Microscopic agglutination test. Reference Ananthanarayanan 5th Edition Page 359 Quality: Reader Status: Topic Repeat from AI 2002 QTDF: Discussion First we have diagnose the condition and then look out for the appropriate investigation The points given are 1. Sewers 2. Fever 3. Jaundice 4. Renal Failure It does not need an Infectious disease expert to tell that this is a case of Leptospirosis. And we have to find the appropriate investigation for it Diagnosis of Leptospirosis can be by 1. Isolation of the Organism a. From blood or CSF during the first 10 days b. From Urine 2. Serological a. The antigens are prepared from L. biflexa Patoc 1 Strain b. Tests employed include Sensitised Erythrocyte Lysis (SEL) Test, Complement fixation, Indirect Immunoflouresence and Microscopic Agglutination c. In Microscopic Agglutination Test (MAT), an antibody titre of 1 : 100 is neede Explanation 1. Weil Felix test is for Rickettsiae and uses cross-reactive Proteus species antigens. 2. Heterophile antibodies agglutinate cells from species different from those in the source serum. The transient heterophile antibodies seen in infectious mononucleosis, also known as Paul-Bunnell antibodies, are IgM antibodies detected by the Paul-Bunnell{endash}Davidsohn test for sheep red cell agglutination. The heterophile antibodies of infectious mononucleosis agglutinate sheep or, for greater sensitivity, horse red cells but not guinea pig kidney cells. This adsorption property differentiates this response from the heterophile response found in patients with serum sickness, rheumatic diseases, and some normal individuals. Titers greater than 1:28 or 1:40 (depending on the dilution system used) after absorption with guinea pig cells are considered positive 3. Microscopic agglutination test is used for Leptospirosis 4. Micro immunofluorescence test is for Pneumonia, Herpes, Chlamydia , Rickettsiae etc Comments Leptospirosis and Rickettsiae are favourite areas for MCQ setters Tips Questions are often repeated from the chapter on Antigen Antibody reactions Question. 134. All of the following infections are often associated with acute intravascular hemolysis except: 1. Clostridium tetani. 2. Bartonella bacilliformis. 3. Plasmodium falciparum. 4. Babesia microti. Answer 1. Clostridium tetani. Reference Ananthanarayanan 6th Edition Page 238 Harrison 15th Edition Chapters 163, 214 Quality: Thinker Status: New QTDF: Ananthanarayanan Discussion Clostridium tetani produces Tetanolysin and Tetanospasmin Tetanolysisn o Heat Labile o Oxygen labile o Lyses the erythrocytes of rabbit and horse (used in the test by Lowbury and Lilly) Tetanospasmin o Heat Labile o Plasmid Coded o Good Antigen o Responsible for the Clinical features Explanation 1. (As far as we know)Clostridium tetani doesnot cause Acute Intravascualr hemolysis. a. Typically, the patient first notices increased tone in the masseter muscles (trismus, or lockjaw). b. Dysphagia or stiffness or pain in the neck, shoulder, and back muscles appears concurrently or soon thereafter. c. The subsequent involvement of other muscles produces a rigid abdomen and stiff proximal limb muscles; d. the hands and feet are relatively spared. e. Sustained contraction of the facial muscles results in a grimace or sneer (risus sardonicus), and f. contraction of the back muscles produces an arched back (opisthotonos). g. Some patients develop paroxysmal, violent, painful, generalized muscle spasms that may cause cyanosis and threaten ventilation. h. These spasms occur repetitively and may be spontaneous or provoked by even the slightest stimulation. i. A constant threat during generalized spasms is reduced ventilation or apnea or laryngospasm. j. The severity of illness may be mild (muscle rigidity and few or no spasms), moderate (trismus, dysphagia, rigidity, and spasms), or severe (frequent explosive paroxysms). k. The patient may be febrile, although many have no fever; mentation is unimpaired. l. Deep tendon reflexes may be increased. m. Dysphagia or ileus may preclude oral feeding. 2. Bartonella spp., including B. bacilliformis, B. henselae, B. quintana, and B. clarridgeiae, are tiny gram-negative bacilli that can adhere to and invade mammalian cells, including endothelial cells and erythrocytes. a. Previously classified as Rochalimaea spp. within the rickettsia group, Bartonella spp. have now been removed from the order Rickettsiales on the grounds that they are not obligate intracellular parasites. b. These agents cause a wide spectrum of clinical illnesses, including i. trench fever, ii. cat-scratch disease (CSD), iii. bacillary angiomatosis, iv. endocarditis, v. Oroya fever, and vi. verruga peruana. c. The pathologic manifestations of Bartonella disease vary with the immune status of the host d. Sandfly vector Phlebotomus e. During initial infection in the nonimmune host, B. bacilliformis cells adhere to erythrocytes and produce indentations in the cell membrane; the bacteria subsequently enter the erythrocytes and cause persistent deformation of the cytoskeleton. f. The parasitized erythrocytes are ultimately phagocytosed and destroyed. Although the life span of infected erythrocytes is markedly shortened, not all of this change can be attributed to the mechanical fragility induced by the internalization of bacteria. Decreased bone marrow erythropoiesis also contributes to anemia 3. Plasmodium falciparum. a. In P. falciparum infections, membrane protuberances appear on the erythrocytes surface in the second 24 h of the asexual cycle. b. These knobs extrude a high-molecular-weight, antigenically variant, strain-specific, adhesive protein (PfEMP1) that mediates attachment to receptors on venular and capillary endothelium-an event termed cytoadherence. c. Several receptors have been identified, of which i. intercellular adhesion molecule 1 is probably the most important in the brain, ii. chondroitin sulfate B in the placenta, and iii. CD36 in most other organs. d. Thus the infected erythrocytes stick inside the small blood vessels. e. At the same stage, these P. falciparum-infected red cells may also adhere to uninfected red cells to form rosettes. f. The processes of cytoadherence and rosetting are central to the pathogenesis of falciparum malaria. g. They result in the sequestration of red cells containing mature forms of the parasite in vital organs (particularly the brain), where they interfere with microcirculatory flow and metabolism. h. Sequestered parasites continue to develop out of reach of the principal host defense mechanism: splenic processing and filtration. i. As a consequence, only the younger ring forms of the asexual parasites are seen in the peripheral blood in falciparum malaria, and the level of peripheral parasitemia underestimates the true number of parasites within the body. j. Severe malaria is also associated with reduced deformability of the uninfected erythrocytes, which compromises their passage through the partially obstructed capillaries and venules and shortens red cell survival. k. In the other three benign malarias, sequestration does not occur, and all stages of the parasites development are evident on peripheral blood smears. Whereas P. vivax, P. ovale, and P. malariae show a marked predilection for either old red cells or reticulocytes and produce a level of parasitemia seldom exceeding 2%, P. falciparum can invade erythrocytes of all ages and may be associated with very high levels of parasitemia l. Anemia results from accelerated red cell destruction and removal by the spleen in conjunction with ineffective erythropoiesis. In severe malaria, both infected and uninfected red cells show reduced deformability, which correlates with prognosis and development of anemia. Splenic clearance of cells is also increased. In nonimmune individuals and in areas with unstable transmission, anemia can develop rapidly and transfusion is often required. In many areas of Africa, children may develop severe anemia as a result of repeated malarial infections. Anemia is a common consequence of antimalarial drug resistance, which results in repeated or continued infection. 4. Babesia microti. a. The incubation period for B. microti infection is about 1 to 4 weeks. b. Immunosuppressed patients, splenectomized individuals, and the elderly have the most severe illness. c. The clinical presentation varies widely; symptoms and signs include a i. gradual onset of irregular fever, ii. chills, iii. sweating, iv. muscle pain, and v. fatigue. vi. Mild hepatosplenomegaly and vii. mild hemolytic anemia may develop. d. The level of parasitemia may exceed 10%. e. The illness may continue for weeks or months Comments Since it is given in all books that hemolysis is produced by 2,3 and 4 and since Ananthanarayanan specifically mentions that the Tetanolysis causes hemolysis in Rabbits and Horse and in humans its pathogenic role is unknown, we go for the answer 1 But remember that Clostridium welchii produces a phospholipase that can release the phosphoryl bond of Lecithin thereby lysing Human RBCs Tips Tetanus Acts in the Presynpse and Strychine at the Postsynaptic level. Use this Mnemonic poSTrychnine, if you have difficulty in remembering this !!! Question 135. Which of the following statements is true about endemic typhus. 1. Is caused by R. rickettsii. 2. Is transmitted by the bite of fleas. 3. Has no mammalian reservoir. 4. Can be cultured in chemical defined culture medium. Answer 2. Is transmitted by the bite of fleas. Reference Ananthanarayanan Chapter on Rickettsia Quality: Spotter Status: Repeat QTDF: All books give this Discussion The following table gives you an overview Group Species Disease Vector Called as Vector Reservoir Geographical Incbtion Period in days Duration in days Typhus R.prowazekki Epidemic Typhus Classical Typhus Goal Fever Louse Pedicilus humanis corporis Dies Human Worldwide 7-14 10-18 R.prowazekki Recrudescent Typhus Brill Zinser Disease - - - Human America, Europe, Australia Years 7-11 R.typhi Endemic Typhus Rat Flea Xenopsylla cheopis Unaffected Rat Worldwide 8-16 8-16 Cat Flea Ctenocephalides felis 8-16 8-16 Spotted Fever Group R.rickettsiae Rocky Mountain Spotted Fever Wood Tick Dermacenter andersoni Transovarian 2-14 10-20 Dog Tick Dermacenter Variabilis R.siberica Siberian Tick Typhus Ixodid Tick Transovarian R.conori Fever Boutonneuse Tick Rhipicephalis sanguines Transovarian Mediterranean 5-7 7-14 R.conori South African Tick Typhus Haemophysalis leachi Transovarian R.conori Kenyan Tick Typhus Amblyomma cajennense Transovarian Central America South America R.conori Indian Tick Typhus Hyalomma Transovarian R.australis Queensland Tick Typhus Ixodid Tick Transovarian R.akari Rickettsial Pox Gamasid Mite Allodermanyssus sanguines Transovarian Mus musculus Liponyssoides sanguineus 10-17 3-11 Scrub T R.tsutsugamushi Scrub Typhus Trombiculid Mite Trombicula akanushi Transovarian Japan Trombicula deliensis India Leptotrombidium deliense Asia, Australia, New Guinea, Pacific Islands 9-18 6-21 Rochalimaea R.quintana Trench Fever Louse No Vertical Unharmed Human Europe, North Africa, Mexico Coxiella C.burnetti Q Fever Extrahuman Tick Ixodid ? Rodents Worldwide Human Nil Cattle,Sheep Poultry Ehrlichia Her.sennetsu Infectious Mononucleosis Syndrome - - - - Japan Explanation 1. Endemic Typhus is caused by R.prowazekki 2. Endemic Typhus Is transmitted by the bite of fleas. a. Rat Flea Xenopsylla cheopis b. Cat Flea Ctenocephalides felis 3. The agent causing Endemic Typhus Has a mammalian reservoir, Rat. 4. The agent causing Endemic Typhus Cannot be cultured in chemical defined culture medium. In fact none of the Rickettsia can be cultured in a cell free medium Comments Rickettsiae is an important topic. The old table is given as this is still not obsolete. However read this topic from the New Harrison 15th Edition (especially the new classification) Tips Read Table 177-2 From Harrison 15th Edition for Diagnosis and treatment of Rickettsial Diseases Question. 136. Commonest cause of sporadic encephalitis is: 1. Japanese B Virus 2. Herpes Simplex Virus. 3. Human Immunadeficiency Virus. 4. Rubeola Virus. Answer 2. Herpes Simplex Virus. Reference Harrison 15th Edition Chapter 182, 372 and Page 2475 Also Given in SARP Quality: Spotter Status: Repeat QTDF: Harrison Discussion The number of viruses reported to cause encephalitis is legion. The most important viruses causing sporadic cases of encephalitis in immunocompetent adults are HSV-1, VZV, and, less commonly, enteroviruses. Epidemics of encephalitis are caused by arboviruses, which belong to several different viral taxonomic groups including Alphavirus of the family Togaviridae (e.g. Eastern equine encephalitis virus, Western equine encephalitis virus), Flavivirus of the family Flaviviridae (e.g., St. Louis encephalitis virus, Powassan virus), and Bunyavirus of the family Bunyaviridae (e.g., California encephalitis virus serogroup, LaCrosse virus). In most years, the largest number of cases of arbovirus encephalitis are generally due to St. Louis encephalitis virus and the California encephalitis virus serogroup. Central and Peripheral Nervous System Infections HSV accounts for 10 to 20% of all cases of sporadic viral encephalitis. Subtype 1 virus causes ?95% of cases of HSV encephalitis West Nile virus falls into the same phylogenetic group of flaviviruses as St. Louis and Japanese encephalitis viruses, as do Murray Valley and Rocio viruses. The latter two viruses are both maintained in mosquitoes and birds and produce a clinical picture resembling that of Japanese encephalitis. Murray Valley virus has caused occasional epidemics and sporadic cases in Australia. Rocio virus caused recurrent epidemics in a focal area of Brazil in 1975 to 1977 and then virtually disappeared Explanation 1. Japanese B Virus causes encephalitis, no doubt, but is not the most common cause of sporadic encephalitis 2. Herpes Simplex Virus is the most common cause of sporadic encephalitis. 3. Human Immunadeficiency Virus is not the most common cause of sporadic encephalitis. 4. Rubeola Virus is not the most common cause of sporadic encephalitis. Comments A repeated Question and all those who have read the small books like SARP would have got this Tips You will find Herpes Virus and Arbo Virus, in one form or another in all question papers Question. 137. Which of the following statements is true about rabies virun: 1. It is a double stranded RNA virus. 2. Contains a DNA dependant RNA polymerase. 3. RNA has a negative polarity. 4. Affects motor neurons Answer 3. RNA has a negative polarity. Reference Ananthanarayanan 5th Edition Page Paniker,5th,Pg-406 Quality: Thinker Status: New QTDF: Ananthanarayanan Discussion Single stranded RNA Viruses are classified into 1. Positive polarity: o In which the virus strand itself acts as mRNA o The viral RNA is infectious. o Also called as Plus Strand Positive Sense o Example Picorna and Yogaviruses. 2. Negative polarity: o They have there own RNA polymerases o i.e.RNA dependent RNA polymerases & o Extracted nucleic acids are not infectious.. o Also called as Minus Strand Negative Sense o Example Rhabdo, orthomyxoviruses, paramyxoviruses Explanation 1. Rabies virus is a single stranded RNA Virus and double stranded RNA virus is Reo Virus. (An example of Single stranded DNA Virus is Parvo Virus) 2. Rabies virus does not Contains a DNA dependant RNA polymerase. It contains a RNA dependant RNA polymerase. 3. The RNA has a negative polarity. 4. Affects autonomic neurons Comments There are a lot of classification on the chapter on Virus 1. Enveloped ot not 2. Shape etc Prepare them. Tips Question. 138. An anxius mother brought her 4 year old daughter to the pediatrician. The girl was passing loose bulky stools for the past 20 days. This was often associated with pain in abdomen. The pediatrician ordered the stool examination which showed the following organisms. Identify the organism: [* | In-line.WMF 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1. Entamoeba histolytica 2. Giardia lamblia 3. Cryptosporidium 4. E. Coli Answer 2. Giardia lamblia Reference Textbook of Medical parasitology by C.K.Jayaram Paniker 4th Edition Page 35 Parasitology by K.D.Chaterjee Twelfth Edition Page 37 Quality: Spotter A Real Spotter You see and diagnose !!! Status: New Question and New Format QTDF: Chatterjee Discussion The majority of individuals infected with Giardia are probably asymptomatic. Symptoms develop 1-3 wk after exposure to the parasite. o Giardiasis is more frequently symptomatic in children than in adults. o Symptoms occur in 40-80% of infected children after an average incubation period of 8 days. The most common presentation is o diarrhea, o weight loss, o crampy abdominal pain, and o failure to thrive or o a spruelike illness. The onset of symptoms may be o abrupt or o gradual; the disease may be o self-limited or o produce severe protracted diarrhea and malabsorption. Alterations in the digestive function of the brush border are common in those with protracted symptoms. Malabsorption of o sugars (such as xylose and disaccharides), o fats, and o fat-soluble vitamins occurs in more than half of patients who have nonspecific morphologic abnormalities of the small intestinal mucosa, which are similar to those seen in other malabsorptive disorders. Lactose intolerance is common after infection with Giardia and may mimic relapse or reinfection. The impact of chronic infection with Giardia on children in the developing world is controversial, but some investigators believe Giardia infection may affect growth and development in this setting. Trophozoites rarely invade the lamina propria of the intestinal mucosa, and Giardia is only rarely reported as a cause of inflammatory diarrhea or fever. Enterotoxin production by Giardia has not been demonstrated. Giardia is not an invasive parasite and thus does not elicit eosinophilia Explanation 1. Entamoeba histolytica 2. Giardia lamblia 3. Cryptosporidium 4. E. Coli Comments Organism Antimicrobial Agent Giardia lamblia Quinacrine HCl or metronidazole or furazolidone Entamoeba histolytica Metronidazole followed by iodoquinol Cryptosporidium None available Cyclospora spp. Trimethoprim/sulfamathoxazole (TMP/SMX) Isospora belli TMP/SMX Enterocytozoon bieneusi None available Strongyloides Thiabendazole Tips Next Time it will be not Giardia, you can be given a Gram Stain or You may be asked to identify the species of Entamoeba or Plasmodium or Even Microfilaria. Who knows!!! You can even get a HPE section J Go patiently through all the pictures in Parasitology and Micorbiology OBSTETRIC AND GYNAECOLOGY 19 Questions The questions were distributed as follows Gynaecology : 12 o Development 1 o Physiology 1 o Contraception 3 o Tumours 6 o Surgeries 1 Normal Pregnancy 1 Pregancy Complication 6 Note that 1/3rd of the questions are from Tumours and are often repeats and could be easily answered by studying Classification, Staging and treatment. And Contraception will give another few questions and a knowledge of Contraception + Tumours will make one get 50 % of OG Questions and this is the trend in every exam (including state exams). All the topics listed above are important. In addition a few more important topics are 1. Clinical Histories a. A multi gravida with painless bleeding PV. b. A primigravida with High BP .. c. A 35 year old women with irregular bleeding .. 2. Fetal Diameters and Pelvic Measurements and Positions 3. Changes in Pregnancy (Normal and the common Abnormal conditions) 4. Vesicular Mole and Ectopic Pregnancy Question. 139. Pure gonadal dysgenesis will be diagnosed in the presence of:: 1. Bilateral streak gonads. 2. Bilateral dysgenetic gonads. 3. One side streak and other dygenetic gonads. 4. One side streak and other normal looking gonad. Answer 1. Bilateral streak gonads. Reference Harrison 15th Edition Page 2176 Quality: Spotter Status: Repeat QTDF: Harrison Discussion Few conditions that are favourite for examiners: Turners Syndrome o Gonadal dysgenesis is characterized by primary amenorrhea, sexual infantilism, short stature, multiple congenital anomalies, and bilateral streak gonads in phenotypic women with any of several defects of the X chromosome. Mixed gonadal dysgenesis o in which a unilateral testis and a contralateral streak gonad may be present; Pure gonadal dysgenesis o in which bilateral streak gonads are associated with a normal 46,XX or 46,XY karyotype, normal stature, and primary amenorrhea; and Noonan syndrome, o an autosomal dominant disorder in both sexes characterized by webbed neck, short stature, congenital heart disease, cubitus valgus, and other congenital defects despite normal karyotypes and normal gonads Explanation Self Explanatory Comments In Pure Gonadal Dysgenesis, the gonads are not developed and the Female Phenotype is due to the failure of Gonadal development Tips Chromosomal Aberrations and Variations in Sexual Development are hot topics Question. 140. A 20 year old woman gives a history of sharp pain in the lower abdomen for 2-3 days every month approximately 2 weeks before the menses. The most probable etiology for her pain is: 1. Endometriosis. 2. Dysmenorrhea. 3. Pelvic tuberculosis. 4. Mittelschmerz. Answer 4. Mittelschmerz. Reference Shaw 12th Edition Page 229 Quality: Spotter Status: Repeat QTDF: Shaw Discussion Mittleschmerz is Painful Ovulation Pain associated with rupture of Ovarian Follicle at the Time of Ovulation Pain occurs at regular time in succeeding or intermittent cycles Usually at the time of cvulation Short Duration < 12 hours Slight Vaginal Bleeding may be present Treated with Analgesics and Assurance Explanation 1. In Endometriosis pain is at the time of Menstraution. 2. In Dysmenorrhea. pain is at the time of Menstraution 3. In Pelvic tuberculosis pain is not cyclical. 4. Mittelschmerz classically presents as described above. Comments The only factor that created concern in this question is that OUR PATIENT experiences pain for 2 to 3 days, where as Shaw says that Mittelschmerz is usually of shorter duration Tips Question. 141. All of the follwing are mechanisms of action of emergency contraception except: 1. Delaying ovulation. 2. Inhibiting fertilization. 3. Preventing implantation of the fertilized egg. 4. Interrupting an early pregnancy. Answer 2. Inhibiting fertilization. Reference Shaw Chapter Birth Control Topic Post coital contraception Test book of Obstetrics 4th Edition D.C.Dutta 588 Quality: Reader Status: Repeat QTDF: Shaw Discussion Emergency Contraception or Post Coital Contraception is indicated in 1. Unprotected Intercourse 2. Condom Rupture 3. Missed Pill 4. Sexual Assault 5. Rape 6. First time intercourse [(according to Dutta) is known to be ALWAYS Unplanned!! J] Methods Used are 1. Morning after Pill a. Endometrium Unfavourable b. Interferes with the function of Corpus Luteum and Luteolysis c. Increased Tubal Peristalsis d. Delay of Ovulation 2. Yuzpe Method 3. IUCD a. Prevents Implantation 4. Anti Progesterone(Mifepristone), on the 27th day of the cycle, irrespective of the day of intercourse a. It does not prevent Fertilisation, but acts by blocking the action of Progesterone on Endometrium 5. Danazol 6. Interception a. Zygote is Formed, but prevented from Implantation or Organogenesis Explanation 1. Delaying ovulation is the mechanism of Pills. 2. No method acts by Inhibiting fertilization. 3. Preventing implantation of the fertilized egg is by IUCD. 4. Interrupting an early pregnancy is by RU 486. Comments The answer is very clear. For those who may think that the answer is 4, please note that 3 and 4 are essentially the same process and RU 486 as well as IUCDS do both Tips Take a note of Another drug Epostane that prevents Progesterone Synthesis Question. 142. Most common cause of first trimester abortion is: 1. Chromosomal abnormalities. 2. Syphilis. 3. Rhesus isoimmunisation. 4. Cervical incompetence. Answer 1. Chromosomal abnormalities. Reference Test book of Obstetrics 4th Edition D.C.Dutta Page 172 Quality: Spotter Status: Repeat QTDF: All books give this Discussion Causes of First Trimester Abortion 1. Defective Germ Plasm a. Chromosomal Abnormalities i. Most common among this is Autosomal Trisomy b. Congenital Malforamtion c. Blighted Ovum 2. Chromosomal Abonormalities 3. Hormonal deficiency 4. Trauma 5. Acute Infection Causes of Mid Trimester Abortion 1. Cervical Incompetence 2. Uterine Malformation - bicornuate or Septate uterus 3. Uterine Fibroid 4. Low implantation of Placenta 5. Twins 6. Hydramnios Explanation 1. Chromosomal abnormalities are the Most common cause of First Trimester Abortion. 2. In Syphilis the outcome improves with successive pregnancies.. 3. In Rhesus isoimmunisation, the out come becomes grave with successive pregnancies. 4. Cervical incompetence. Is the Most common cause of Mid Trimester Abortion Comments In earlier weeks, the foetus dies and is then expelled In the later period the foetus is expelled out and then dies as it is too small to survive Tips Cervical Abortion is a condition in which the external os fails to dilate and so the Ovum, with the decidual coverings is accommodated in the dilated cervical canal Question. 143. In prenatal diagnostic technique Act 1994 which one of the following is not a ground for carrying out prenatal test? 1. Pregnant women above 35 years of age 2. History of two or more spontaneous abortion of fetal loss. 3. When fetal heart rate is 160 per min at fifth and 120 per min at ninth month. 4. History of exposure to potentially teratogenic drugs. Answer 3. When fetal heart rate is 160 per min at fifth and 120 per min at ninth month. Reference Prenatal Diagnosis - Regulation and Prevention of Misuse Act 1994 Also can be seen in the web sites of Ministry of Health Quality: Thinker Status: New QTDF: Act !!! Discussion The sections of the act relevant to our question state 2) No prenatal diagnostic techniques shall be conducted except for the purposes of detection of any of the following abnormalities, namely:- 1. chromosomal abnormalities; 2. genetic metabolic diseases; 3. haemoglobinopathies; 4. sex-linked genetic diseases; 5. Congenital Abnormalities 6. Any other abnormalities or diseases as may be specified by the Central Supervisory Board; (3) No prenatal diagnostic techniques shall be used or conducted unless the person qualified to do so is satisfied that any of the following conditions are fulfilled, namely: 1. age of the pregnant woman is above thirty-five years; 2. the pregnant woman has undergone of two or more spontaneous abortions or fatal loss; 3. the pregnant woman had been exposed to potentially Teratogenic agents such as drugs, radiation, infections or chemicals; 4. the pregnant woman has a family history of mental retardation or physical deformities such as spastically or any other genetic disease; 5. any other condition as may be specified by the Central Supervisory Board; Explanation Self Explanatory Comments Even without knowing the details of the act, one can answer the question if he/she knows that the normal heart rate of the foetus Tips Questions can come in FM, SPM and OG from MTP Act of 1971 and Prenatal Diagnosis Act of 1994. The entire acts can be seen at www.rxpgonline.com and www.rxpg.com and www.targetpg.com Question. 144. All of the following are known risk factors for development of endometrial carcinoma except: 1. Obesity. 2. Family History. 3. Use of Hormone Replacement Therapy 4. Early Menopause. Answer 4. Early Menopause. Reference Test book of Gynaecology 2nd Edition D.C.Dutta Page 324 Shaw 12th Edition Page 302 Quality: Spotter Status: Repeat QTDF: Shaw Discussion Endometrial Carcinoma is associated with all conditions that produce High Estrogen Level. The risk factors are 1. Nulliparity 2. Late Menopause 3. Estrogen Therapy for a. Osteoporosis 4. Obesity, Hypertension, Diabetes Corpus Cancer Syndrome 5. Conditions with High Estrogen Levels a. Fibroids b. PCOD 6. DUB 7. Diet Rich in fat 8. Endometrial hyperplasia 9. Familial Explanation 1. Obesity is a risk factor. 2. Family History is a risk factor. 3. Use of Hormone Replacement Therapy is a risk factor. But adding Progesterone nullifies this risk 4. Early Menopause is not a risk factor and late menopause is a risk factor. Comments Straight from Shaw / Dutta Tips Tumours are important in Gynaecology Question. 145. A 55 year old lady presenting to out patent department (OPD) with postmenopausal bleding for 3 months has a 1x1 cm nodule on the anterior lip of cervix. The most appropriate investigation to be done subsequently is: 1. Pap smear. 2. Punch biopsy. 3. Endocervical curettage. 4. Colposcopy. Answer 2. Punch biopsy. Reference Test book of Gynaecology 2nd Edition D.C.Dutta 316 , 519 Shaw Quality: Spotter Status: Repeat QTDF: Shaw Discussion Cytological Examination is now obligatory for establishing a diagnosis Explanation 1. Pap smear can be used, and will be an answer if Punch biopsy is not given. 2. Punch biopsy is the most appropriate answer in this setting. 3. Endocervical curettage can be done after Punch Biopsy. 4. Coloposcopy is inferior to Punch biopsy. Comments An often and most repeated Question Tips Question. 146. A 45 year old female is having bilateral ovarian mass, ascites and omental caking on CT scan, There is high possibility that patient is having . 1. Benign ovarian tumor. 2. Malignant epithelial ovarian tumor. 3. Dysgerminoma of ovary. 4. Lymphoma of ovary. Answer 2. Malignant epithelial ovarian tumor. Reference Reference Test book of Gynaecology 2nd Edition D.C.Dutta Shaw 12th Edition Page 311, 316 Test book of Obstetrics 4th Edition D.C.Dutta Mudaliar Ninth Edition Page Quality: Thinker Status: Repeat QTDF: Shaw Discussion Let us see the main points in the Question 45 years bilateral ovarian mass, favours Malignancy ascites and omental caking CONFIRMS Malignancy Explanation 1. Benign ovarian tumor are usually unilateral. 2. Malignant epithelial ovarian tumor is the correct answer. 3. Dysgerminoma of ovary are seen in children and younger women and correspond to the Seminoma in Males. Usually seen around 20 years 4. Lymphoma of ovary is very rare. Comments Ovarian Cancer has 2 questions - another theme couple Tips You can see for yourself that only one of the choices points towards a malignant tumour Question. 147. Laporatomy performed in a case of ovarian tumor revealed unilateral ovarian tumor with ascities positive for malignatn cells and positive pelvic lymph nodes. All other structures were free of disease. what is stage of the disease: 1. Stage IIc. 2. Stage IIIa. 3. Stage IIIb. 4. Stage IIIc. Answer 1. Stage IIc. 4. Stage IIIc. Reference Test book of Gynaecology 2nd Edition D.C.Dutta page 340 Shaw FIGO Staging Quality: 2 Spotters !! Status: Repeat QTDF: FIGO Staging is Given in all books Discussion Points given are 1. Ovarian Tumour 2. Unilateral 3. Ascites - Malignant Cells 4. Pelvic Nodes Please refer to the FIGO Staging. It is Identical in Shaw and Durtta. The problem is with the interpretation. The constraints of space prevents me from putting this lengthly table here again. In short Stage II is : Tumour involving one or both ovaries with pelvic extension Stage III is : Tumour involving one or both ovaries with peritoneal implants outside the pelvis and/or positive retroperitoneal or inguinal nodes. Supf Liver Metastasis is State III The classical description of Ascites containing Malignant cells fit in with the staging IIc. But There is no mention of any lymph node in Stage IIc When Retroperitoneal nodes are involved, it is Stage IIIc The question says Pelvic node Now if we consider Pelvic node as a Pelvic Tissue, the answer will be IIc Pelvic node as a Retroperitoneal Node, the answer will be IIIc Explanation 1. The Tumour is Stage IIc if we consider Pelvic node as a Pelvic Tissue. 2. The Tumour cannot be Stage IIIa as in Stage IIIa Nodes are negative. 3. The Tumour cannot be Stage IIIb as in Stage IIIb Nodes are negative 4. The Tumour is Stage IIIc if we consider Pelvic node as a Retroperitoneal Node Comments You decide!!! Tips Most Question paper will have Questions from Staging and they will be 99 % Straightforward. This is a rare occasion where there is a controversy Question. 148. Pyometra is a complication associated with all of the following conditions except: 1. Carcinoma of the vulva. 2. Carcinoma of the cervix. 3. Carcinoma of endometrium. 4. Pelvic radiotherapy. Answer 1. Carcinoma of the vulva. Reference Test book of Gynaecology 2nd Edition D.C.Dutta Page 155 Shaw 15th Edition Page 250 Quality: Reader Status: Repeat QTDF: All books give this Discussion Pyometra Defn : Collection of Pus in uterine cavity Prerequisites o Occlusion of Cervical Canal o Enough Source of Pus foirmation o Presence of low grade infection Causes o Obstetrical Infection of Lochiometra o Gynaecological Carcinoma Loweer part of Uterus Endocervical Carcinoma Infected hematometra following Amputation, Conisation or Deep Cauterisation of Cervix Tubercular Endometritis o Pelvic Radiotherapy Explanation 1. Carcinoma of the vulva does not cause Pyometra. 2. Carcinoma of the cervix is the chief cause of Pyometra. 3. Carcinoma of endometrium causes Pyometra. 4. Pelvic radiotherapy causes Pyometra. Comments Simple Question Tips Question. 149. A 55- year -old woman has recurrent urinary retention after a hysterectomy done for huge fibroid. The most likely cause is: 1. Atrophic and stenotic urethra. 2. Lumbar disc prolapse. 3. Injury to the bladder neck. 4. Injury to the hypogastric plexi. Answer 4. Injury to the hypogastric plexi. Reference Shaw 12th Edition Diseases of Urinary System Pg-132 Quality: Spotter Status: Repeat QTDF: Shaw Discussion Radical Operations like Wertheims Hysterectomy involve extensive dissection causing denervation of the bladder, leaving the patient with an insensitive bladder comparable to neurological bladder Explanation 1. Atrophic and stenotic urethra follows surgeries on the bladder neck for a fistula. 2. Lumbar disc prolapse is not related to this question. 3. Injury to the bladder neck is not common in Hysterectomy. 4. Injury to the hypogastric plexi. Comments Tips Question. 150. A case of Gestational Trophoblastic Neoplasia belongs to high risk group if disease develop after: 1. Hydatidiform mole. 2.Full term pregancy. 3. Spontaneous abortion. 4. Ectopic Pregancy. Answer 2.Full term pregancy. Reference Williams Page 836 Test book of Gynaecology 2nd Edition D.C.Dutta Page 332 Quality: Reader Status: Repeat QTDF: Dutta Discussion Gestational Trophoblastic Neoplasia is graded in to low risk and high risk as follows Low Risk High Risk Duration of Symptoms < 4 months Duration of Symptoms > 4 months Initial hCG titres < 100,000 IU / 24 hours urine Initial hCG titres > 100,000 IU / 24 hours urine Metastasis other than liver and brain Metastasis in liver and brain No previous chemotherapy Previous chemotherapy Following Term Pregnancy Explanation Self Explanatory Comments Straight from Dutta Tips Another Question from Malignancy Question. 151. All of the following may be observed in a normal pregnancy except: 1. Fall in serum iron concentration falls. 2. Increase in serum iron building capacity. 3. Increase in blood viscosity increases. 4. Increase in blood oxygen carrying capacity. Answer 3. Increase in blood viscosity increases. Reference Test book of Obstetrics 4th Edition D.C.Dutta Page 52 Mudaliar Ninth Edition Page 39 Quality: Reader with a mistake Status: Repeat QTDF: All books Discussion Obviously there is a mistake in the choice. At first look it may look that the answers are 3 and 4 as there is a fall in the viscosity and there is aneamia pregnancy. Explanation 1. Serum iron concentration falls in Pregnancy. 2. There is an Increase in serum iron building capacity. 3. There is an decrease in blood viscosity increases. 4. There is Increase in blood oxygen carrying yet there is anaemia because of the disproportionate increase in Plasma Volume. Comments A Question with Printing mistake(s) which is very rare in AIIMS / AIPG and very common in . (well you yourself know. Why should I tell J) Tips Question. 152. A hemodynamically stable nulliparous patient with ectopic preganancy has adnexal mass of 2.5 x 3 cms and Beta hCG titre of 1500 miu/ml. What modality of treatment is suitable for her: 1. Conservative management. 2. Medical Management. 3. Laparoscopic Surgery. 4. Laparotomy. Answer 2. Medical Management. Reference Test book of Obstetrics 4th Edition D.C.Dutta Page 202 Mudaliar Ninth Edition Page 233 Quality: Reader Status: Repeat QTDF: Dutta Discussion The indications of Medical Management are 1. Hemodynam,ically Stable Patient 2. Size of Ectopic < 4 cm 3. Gestation < 6 weeks 4. FH Absent 5. Serum beta HCG less than 1500 mIU/ml Methotrexate is used in Medical Management Dose 50 mg /M2 Explanation 1. Conservative management is not a definite management in this case. 2. Medical Management is the most approprite. 3. Laparoscopic Surgery is not needed as size less than 4 cm. 4. Laparotomy is not needed. Comments Straght from Dutta Tips Question. 153 Cut-off value of cervical length at 24 weeks of gestation for prediction of preterm delivery is: 1. 0.5cm. 2. 1.5cm 3. 2.5cm 4. 3.5cm Answer 3. 2.5cm Reference Williams Page 701 CMDT 2003 Quality: MD OG Status: New QTDF: Williams ? CMDT Discussion Increased Risk of Pre term 1. Positive Mid Trimester Vaginal Fetal Fibronectin Test more than or equal to 50 microgram/dl 2. Cervical Shortening (by UCG, at 24 weeks) less than 25 mm Explanation Self Explanatory Comments A fit Question for MCQ in MD OG Final Year Theory paper!!! Tips Dont get tensed if you dont know these questions. Only Obstetricians and (probably Sonologists) may know the answer and both of these category people are not competing with you for the rank !!! Question. 154. A primigravida at 37 week of gestation reported to labour room with central placenta praevia with heavy bleeding per vaginum. The fetal heart rate was normal at the time of examination. The best management option for her is: 1. Expectant management. 2. Caesarean section. 3. Induction and vaginal delivery. 4. Induction and forceps delivery. Answer 2. Caesarean section. Reference Test book of Obstetrics 4th Edition D.C.Dutta 265 to 267 Mudaliar Ninth Edition Page 247 Quality: Reader Status: Repeat QTDF: All books Discussion Central Placenta Praevia You have to do LSCS sooner or later The patient is bleeding PV Gestation is 37 weeks FH Normal - The child is alive You have to save the child Explanation 1. Expectant management can be considered if the baby is not matured ie Duration of Pregnancy LESS THAN 37 weeks. 2. Caesarean section is the ideal option. 3. Induction and vaginal delivery is not possible in Central Placenta Praevia. 4. Induction and forceps delivery is not possible in Central Placenta Praevia. Comments This question is asked in almost all UPSC Exams !! Tips Placenta Praevia and Accidental haemorrhages are being asked in MCQ exams for years !!! and will be asked in future also. Refer to the Criteria for expectant management in Dutta Question. 155. A hypertensive pregnant woman at 34 weeks comes with history of pain in abdomen, bleeding per vaginum and loss of fetal movements. On examination the uterus is contracted with increased uterine tone. Fetal heart sounds are absent. The most likely diagosis is: 1. Placenta praevia. 2. Hydramnios. 3. Premature labour. 4. Abruptio placenta. Answer 4. Abruptio placenta. Reference placenta Test book of Obstetrics 4th Edition D.C.Dutta Page 268 Mudaliar Ninth Edition Page 237 Quality: Reader Status: Repeat QTDF: All books Discussion Abruptio Placenta is also called as Accidental haemorrhage Ablatio Palcenta Premature Seperation of Placenta Look at the features Pain Abdomen Bleeding per vaginum Loss of fetal movements. Uterus is contracted with Increased uterine tone. Fetal heart sounds are absent. Explanation 1. Placenta praevia is painless bleeding PV. 2. Hydramnios is not associated with Bleeding PV. 3. Premature labour may not have absent FH . 4. Abruptio placenta is the ideal choice. Comments The differences between Placenta Praevia and Accidental Haemorrhage are given in all books and to repeat it once again in this small book is going to serve no further purpose Tips Note that presence of Couvelaire Uterus per se in Not an indication for Hysterectomy Question. 156. All of the following drugs are used for management of post partum haemorrhage except: 1. Misoprostol. 2. Oxytocin. 3. Prostaglandin. 4. Mifepristone (RU-486) Answer 4. Mifepristone (RU-486) Reference KDT Page 330 Test book of Obstetrics 4th Edition D.C.Dutta 448 Mudaliar Ninth Edition Page 355 Quality: Reader Status: Repeat QTDF: Dutta Discussion Please refer to the books quoted above. Management of PPH is an important topic and the basic points are best read from Standard Texts. Traumatic PPH can be managed by Hemostatic Sutures Explanation 1. Misoprostol is used. 2. Oxytocin is used. 3. Prostaglandin is used. 4. Mifepristone (RU-486) is a progesterone antagonist Comments Of late there are Clinical Trials where they are evaluating the use of Mifepristone in PPH. So, be on guard next time when you see this choice and analyse all other choices before coming to a conclusion. But in this question, RU-486 is the obvious answer Tips Bilateral Internal Iliac Ligation is another procedure done for PPH Question. 157. B Lynch suture is applied on: 1. Cervix. 2. Uterus. 3. Fallopian tubes. 4. Ovaries. Answer 2. Uterus. Reference Internet Quality: Referer !! Status: New QTDF: Who knows ?? Discussion [* | In-line.WMF 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The B-Lynch suture, also known as the brace suture, was described by Christopher B Lynch and co-workers in 1997 as an alternative surgical method of controlling postpartum haemorrhage due to uterine atony. The method is simple and seems to be effective, although only case reports are available to evaluate the efficacy of the procedure thus far. The technique can be summarised as follows: (see figure 1) 1. General anaesthesia, urinary catheter in place and the patient in the Lloyd Davies position. 2. Pfannenstiel incision usually adequate. 3. Lower segment uterine incision (as for Caesarean Section) made after dissecting off the bladder. 4. Bimanual compression of the uterus to assess the potential chance of success of the B-Lynch suturing technique. If bimanual compression controls the bleeding as observed vaginally, the suture is placed. 5. A no.2 chromic suture on a round bodied needle is used to puncture the uterus about 3 cm below the right hand corner of the lower segment incision and brought out about 3 cm above the same corner (as one would place the first suture when closing this corner of the incision). 6. From this point the suture is passed over the right hand cornu of the uterus, approximately 3-4cm from the right corneal border, where it may be fixed to prevent it from slipping off the fundus, and then fed posteriorly and vertically down to the same level where the suture has previously left the uterine cavity from anterior. 7. The suture is then placed through the posterior uterine wall into the cavity under direct vision of the surgeon and back through the posterior wall about 4-5cm left of the previous entry site. 8. With the suture outside and posterior of the uterine cavity at this stage, it is now passed over the left hand cornu, approximate 3-4cm from the left corneal border, where again it may be fixed to the fundus, then fed anteriorly and vertically down to the level of the left corner of the lower segment incision. 9. The needle is then passed through the left corner in the same fashion as on the right hand side, to emerge below the incision margin on the left side. 10. With the suture now in place, the assistant bimanually compresses the uterus while the surgeon pulls the chromic suture taught. 11. If a third person confirms that the bleeding is controlled (as observed vaginally), the surgeon ties the suture to keep it in position and closes the lower segment uterine incision. 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